Search Results - "SPIRITO, Paolo"

Saving More Lives by Spirito, Paolo, MD

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The Dawn of a Better Day for Patients With Hypertrophic Cardiomyopathy by Spirito, Paolo, MD

“…Of the remaining 23 patients whose deaths were HCM-related, 17 died of advanced heart failure (with or without heart transplants) in the absence of LV outflow…”
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Prevention of Sudden Cardiac Death With Implantable Cardioverter-Defibrillators in Children and Adolescents With Hypertrophic Cardiomyopathy by Maron, Barry J., MD, Spirito, Paolo, MD, Ackerman, Michael J., MD, PhD, Casey, Susan A., RN, Semsarian, Christopher, MB, BS, PhD, Estes, N.A. Mark, MD, Shannon, Kevin M., MD, Ashley, Euan A., PhD, Day, Sharlene M., MD, Pacileo, Giuseppe, MD, Formisano, Francesco, MD, Devoto, Emmanuela, MD, Anastasakis, Aristidis, MD, Bos, J. Martijn, MD, PhD, Woo, Anna, MD, Autore, Camillo, MD, Pass, Robert H., MD, Boriani, Giuseppe, MD, PhD, Garberich, Ross F., MS, Almquist, Adrian K., MD, Russell, Mark W., MD, Boni, Luca, MD, PhD, Berger, Stuart, MD, Maron, Martin S., MD, Link, Mark S., MD

“…Objectives The aim of this study was to determine the efficacy of implantable cardioverter-defibrillators (ICDs) in children and adolescents with hypertrophic…”
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Prevalence, clinical profile, and significance of left ventricular remodeling in the end-stage phase of hypertrophic cardiomyopathy by HARRIS, Kevin M, SPIRITO, Paolo, MARON, Martin S, ZENOVICH, Andrey G, FORMISANO, Francesco, LESSER, John R, MACKEY-BOJACK, Shannon, MANNING, Warren J, UDELSON, James E, MARON, Barry J

“…End stage (ES) is a recognized part of the hypertrophic cardiomyopathy (HCM) disease spectrum. Frequency, clinical profile and course, and treatment strategies…”
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Syncope and Risk of Sudden Death in Hypertrophic Cardiomyopathy by SPIRITO, Paolo, AUTORE, Camillo, BIAGINI, Elena, QUARTA, Giovanni, CONTE, Maria Rosa, BRUZZI, Paolo, MARON, Barry J, RAPEZZI, Claudio, BERNABO, Paola, BADAGLIACCA, Roberto, MARON, Martin S, BONGIOANNI, Sergio, COCCOLO, Fabio, ESTES, N. A. Mark, BARILLA, Caterina S

“…The prognostic significance of syncope has not been investigated systematically in hypertrophic cardiomyopathy, and treatment strategies have been based…”
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Implantable Cardioverter-Defibrillators and Prevention of Sudden Cardiac Death in Hypertrophic Cardiomyopathy by Maron, Barry J, Spirito, Paolo, Shen, Win-Kuang, Haas, Tammy S, Formisano, Francesco, Link, Mark S, Epstein, Andrew E, Almquist, Adrian K, Daubert, James P, Lawrenz, Thorsten, Boriani, Giuseppe, Estes, N. A. Mark, Favale, Stefano, Piccininno, Marco, Winters, Stephen L, Santini, Massimo, Betocchi, Sandro, Arribas, Fernando, Sherrid, Mark V, Buja, Gianfranco, Semsarian, Christopher, Bruzzi, Paolo

“…CONTEXT Recently, the implantable cardioverter-defibrillator (ICD) has been promoted for prevention of sudden death in hypertrophic cardiomyopathy (HCM)…”
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Diagnosis and Evaluation of Hypertrophic Cardiomyopathy by Maron, Barry J., Desai, Milind Y., Nishimura, Rick A., Spirito, Paolo, Rakowski, Harry, Towbin, Jeffrey A., Rowin, Ethan J., Maron, Martin S., Sherrid, Mark V.

