Search Results - "Vilchez, J J"

Powertrain technologies and their impact on greenhouse gas emissions in key car markets by Gómez Vilchez, Jonatan J., Jochem, Patrick

“…•Market uptake of nine car powertrain technologies explored using system dynamics.•The model covers China, France, Germany, India, Japan and the United…”
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Simulating vehicle fleet composition: A review of system dynamics models by Gómez Vilchez, Jonatan J., Jochem, Patrick

“…While the market evolution of electric vehicles is uncertain, numerous studies have explored the future market diffusion of this and alternative powertrain…”
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Analysis and testing of electric car incentive scenarios in the Netherlands and Norway by Deuten, Sebastiaan, Gómez Vilchez, Jonatan J., Thiel, Christian

“…•Dynamic model updated to explore Dutch and Norwegian zero emission vehicle uptake•Behaviour reproduction, policy sensitivity and loop knock-out tests…”
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Methods for forecasting the market penetration of electric drivetrains in the passenger car market by Jochem, Patrick, Gómez Vilchez, Jonatan J., Ensslen, Axel, Schäuble, Johannes, Fichtner, Wolf

“…Current car technologies will not solve upcoming challenges of mitigating greenhouse gas emissions in road transport. Projections of the market penetration by…”
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EFNS guidelines on the diagnostic approach to pauci- or asymptomatic hyperCKemia by Kyriakides, T., Angelini, C., Schaefer, J., Sacconi, S., Siciliano, G., Vilchez, J. J., Hilton-Jones, D.

“…Objective:  To provide evidence‐based guidelines to general neurologists for the assessment of patients with pauci‐ or asymptomatic hyperCKemia. Background: …”
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How to integrate real-world user behavior into models of the market diffusion of alternative fuels in passenger cars - An in-depth comparison of three models for Germany by Gnann, T., Speth, D., Seddig, K., Stich, M., Schade, W., Gómez Vilchez, J.J.

“…The future market diffusion of alternative fuels in the passenger car sector is of great interest to both carmakers and policymakers in order to decrease CO2…”
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Soft-linking of a behavioral model for transport with energy system cost optimization applied to hydrogen in EU by Blanco, Herib, Gómez Vilchez, Jonatan J., Nijs, Wouter, Thiel, Christian, Faaij, André

“…Fuel cell electric vehicles (FCEV) currently have the challenge of high CAPEX mainly associated to the fuel cell. This study investigates strategies to promote…”
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Effects of Mental Footnotes on the Trajectory Movement in a Driving Simulation Task by Vilchez, J. L.

“…A number of experimental results about the influence of attention on movement have been explained by theoretical models based on neuronal movement…”
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New insights into the pre-ignition behavior of methane behind reflected shock waves by Caravaca-Vilchez, J., Heufer, K. A.

“…Pre-ignition is an undesired combustion event known to restrict kinetic modeling validation. Previous methane oxidation studies reported premature ignition as…”
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Interlinking major markets to explore electric car uptake by Gómez Vilchez, Jonatan J., Jochem, Patrick, Fichtner, Wolf

“…The purpose of this research is to investigate policy synergies and market interdependencies in the field of alternative powertrain technologies. The…”
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Clinical outcome in adult onset idiopathic or paraneoplastic opsoclonus–myoclonus by Bataller, L., Graus, F., Saiz, A., Vilchez, J. J.

“…We analysed a series of 24 adult patients with idiopathic (10 cases) and paraneoplastic (14 cases) opsoclonus–myoclonus syndrome (OMS) to ascertain possible…”
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Sensory neuropathy with bone destruction due to a mutation in the membrane-shaping atlastin GTPase 3 by KORNAK, Uwe, MADEMAN, Inès, POU-SERRADELL, Adolf, VILCHEZ, Juan J, BEETZ, Christian, DECONINCK, Tine, TIMMERMAN, Vincent, KAETHER, Christoph, DE JONGHE, Peter, HÜBNER, Christian A, GAL, Andreas, AMLING, Michael, SCHINKE, Marte, MUNDLOS, Stefan, BAETS, Jonathan, KURTH, Ingo, VOIGT, Martin, KRAWITZ, Peter, HECHT, Jochen, BARVENCIK, Florian, SCHINKE, Thorsten, GIESSELMANN, Sebastian, TIMO BEIL, F

“…Many neurodegenerative disorders present with sensory loss. In the group of hereditary sensory and autonomic neuropathies loss of nociception is one of the…”
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Genetics of Charcot-Marie-Tooth disease type 4A: mutations, inheritance, phenotypic variability, and founder effect by Claramunt, R, Pedrola, L, Sevilla, T, López de Munain, A, Berciano, J, Cuesta, A, Sánchez-Navarro, B, Millán, J M, Saifi, G M, Lupski, J R, Vílchez, J J, Espinós, C, Palau, F

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Using transportation accident databases to investigate ignition and explosion probabilities of flammable spills by Ronza, A., Vílchez, J.A., Casal, J.

