Alveolar capillary dysplasia with misalignment of the pulmonary veins associated with aortic coarctation and intestinal malrotation

Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal cause of refractory pulmonary hypertension of the newborn. We describe the clinical course of a neonate with refractory pulmonary hypertension diagnosed with ACD/MPV, aortic coarctation and other not...

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Bibliographic Details
Published in:	Journal of perinatology Vol. 34; no. 10; pp. 795 - 797
Main Authors:	Arreo del Val, V, Avila-Alvarez, A, Schteffer, L R, Santos, F, Deiros, L, Del Cerro, M J
Format:	Journal Article
Language:	English
Published:	New York Nature Publishing Group US 01-10-2014 Nature Publishing Group
Subjects:	692/699/1503/1581 692/699/1785 692/699/75/593 692/700/1720/3186 Abnormalities, Multiple - diagnosis Abnormalities, Multiple - therapy Alveoli Aorta Aortic Coarctation - diagnostic imaging Aortic Coarctation - surgery Autopsies Autopsy Biopsy Bronchopulmonary dysplasia Cardiac Surgical Procedures - methods Care and treatment Case studies Development and progression Diagnosis Digestive System Abnormalities - diagnosis Digestive System Abnormalities - surgery Disease Progression Dysplasia Echocardiography, Doppler Fatal Outcome Heart Humans Hypertension Hypertension, Pulmonary - diagnosis Hypertension, Pulmonary - etiology Infant, Newborn Infant, Premature Intestinal Volvulus - diagnosis Intestinal Volvulus - surgery Male Medical examination Medicine Medicine & Public Health Misalignment Mutation Nitric oxide Pediatric Surgery Pediatrics perinatal-neonatal-case-presentation Persistent Fetal Circulation Syndrome - diagnosis Postoperative Complications - pathology Pulmonary arteries Pulmonary hypertension Pulmonary veins Rare Diseases Respiratory Distress Syndrome, Newborn - diagnosis Respiratory Distress Syndrome, Newborn - etiology Veins Veins & arteries Ventilators Madrid Spain Spain
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Summary:	Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal cause of refractory pulmonary hypertension of the newborn. We describe the clinical course of a neonate with refractory pulmonary hypertension diagnosed with ACD/MPV, aortic coarctation and other not previously reported associated malformations.
Bibliography:	ObjectType-Case Study-3 SourceType-Scholarly Journals-1 content type line 23 ObjectType-Review-1 ObjectType-Feature-5 ObjectType-Report-2 ObjectType-Article-4
ISSN:	0743-8346 1476-5543
DOI:	10.1038/jp.2014.94