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Implantable Defibrillators and Prevention of Sudden Death in Hypertrophic Cardiomyopathy by MARON, BARRY J., SPIRITO, PAOLO

“…Hypertrophic cardiomyopathy (HCM) is the most common cause of sudden cardiac death in young people, including trained athletes. The implantable…”
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Risk of Sudden Death and Outcome in Patients With Hypertrophic Cardiomyopathy With Benign Presentation and Without Risk Factors by Spirito, Paolo, MD, Autore, Camillo, MD, Formisano, Francesco, MD, Assenza, Gabriele Egidy, MD, Biagini, Elena, MD, Haas, Tammy S., RN, Bongioanni, Sergio, MD, Semsarian, Christopher, MD, Devoto, Emmanuela, MD, Musumeci, Beatrice, MD, Lai, Francesco, MD, Yeates, Laura, BSc, Conte, Maria Rosa, MD, Rapezzi, Claudio, MD, Boni, Luca, MD, Maron, Barry J., MD

“…Patients with hypertrophic cardiomyopathy (HC) are reported to have a mortality rate of about 1.0% per year, and those patients without sudden death risk…”
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Prognostic Implications of the Doppler Restrictive Filling Pattern in Hypertrophic Cardiomyopathy by Biagini, Elena, MD, PhD, Spirito, Paolo, MD, Rocchi, Guido, MD, Ferlito, Marinella, MD, Rosmini, Stefania, MD, Lai, Francesco, MD, Lorenzini, Massimiliano, MD, Terzi, Francesca, MD, Bacchi-Reggiani, Letizia, MSc, Boriani, Giuseppe, MD, Branzi, Angelo, MD, Boni, Luca, MD, Rapezzi, Claudio, MD

“…The Doppler echocardiographic pattern of restrictive left ventricular (LV) filling has proved to be an important predictor of clinical course and prognosis in…”
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Surgical Ventricular Septal Myectomy in the Developing World by Maron, Barry J., MD, Spirito, Paolo, MD

“…Surgical septal myectomy is the preferred treatment strategy in hypertrophic cardiomyopathy (HC) to reverse progressive heart failure symptoms due to left…”
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Significance of Late Gadolinium Enhancement at Right Ventricular Attachment to Ventricular Septum in Patients With Hypertrophic Cardiomyopathy by Chan, Raymond H., MD, MPH, Maron, Barry J., MD, Olivotto, Iacopo, MD, Assenza, Gabriele E., MD, Haas, Tammy S., RN, Lesser, John R., MD, Gruner, Christiane, MD, Crean, Andrew M., MD, Rakowski, Harry, MD, Rowin, Ethan, MD, Udelson, James, MD, Lombardi, Massimo, MD, Tomberli, Benedetta, MD, Spirito, Paolo, MD, Formisano, Francesco, MD, Marra, Martina P., MD, Biagini, Elena, MD, Autore, Camillo, MD, Manning, Warren J., MD, Appelbaum, Evan, MD, Roberts, William C., MD, Basso, Cristina, MD, PhD, Maron, Martin S., MD

“…Cardiovascular magnetic resonance (CMR) with extensive late gadolinium enhancement (LGE) is a novel marker for increased risk for sudden death (SD) in patients…”
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Significance of Sarcomere Gene Mutations Analysis in the End-Stage Phase of Hypertrophic Cardiomyopathy by Biagini, Elena, MD, PhD, Olivotto, Iacopo, MD, Iascone, Maria, BSc, PhD, Parodi, Maria I., BSc, Girolami, Francesca, BSc, Frisso, Giulia, MD, PhD, Autore, Camillo, MD, Limongelli, Giuseppe, MD, Cecconi, Massimiliano, BSc, Maron, Barry J., MD, Maron, Martin S., MD, Rosmini, Stefania, MD, Formisano, Francesco, MD, Musumeci, Beatrice, MD, Cecchi, Franco, MD, Iacovoni, Attilio, MD, Haas, Tammy S., RN, Bacchi Reggiani, Maria L., MSc, MStat, Ferrazzi, Paolo, MD, Salvatore, Francesco, MD, PhD, Spirito, Paolo, MD, Rapezzi, Claudio, MD

