Search Results - "Shell, Richard"
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Onasemnogene abeparvovec preserves bulbar function in infants with presymptomatic spinal muscular atrophy: a post-hoc analysis of the SPR1NT trial
Published in Neuromuscular disorders : NMD (01-08-2023)“…•Bulbar function includes normal swallow, oral nutrition, and pulmonary stability.•Onasemnogene abeparvovec before SMA symptom onset preserves bulbar…”
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Cysteamine-mediated clearance of antibiotic-resistant pathogens in human cystic fibrosis macrophages
Published in PloS one (05-10-2017)“…Members of the Burkholderia cepacia complex are virulent, multi-drug resistant pathogens that survive and replicate intracellularly in patients with cystic…”
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Transactional Man: Teaching Negotiation Strategy in the Age of Trump
Published in Negotiation journal (01-01-2019)Get full text
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Applying Adult Learning Practices in Medical Education
Published in Current problems in pediatric and adolescent health care (01-07-2014)“…The application of the best practices of teaching adults to the education of adults in medical education settings is important in the process of transforming…”
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Patients with Spinal Muscular Atrophy Type 1 Achieve and Maintain Bulbar Function Following Onasemnogene Abeparvovec Treatment
Published in Journal of neuromuscular diseases (01-01-2023)“…Improvement and maintenance of bulbar function are goals of disease-modifying treatments for spinal muscular atrophy (SMA). Lack of standardized measures and a…”
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Randomized trial of biofilm testing to select antibiotics for cystic fibrosis airway infection
Published in Pediatric pulmonology (01-02-2011)“…Rationale In cystic fibrosis (CF), conventional antibiotic susceptibility results correlate poorly with clinical outcomes. We hypothesized that biofilm testing…”
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Pretransplant Panel Reactive Antibodies and Lung Transplant Outcomes in Children
Published in The Thoracic and cardiovascular surgeon (01-01-2017)“…Pre-lung transplant (LTx) panel reactive antibody (PRA) levels are associated with adverse outcomes in adult LTx recipients, but their impact in pediatric LTx…”
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Clinico-pathological Conference: A hypotonic newborn with cleft palate, micrognathia and bilateral club feet
Published in Pediatric neurology (04-02-2017)Get full text
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Workplace bullying: a systematic review of risk factors and outcomes
Published in Theoretical issues in ergonomics science (01-05-2006)“…Background: Studies investigating workplace bullying started in the early 1990s in Scandinavian countries. Research has been conducted regarding bullying…”
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Impact of added rest breaks on the productivity and well being of workers
Published in Ergonomics (01-02-2001)“…The impact of frequent short rest breaks on the productivity and well being of a group of 30 workers in a meat-processing plant was studied. Two rest break…”
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Comparison and evaluation of maintenance operations in lean versus non-lean production systems
Published in Journal of quality in maintenance engineering (14-08-2009)“…Purpose - Previous studies have found general differences between non-lean and lean production systems, but none of them have identified the major factors in…”
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Breaking Bad News Is a Teachable Skill in Pediatrics
Published in Academic pediatrics (01-07-2014)Get full text
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Molecular Characterization of Adeno-Associated Viruses Infecting Children
Published in Journal of Virology (01-12-2005)“…Article Usage Stats Services JVI Citing Articles Google Scholar PubMed Related Content Social Bookmarking CiteULike Delicious Digg Facebook Google+ Mendeley…”
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Chronic aspiration without gastroesophageal reflux as a cause of chronic respiratory symptoms in neurologically normal infants
Published in Chest (01-10-2001)“…To describe 13 neurologically normal infants with chronic respiratory symptoms who had swallowing dysfunction with silent chronic aspiration without…”
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Does emotional intelligence predict breaking bad news skills in pediatric interns? A pilot study
Published in Medical education online (01-01-2015)“…While both patients and physicians identify communication of bad news as an area of great challenge, the factors underlying this often complex task remain…”
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The Experimental Appraisal Instrument: A brief overview
Published in Human factors and ergonomics in manufacturing & service industries (01-05-2008)“…Background Recently, there has been a great influx in experimental research to assess the health effects of nanoparticles/materials/fibers. Currently, there is…”
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Five-Year Extension Results of the Phase 1 START Trial of Onasemnogene Abeparvovec in Spinal Muscular Atrophy
Published in JAMA neurology (01-07-2021)“…This ongoing study assesses long-term safety and durability of response in infants with spinal muscular atrophy (SMA) type 1 after dosing with onasemnogene…”
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Assessment of Systemic Delivery of rAAVrh74.MHCK7.micro-dystrophin in Children With Duchenne Muscular Dystrophy: A Nonrandomized Controlled Trial
Published in JAMA neurology (01-09-2020)“…Micro-dystrophin gene transfer shows promise for treating patients with Duchenne muscular dystrophy (DMD) using recombinant adeno-associated virus serotype…”
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Single-Dose Gene-Replacement Therapy for Spinal Muscular Atrophy
Published in The New England journal of medicine (02-11-2017)“…Fifteen children with spinal muscular atrophy type 1 received gene-replacement therapy with a single dose of adeno-associated virus containing SMN. In marked…”
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