Search Results - "Raphael, Bram P"

Intestinal Rehabilitation Programs in the Management of Pediatric Intestinal Failure and Short Bowel Syndrome by Merritt, Russell J., Cohran, Valeria, Raphael, Bram P., Sentongo, Timothy, Volpert, Diana, Warner, Brad W., Goday, Praveen S.

“…ABSTRACT Intestinal failure is a rare, debilitating condition that presents both acute and chronic medical management challenges. The condition is incompatible…”
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Necrotizing Enterocolitis and Central Line Associated Blood Stream Infection Are Predictors of Growth Outcomes in Infants with Short Bowel Syndrome by Raphael, Bram P., MD, Mitchell, Paul D., MS, Finkton, Darryl, BA, Jiang, Hongyu, PhD, Jaksic, Tom, MD, PhD, Duggan, Christopher, MD, MPH

“…Objectives To describe the natural history of growth patterns and nutritional support in a cohort of infants with short bowel syndrome (SBS), and to…”
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A novel mutation in ICOS presenting as hypogammaglobulinemia with susceptibility to opportunistic pathogens by Chou, Janet, MD, Massaad, Michel J., PhD, Cangemi, Brittney, BA, Bainter, Wayne, BA, Platt, Craig, MD, PhD, Badran, Yousef R., MD, Raphael, Bram P., MD, Kamin, Daniel S., MD, Goldsmith, Jeffrey D., MD, Pai, Sung-Yun, MD, Al-Herz, Waleed, MD, Geha, Raif S., MD

“…To the Editor: Inducible T-cell costimulator (ICOS) is a costimulatory receptor upregulated on activated T cells.1ICOS mutations have been identified in 11…”
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Teduglutide improves liver chemistries in short bowel syndrome–associated intestinal failure: Post hoc analysis by Micic, Dejan, Robinson, Ian, Kidd, Tanya, Terreri, Brian, Raphael, Bram P.

“…Background Chronic hepatic complications are common in patients with short bowel syndrome–associated intestinal failure (SBS‐IF). Teduglutide, a glucagon‐like…”
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Effects of Teduglutide on Diarrhea in Pediatric Patients with Short Bowel Syndrome‐Associated Intestinal Failure by Fifi, Amanda, Raphael, Bram P., Terreri, Brian, Uddin, Sharif, Kaufman, Stuart S.

“…Objectives: This post‐hoc analysis evaluated the effect of teduglutide treatment on diarrhea in patients with short bowel syndrome‐associated intestinal…”
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Analysis of Healthcare Institutional Costs of Pediatric Home Parenteral Nutrition Central Line Infections by Raphael, Bram P., Hazekamp, Christina, Samnaliev, Mihail, Ozonoff, Al

“…ABSTRACT Background: Although previous literature suggests home parenteral nutrition (HPN)–dependent children experience frequent complications like…”
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Long‐term teduglutide associated with improved response in pediatric short bowel syndrome‐associated intestinal failure by Wales, Paul W., Hill, Susan, Robinson, Ian, Raphael, Bram P., Matthews, Cheney, Cohran, Valeria, Carter, Beth, Venick, Robert, Kocoshis, Samuel

“…Objectives Patients with short bowel syndrome‐associated intestinal failure (SBS‐IF) require long‐term parenteral nutrition and/or intravenous fluids (PN/IV)…”
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S574 Dupilumab Is Effective in Treating EoE in Patients Weighing ≥15 kg: Results From the Phase 3 KIDS Study by Chehade, Mirna, Cianferoni, Antonella, Xia, Changming, Pela, Tiffany, Raphael, Bram P., Radwan, Amr, Jacob-Nara, Juby A.

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Management of short‐bowel syndrome: A survey of unmet educational needs among healthcare providers by Belcher, Emily, Mercer, David, Raphael, Bram P., Salinas, Gregory D., Stacy, Sylvie, Tappenden, Kelly A.

