Primary Hepatic Epithelioid Hemangioendothelioma masquerading as metastases: A rare case report

Epithelioid hemangioendothelioma (EHE) of liver is an extremely rare malignant tumour of vascular origin, representing less than 1 % of all vascular tumours. Nearly 260 cases have been reported in English literature. Radiologically it is seen as multifocal lesions. It can be seen at different sites...

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Bibliographic Details
Published in:Radiology case reports Vol. 18; no. 10; pp. 3739 - 3747
Main Authors: Marak, Dr James R., Raj, Dr Gaurav, Verma, Dr Shashwat, Gandhi, Dr Ajeet
Format: Journal Article
Language:English
Published: Elsevier Inc 01-10-2023
Elsevier
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Summary:Epithelioid hemangioendothelioma (EHE) of liver is an extremely rare malignant tumour of vascular origin, representing less than 1 % of all vascular tumours. Nearly 260 cases have been reported in English literature. Radiologically it is seen as multifocal lesions. It can be seen at different sites like lungs, bones, lymph nodes, breast and soft tissue. Often it is misdiagnosed with metastases, cholangiocarcinoma or angiosarcoma. No definite treatment protocol is available due to its rarity, however these malignancy are treated by radical resection of the tumour or liver transplant and /or chemotherapy. Here we present a primary hepatic epithelioid hemangioendothelioma (HEHE) which was mimicking metastases in a 42 year old male who was treated with chemotherapy and radiotherapy. Sadly patient expired after 1 year of complete course of treatment. Imaging features can help to improve the diagnostic accuracy of this tumour.
ISSN:1930-0433
1930-0433
DOI:10.1016/j.radcr.2023.07.046