“…Risk assessment of hazardous material spill scenarios, and quantitative risk assessment in particular, make use of event trees to account for the possible…”
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Mutations in the MORC2 gene cause axonal Charcot-Marie-Tooth disease by Sevilla, Teresa, Lupo, Vincenzo, Martínez-Rubio, Dolores, Sancho, Paula, Sivera, Rafael, Chumillas, María J, García-Romero, Mar, Pascual-Pascual, Samuel I, Muelas, Nuria, Dopazo, Joaquín, Vílchez, Juan J, Palau, Francesc, Espinós, Carmen

“…Charcot-Marie-Tooth disease (CMT) is a complex disorder with wide genetic heterogeneity. Here we present a new axonal Charcot-Marie-Tooth disease form,…”
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Phenotypical spectrum of DOK7 mutations in congenital myasthenic syndromes by Müller, Juliane S., Herczegfalvi, Agnes, Vilchez, Juan J., Colomer, Jaume, Bachinski, Linda L., Mihaylova, Violeta, Santos, Manuela, Schara, Ulrike, Deschauer, Marcus, Shevell, Michael, Poulin, Chantal, Dias, Ana, Soudo, Ana, Hietala, Marja, Äärimaa, Tuula, Krahe, Ralf, Karcagi, Veronika, Huebner, Angela, Beeson, David, Abicht, Angela, Lochmüller, Hanns

“…Dok ('downstream-of-kinase') family of cytoplasmic proteins play a role in signalling downstream of receptor and non-receptor phosphotyrosine kinases…”
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Multi-residue analysis of 36 priority and emerging pollutants in marine echinoderms (Holothuria tubulosa) and marine sediments by solid-liquid extraction followed by dispersive solid phase extraction and liquid chromatography–tandem mass spectrometry analysis by Martín, J., Zafra-Gómez, A., Hidalgo, F., Ibáñez-Yuste, A.J., Alonso, E., Vilchez, J.L.

“…Marine echinoderms are filter-feeding invertebrates widely distributed along the coasts, and which are therefore extensively exposed to anthropogenic…”
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Vocal cord paresis and diaphragmatic dysfunction are severe and frequent symptoms of GDAP1-associated neuropathy by Sevilla, Teresa, Jaijo, Teresa, Nauffal, Dolores, Collado, Diego, Chumillas, María José, Vilchez, Juan J., Muelas, Nuria, Bataller, Luis, Domenech, Rosalía, Espinós, Carmen, Palau, Francesc

“…Cranial nerve involvement in Charcot-Marie-Tooth disease (CMT) is rare, though there are a number of CMT syndromes in which vocal cord paralysis is a…”
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ANKK1 is found in myogenic precursors and muscle fibers subtypes with glycolytic metabolism by Rubio-Solsona, Estrella, Martí, Salvador, Vílchez, Juan J, Palau, Francesc, Hoenicka, Janet

“…Ankyrin repeat and kinase domain containing 1 (ANKK1) gene has been widely related to neuropsychiatry disorders. The localization of ANKK1 in neural…”
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Limb-girdle muscular dystrophy 1F is caused by a microdeletion in the transportin 3 gene by MELIA, Maria J, KUBOTA, Akatsuki, GARCIA-ARUMI, Elena, ANDREU, Antoni L, NAVARRO, Carmen, HIRANO, Michio, MARTI, Ramon, ORTOLANO, Saida, VILCHEZ, Juan J, GAMEZ, Josep, TANJ I, Kurenai, BONILLA, Eduardo, PALENZUELA, Lluís, FERNANDEZ-CADENAS, Israel, PRISTOUPILOVA, Anna

“…In 2001, we reported linkage of an autosomal dominant form of limb-girdle muscular dystrophy, limb-girdle muscular dystrophy 1F, to chromosome 7q32.1-32.2, but…”
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