“…End-stage hypertrophic cardiomyopathy (ES-HC) has an ominous prognosis. Whether genotype can influence ES-HC occurrence is unresolved. We assessed the spectrum…”
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Glycogen Storage Diseases Presenting as Hypertrophic Cardiomyopathy by Arad, Michael, Maron, Barry J, Gorham, Joshua M, Johnson, Walter H, Saul, J. Philip, Perez-Atayde, Antonio R, Spirito, Paolo, Wright, Gregory B, Kanter, Ronald J, Seidman, J.G, Seidman, Christine E

“…Hypertrophic cardiomyopathy is usually caused by mutations in sarcomere proteins, but in some patients such mutations are not found. This study identified…”
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The prognostic importance of left ventricular outflow obstruction in hypertrophic cardiomyopathy varies in relation to the severity of symptoms by Autore, Camillo, Bernabò, Paola, Barillà, Caterina Stella, Bruzzi, Paolo, Spirito, Paolo

“…The aim of this study was to investigate whether the prognostic importance of left ventricular (LV) outflow obstruction in hypertrophic cardiomyopathy (HCM) is…”
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Magnitude of Left Ventricular Hypertrophy and Risk of Sudden Death in Hypertrophic Cardiomyopathy by Spirito, Paolo, Bellone, Pietro, Harris, Kevin M, Bernabò, Paola, Bruzzi, Paolo, Maron, Barry J

“…Sudden death has been recognized as a possible consequence of hypertrophic cardiomyopathy since the first modern descriptions of the disease. 1 , 2 However,…”
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Targeted next-generation sequencing helps to decipher the genetic and phenotypic heterogeneity of hypertrophic cardiomyopathy by Cecconi, Massimiliano, Parodi, Maria I, Formisano, Francesco, Spirito, Paolo, Autore, Camillo, Musumeci, Maria B, Favale, Stefano, Forleo, Cinzia, Rapezzi, Claudio, Biagini, Elena, Davì, Sabrina, Canepa, Elisabetta, Pennese, Loredana, Castagnetta, Mauro, Degiorgio, Dario, Coviello, Domenico A

“…Hypertrophic cardiomyopathy (HCM) is mainly associated with myosin, heavy chain 7 (MYH7) and myosin binding protein C, cardiac (MYBPC3) mutations. In order to…”
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Why we Need More Septal Myectomy Surgeons: an Emerging Recognition by Maron, Barry J., MD, Dearani, Joseph A., MD, Maron, Martin S., MD, Ommen, Steve R., MD, Rastegar, Hassan, MD, Nishimura, Rick A., MD, Swistel, Daniel G., MD, Sherrid, Mark V., MD, Ralph-Edwards, Anthony, MD, Rakowski, Harry, MD, Smedira, Nicholas G., MD, Rowin, Ethan J., MD, Desai, Milind Y., MD, Lever, Harry M., MD, Spirito, Paolo, MD, Ferrazzi, Paolo, MD, Schaff, Hartzell V., MD

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The Management of Hypertrophic Cardiomyopathy by Spirito, Paolo, Seidman, Christine E, McKenna, William J, Maron, Barry J

“…Hypertrophic cardiomyopathy is a complex cardiac disease with unique pathophysiologic characteristics and a great diversity of morphologic, functional, and…”
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Usefulness of Delayed Enhancement by Magnetic Resonance Imaging in Hypertrophic Cardiomyopathy as a Marker of Disease and Its Severity by Aquaro, Giovanni Donato, MD, Masci, Piergiorgio, MD, Formisano, Francesco, MD, Barison, Andrea, MD, Strata, Elisabetta, MD, Pingitore, Alessandro, PhD, Positano, Vincenzo, MSC, Spirito, Paolo, MD, Lombardi, Massimo, MD

“…The aim of the present study was to evaluate, in patients with hypertrophic cardiomyopathy (HC), the association between late gadolinium enhancement and…”
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