Search Results - "Sturm, Ekkehard"

A new variant of Abernethy malformation treated by transhepatic interventional closure: a case report by Sieverding, Ludger, Hofbeck, Michael, Michel, Jörg, Hornung, Andreas, Scheckenbach, Christian, Grözinger, Gerd, Sturm, Ekkehard, Warmann, Steven W, Hanser, Anja

“…Congenital portosystemic shunts (CPSS) are rare vascular malformations and can be classified into extrahepatic and intrahepatic shunts. Extrahepatic CPSS, also…”
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Position statement on access to care in rare liver diseases: advancements of the European reference network (ERN) RARE-LIVER by Bernts, Lucas H P, Jones, David E J, Kaatee, Marleen M, Lohse, Ansgar W, Schramm, Christoph, Sturm, Ekkehard, Drenth, Joost P H

“…The European Reference Network for rare liver diseases (ERN RARE-LIVER) is a Europe-wide network of paediatric and adult hepatologists from expert centres in…”
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Benign recurrent intrahepatic cholestasis type 2 is caused by mutations in ABCB11 by van Mil, Saskia W C, van der Woerd, Wendy L, van der Brugge, Gerda, Sturm, Ekkehard, Jansen, Peter L M, Bull, Laura N, van den Berg, Inge E T, Berger, Ruud, Houwen, Roderick H J, Klomp, Leo W J

“…Progressive familial intrahepatic cholestasis (PFIC) and benign recurrent intrahepatic cholestasis (BRIC) are hereditary liver disorders; PFIC is characterized…”
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The Orphan Nuclear Receptor, shp, Mediates Bile Acid-Induced Inhibition of the Rat Bile Acid Transporter, ntcp by Denson, Lee A., Sturm, Ekkehard, Echevarria, Wihelma, Zimmerman, Tracy L., Makishima, Makoto, Mangelsdorf, David J., Karpen, Saul J.

“…Background & Aims: Hepatic bile acid homeostasis is regulated by negative feedback inhibition of genes involved in the uptake and synthesis of bile acids. Bile…”
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Spectrum of Interventional Procedures During Hybrid Central Line Placement in Pediatric Intestinal Rehabilitation Patients With End-Stage Vascular Access by Sieverding, Ludger, Michel, Jörg, Urla, Christian, Sturm, Ekkehard, Winkler, Franziska, Hofbeck, Michael, Fuchs, Jörg, Hilberath, Johannes, Warmann, Steven Walter

“…Loss of available central vein access sites for parenteral nutrition delivery represents one of the main indications for intestinal transplantation in children…”
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ERCP in infants, children and adolescents is feasible and safe: results from a tertiary care center by Felux, Jasmin, Sturm, Ekkehard, Busch, Andreas, Zerabruck, Emanuel, Graepler, Florian, Stüker, Dietmar, Manger, Andreas, Kirschner, Hans-Joachim, Blumenstock, Gunnar, Malek, Nisar P., Goetz, Martin

“…Background Indications for endoscopic retrograde cholangiopancreatography (ERCP) in children differ from adults. Paucity of data and concerns about potential…”
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Bile acid-activated nuclear receptor FXR suppresses apolipoprotein A-I transcription via a negative FXR response element by Claudel, Thierry, Sturm, Ekkehard, Duez, Hélène, Torra, Inés Pineda, Sirvent, Audrey, Kosykh, Vladimir, Fruchart, Jean-Charles, Dallongeville, Jean, Hum, Dean W, Kuipers, Folkert, Staels, Bart

“…Serum levels of HDL are inversely correlated with the risk of coronary heart disease. The anti-atherogenic effect of HDL is partially mediated by its major…”
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Safety and Tolerance of Donor-Derived Mesenchymal Stem Cells in Pediatric Living-Donor Liver Transplantation: The MYSTEP1 Study by Nadalin, Silvio, Sturm, Ekkehard, Handgretinger, Rupert, Riethmüller, Joachim, Dahlke, Marc H., Lang, Peter, Mezger, Markus, Döring, Michaela, Schumm, Michael, Hartleif, Steffen, Königsrainer, Alfred

“…Background. Calcineurin inhibitors (CNI) have significantly improved patient and graft survival in pediatric liver transplantation (pLT). However, CNI toxicity…”
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The wide spectrum of multidrug resistance 3 deficiency: From neonatal cholestasis to cirrhosis of adulthood by Jacquemin, Emmanuel, De Vree, J. Marleen L., Cresteil, Danièle, Sokal, Etienne M., Sturm, Ekkehard, Dumont, Micheline, Scheffer, George L., Paul, Marianne, Burdelski, Martin, Bosma, Piter J., Bernard, Olivier, Hadchouel, Michelle, Oude Elferink, Ronald P.J.

