Primary perivascular epithelioid cell tumor of the liver: new case report and literature review

• Published in: Diagnostic pathology Vol. 9; no. 1; p. 149
• Main Authors: Ameurtesse, Hassania, Chbani, Laïla, Bennani, Amal, Toughrai, Imane, Beggui, Nouhad, Kamaoui, Imane, Elfatemi, Hinde, Harmouch, Taoufik, Amarti, Afaf
• Format: Journal Article
• Language: English
• Published: England BioMed Central Ltd 17-07-2014; BioMed Central
• Subjects: Biomarkers, Tumor - analysis; Case Report; Female; Humans; Liver Neoplasms - pathology; Middle Aged; Perivascular Epithelioid Cell Neoplasms - pathology
• ISSN: 1746-1596; 1746-1596
• DOI: 10.1186/1746-1596-9-149

Perivascular epithelioid cell tumors (PEComas) encompass a group of rare mesenchymal neoplasms, which typically have a perivascular location with dual melanocytic and muscular differentiation. They are found in a variety of localizations, though lesions in the liver are exceedingly rare. Because of their rarity, the clinical, radiological and histological features of these tumors have yet to be established. This is why, it seems appropriate to report the observation of this rare hepatic tumor with a literary review including others published cases, assessing through it, clinicopathologic and radiologic features of all reported cases as well as their follow-up whenever possible.
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