Search Results - "Rodinova, Marie"

Loss of Mitochondrial AAA Proteases AFG3L2 and YME1L Impairs Mitochondrial Structure and Respiratory Chain Biogenesis by Cesnekova, Jana, Rodinova, Marie, Hansikova, Hana, Zeman, Jiri, Stiburek, Lukas

“…Mitochondrial protein quality control is crucial for the maintenance of correct mitochondrial homeostasis. It is ensured by several specific mitochondrial…”
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Increased nuclear DNA damage precedes mitochondrial dysfunction in peripheral blood mononuclear cells from Huntington’s disease patients by Askeland, Georgina, Dosoudilova, Zaneta, Rodinova, Marie, Klempir, Jiri, Liskova, Irena, Kuśnierczyk, Anna, Bjørås, Magnar, Nesse, Gaute, Klungland, Arne, Hansikova, Hana, Eide, Lars

“…Huntington’s disease (HD) is a progressive neurodegenerative disorder primarily affecting the basal ganglia and is caused by expanded CAG repeats in the…”
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Deterioration of mitochondrial bioenergetics and ultrastructure impairment in skeletal muscle of a transgenic minipig model in the early stages of Huntington's disease by Rodinova, Marie, Krizova, Jana, Stufkova, Hana, Bohuslavova, Bozena, Askeland, Georgina, Dosoudilova, Zaneta, Juhas, Stefan, Juhasova, Jana, Ellederova, Zdenka, Zeman, Jiri, Eide, Lars, Motlik, Jan, Hansikova, Hana

“…Skeletal muscle wasting and atrophy is one of the more severe clinical impairments resulting from the progression of Huntington's disease (HD). Mitochondrial…”
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Isolation and Characterization of Small Extracellular Vesicles from Porcine Blood Plasma, Cerebrospinal Fluid, and Seminal Plasma by Skalnikova, Helena Kupcova, Bohuslavova, Bozena, Turnovcova, Karolina, Juhasova, Jana, Juhas, Stefan, Rodinova, Marie, Vodicka, Petr

“…Extracellular vesicles (EVs) are a highly attractive subject of biomedical research as possible carriers of nucleic acid and protein biomarkers. EVs released…”
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A transgenic minipig model of Huntington's disease shows early signs of behavioral and molecular pathologies by Askeland, Georgina, Rodinova, Marie, Štufková, Hana, Dosoudilova, Zaneta, Baxa, Monika, Smatlikova, Petra, Bohuslavova, Bozena, Klempir, Jiri, Nguyen, The Duong, Kuśnierczyk, Anna, Bjørås, Magnar, Klungland, Arne, Hansikova, Hana, Ellederova, Zdenka, Eide, Lars

“…Huntington's disease (HD) is a monogenic, progressive, neurodegenerative disorder with currently no available treatment. The Libechov transgenic minipig model…”
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First person – Marie Rodinova

“…First Person is a series of interviews with the first authors of a selection of papers published in Disease Models & Mechanisms, helping early-career…”
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The mammalian homologue of yeast Afg1 ATPase (lactation elevated 1) mediates degradation of nuclear-encoded complex IV subunits by Cesnekova, Jana, Rodinova, Marie, Hansikova, Hana, Houstek, Josef, Zeman, Jiri, Stiburek, Lukas

“…Mitochondrial protein homeostasis is crucial for cellular function and integrity and is therefore maintained by several classes of proteins possessing…”
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A37 Buccal respiratory chain complexes I and IV quantities in huntington’s disease patients by Dusek, Pavel, Rodinova, Marie, Liskova, Irena, Klempir, Jiri, Zeman, Jiri, Roth, Jan, Hansikova, Hana

“…Alterations in mitochondrial parameteres are an important hallmark of Huntington’s disease (HD). Given the ubiquitous expression of mutant huntingtin raises…”
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C17 Increased mitochondrial number, cellular stress and glycogen accumulation in heart of minipig model transgenic for N-terminal part of human mutated huntingtin by Rodinova, Marie, Ondruskova, Nina, Dosoudilova, Zaneta, Juhas, Stefan, Juhasova, Jana, Ellederova, Zdenka, Motlik, Jan, Hansikova, Hana