“…Background & Aims: We have specified the features of progressive familial intrahepatic cholestasis type 3 and investigated in 31 patients whether a defect of…”
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Mutations in the MDR3 Gene Cause Progressive Familial Intrahepatic Cholestasis by J. Marleen L. De Vree, Jacquemin, Emmanuel, Sturm, Ekkehard, Cresteil, Daniele, Bosma, Piter J., Aten, Jan, Deleuze, Jean-Francois, Desrochers, Marc, Burdelski, Martin, Bernard, Olivier, Ronald P. J. Oude Elferink, Hadchouel, Michelle

“…Class III multidrug resistance (MDR) P-glycoproteins (P-gp), mdr2 in mice and MDR3 in man, mediate the translocation of phosphatidylcholine across the…”
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Genetic cholestasis, causes and consequences for hepatobiliary transport by Jansen, Peter L. M., Sturm, Ekkehard

“…: Bile salts take part in an efficient enterohepatic circulation in which most of the secreted bile salts are reclaimed by absorption in the terminal ileum. In…”
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Screening Endoscopy Contributes to Relevant Modifications of Therapeutic Regimen in Children With Intestinal Failure by Busch, Andreas, Sturm, Ekkehard

“…ABSTRACT Objective: The role of endoscopy in the diagnostic workup of children with intestinal failure (IF) is not well defined. It is unclear whether…”
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The farnesoid X receptor: a novel drug target? by Claudel, Thierry, Sturm, Ekkehard, Kuipers, Folkert, Staels, Bart

“…Bile acids are end products of cholesterol metabolism. They are exclusively synthesised by the liver and subsequently secreted via the bile duct into the…”
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Odevixibat and partial external biliary diversion showed equal improvement of cholestasis in a patient with progressive familial intrahepatic cholestasis by Slavetinsky, Christoph, Sturm, Ekkehard

“…Untreated progressive familial intrahepatic cholestasis (PFIC) type 2, or bile salt exporter protein deficiency, frequently leads to severe pruritus, impaired…”
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Mutation detection in cholestatic patients using microarray resequencing of ATP8B1 and ABCB11 [version 2; peer review: 2 approved, 1 approved with reservations] by McKay, Kirsten E, Bruce, Christopher K, Hartley, Jane L, Knisely, A S, Baumann, Ulrich, Bockisch, Sonja-Stephanie, Sturm, Ekkehard, Hendriksz, Christian J, Kelly, Deidre A, Macdonald, Fiona, Gissen, Paul

“…Background : Neonatal cholestasis is a common presentation of childhood liver diseases and can be a feature of various conditions including disorders of bile…”
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Liver, Hormones, and Bones by Sturm, Ekkehard

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The EASL–Lancet Liver Commission: protecting the next generation of Europeans against liver disease complications and premature mortality by Karlsen, Tom H, Sheron, Nick, Zelber-Sagi, Shira, Carrieri, Patrizia, Dusheiko, Geoffrey, Bugianesi, Elisabetta, Pryke, Rachel, Hutchinson, Sharon J, Sangro, Bruno, Martin, Natasha K, Cecchini, Michele, Dirac, Mae Ashworth, Belloni, Annalisa, Serra-Burriel, Miquel, Ponsioen, Cyriel Y, Sheena, Brittney, Lerouge, Alienor, Devaux, Marion, Scott, Nick, Hellard, Margaret, Verkade, Henkjan J, Sturm, Ekkehard, Marchesini, Giulio, Yki-Järvinen, Hannele, Byrne, Chris D, Targher, Giovanni, Tur-Sinai, Aviad, Barrett, Damon, Ninburg, Michael, Reic, Tatjana, Taylor, Alison, Rhodes, Tim, Treloar, Carla, Petersen, Claus, Schramm, Christoph, Flisiak, Robert, Simonova, Marieta Y, Pares, Albert, Johnson, Philip, Cucchetti, Alessandro, Graupera, Isabel, Lionis, Christos, Pose, Elisa, Fabrellas, Núria, Ma, Ann T, Mendive, Juan M, Mazzaferro, Vincenzo, Rutter, Harry, Cortez-Pinto, Helena, Kelly, Deirdre, Burton, Robyn, Lazarus, Jeffrey V, Ginès, Pere, Buti, Maria, Newsome, Philip N, Burra, Patrizia, Manns, Michael P

“…© 2021 Elsevier Ltd. All rights reserved. Liver diseases have become a major health threat across Europe, and the face of European hepatology is changing due…”
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110: Tapering enteroplasty or bowel lengthening? – A surgical algorithm for pediatric intestinal rehabilitation patients with bowel dilatation by Warmann, Steven, Schunn, Matthias, Fuchs, Joerg, Tsiflikas, Ilias, Sturm, Ekkehard, Hartleif, Steffen, Scherer, Simon, Hilberath, Johannes

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Efficacy and safety of maralixibat treatment in patients with Alagille syndrome and cholestatic pruritus (ICONIC): a randomised phase 2 study by Gonzales, Emmanuel, Hardikar, Winita, Stormon, Michael, Baker, Alastair, Hierro, Loreto, Gliwicz, Dorota, Lacaille, Florence, Lachaux, Alain, Sturm, Ekkehard, Setchell, Kenneth D R, Kennedy, Ciara, Dorenbaum, Alejandro, Steinmetz, Jana, Desai, Nirav K, Wardle, Andrew J, Garner, Will, Vig, Pamela, Jaecklin, Thomas, Sokal, Etienne M, Jacquemin, Emmanuel

“…Alagille syndrome is a rare genetic disease that often presents with severe cholestasis and pruritus. There are no approved drugs for management. Maralixibat,…”
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Long-term efficacy and safety of odevixibat in patients with progressive familial intrahepatic cholestasis: results with 96 weeks or more of treatment by Thompson, Richard, Durmaz, Ozlem, Grammatikopoulos, Tassos, Di Giorgio, Angelo, Ni, Quanhong, Stein, Philip, Clemson, Christine, Sturm, Ekkehard

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