“…BackgroundMinipig model transgenic for N-terminal part of human mutated huntingtin (TgHD) created in Libechov allows us to study the development of…”
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B12 Longitudinal view of mitochondrial bioenergetics in skeletal muscle of premanifest transgenic minipig model for huntington’s disease by Rodinova, Marie, Krizova, Jana, Stufkova, Hana, Bohuslavova, Bozena, Askeland, Georgina, Dosoudilova, Zaneta, Juhas, Stefan, Ellederova, Zdenka, Zeman, Jiri, Eide, Lars, Motlik, Jan, Hansikova, Hana

“…BackgroundSkeletal muscle wasting and atrophy is one of the severe clinical impairment connected with progression of Huntington’s disease (HD). Mitochondrial…”
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Mitochondrial bioenergetics in skeletal muscle of premanifest and early manifest transgenic minipig model for Huntington’s disease by Hansikova, Hana, Rodinova, Marie, Krizova, Jana, Stufkova, Hana, Bohuslavova, Bozena, Askeland, Georgina, Dosoudilova, Zaneta, Juhas, Stefan, Ellederova, Zdenka, Zeman, Jiri, Eide, Lars, Motlik, Jan

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C18 The hunt for biomarkers in presymptomatic large animal model: mitochondrial metabolism in spermatozoa of transgenic minipigs modelling huntington’s disease by Krizova, Jana, Stufkova, Hana, Rodinova, Marie, Macakova, Monika, Bohuslavova, Bozena, Pavlok, Antonin, Ellederova, Zdenka, Motlik, Jan, Zeman, Jiri, Hansikova, Hana

“…BackgroundLarge-animal minipig transgenic model of Huntington’s disease (HD), carrying N-terminal part of human mutated huntingtin, was developed in Libechov…”
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Knockout of DAPIT protein disrupts ATP synthase oligomerisation and has a profound role in regulation of glucose homeostasis by Mracek, Tomas, Pecina, Petr, Nuskova, Hana, Kovalcikova, Jana, Pecinova, Alena, Alan, Lukas, Rodinova, Marie, Zidek, Vaclav, Landa, Vladimir, Kaplanova, Vilma, Kolar, Frantisek, Papousek, Frantisek, Habart, David, Kazdova, Ludmila, Bardova, Kristyna, Tauchmannova, Katerina, Drahota, Zdenek, Kopecky, Jan, Pravenec, Michal, Houstek, Josef

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Mitochondrial Metabolism in a Large-Animal Model of Huntington Disease: The Hunt for Biomarkers in the Spermatozoa of Presymptomatic Minipigs by Krizova, Jana, Stufkova, Hana, Rodinova, Marie, Macakova, Monika, Bohuslavova, Bozena, Vidinska, Daniela, Klima, Jiri, Ellederova, Zdenka, Pavlok, Antonin, Howland, David S, Zeman, Jiri, Motlik, Jan, Hansikova, Hana

“…Huntington disease (HD) is a fatal neurodegenerative disorder involving reduced muscle coordination, mental and behavioral changes, and testicular…”
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A17 Targeting mitophagy in huntington’s disease patients’ fibroblasts by Šonský, Ivan, Volfová, Nikol, Rodinová, Marie, Vodička, Petr, Klempíř, Jiří, Hansikova, Hana

“…Huntington’s disease (HD) belongs to a group of neurodegenerative diseases characterized by features, such as the accumulation of aggregates of misfolded…”
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PP100 - Changes in hydrogen sulfide production in cystathionine beta-synthase deficiency by Kožich, Viktor, Krijt, Jakub, Sokolová, Jitka, Vozdek, Roman, Melenovská, Petra, Hansíková, Hana, Kratochvílová, Hana, Rodinová, Marie, Majtan, Tomáš, Kraus, Jan P.

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Changes in hydrogen sulfide production in cystathionine beta-synthase deficiency by Kožich, Viktor, Krijt, Jakub, Sokolová, Jitka, Vozdek, Roman, Melenovská, Petra, Hansíková, Hana, Kratochvílová, Hana, Rodinová, Marie, Majtan, Tomáš, Kraus, Jan P.

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