“…Background Management of short‐bowel syndrome with intestinal failure (SBS‐IF) is complex and requires a multidisciplinary approach. Because of the rarity of…”
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S687 Timing and Durability of Dysphagia Symptom Response to Dupilumab in Patients With Eosinophilic Esophagitis: Post-Hoc Analysis of Part C of the LIBERTY EoE TREET Study by Dellon, Evan S., Chehade, Mirna, Bredenoord, Arjan, Spergel, Jonathan M., Xia, Changming, Tilton, Sarette T., McCann, Eilish, Pela, Tiffany, Raphael, Bram P., Jacob-Nara, Juby A., Radwan, Amr

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S649 Design of the Phase 4 REMODEL Study Assessing the Effect of Dupilumab on Esophageal Function and Remodeling in Adult Patients With Active Eosinophilic Esophagitis by Hirano, Ikuo, Cunoosamy, Danen, Dellon, Evan S., Bredenoord, Arjan, Savarino, Edoardo, Zhang, Mei, Raphael, Bram P., Pela, Tiffany, Radwan, Amr, Jacob-Nara, Juby A.

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Essential Fatty Acid Status in Surgical Infants Receiving Parenteral Nutrition With a Composite Lipid Emulsion: A Case Series by Carey, Alexandra N., Rudie, Coral, Mitchell, Paul D., Raphael, Bram P., Gura, Kathleen M., Puder, Mark

“…Infants requiring prolonged parenteral nutrition (PN) may receive intravenous (IV) lipid in the form of soybean oil, fish oil, or a composite lipid emulsion…”
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One‐year Experience With Composite Intravenous Lipid Emulsion in Children on Home Parenteral Nutrition by Raphael, Bram P., Mitchell, Paul D., Carey, Alexandra, Gura, Kathleen M., Puder, Mark

“…ABSTRACT Background: Composite lipid emulsion (CLE) composed of soybean oil, medium‐chain triglycerides, olive oil, and fish oil is approved in the US for…”
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Prevention and treatment of intestinal failure-associated liver disease in children by Raphael, Bram P, Duggan, Christopher

“…Intestinal failure-associated liver disease (IFALD), a serious complication occurring in infants, children, and adults exposed to long-term parenteral…”
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Pediatric Gastrointestinal Histopathology in Patients With Tetratricopeptide Repeat Domain 7A (TTC7A) Germline Mutations: A Rare Condition Leading to Multiple Intestinal Atresias, Severe Combined Immunodeficiency, and Congenital Enteropathy by Dannheim, Katelyn, Ouahed, Jodie, Field, Michael, Snapper, Scott, Raphael, Bram P., Glover, Sarah C., Bishop, Phyllis R., Bhesania, Natalie, Kamin, Daniel, Thiagarajah, Jay, Goldsmith, Jeffrey D.

“…Mutations in the tetratricopeptide repeat domain 7A (TTC7A) gene are a rare cause of congenital enteropathy that can result in significant morbidity. TTC7A…”
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Growth in Infants and Children With Intestinal Failure‐associated Liver Disease Treated With Intravenous Fish Oil by Raphael, Bram P., Mitchell, Paul D., Gura, Kathleen M., Potemkin, Alexis K., Squires, Robert H., Puder, Mark, Duggan, Christopher P.

“…ABSTRACT Background: Infants with intestinal failure (IF) and IF‐associated liver disease (IFALD) are at risk for poor somatic growth because of increased…”
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Antibiotic Susceptibility and Therapy in Central Line Infections in Pediatric Home Parenteral Nutrition Patients by Raphael, Bram P., Fournier, Greg, McLaughlin, Sarah R., Puder, Mark, Jones, Sarah, Flett, Kelly B.

“…ABSTRACT Background: Patients receiving home parenteral nutrition (HPN) are at high‐risk for central line‐associated bloodstream infections (CLABSI). There are…”
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Growth in Infants and Children With Intestinal Failure-associated Liver Disease Treated With Intravenous Fish Oil by Raphael, Bram P, Mitchell, Paul D, Gura, Kathleen M, Potemkin, Alexis K, Squires, Robert H, Puder, Mark, Duggan, Christopher P

“…Infants with intestinal failure (IF) and IF-associated liver disease (IFALD) are at risk for poor somatic growth because of increased metabolic demands,…”
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Necrotizing enterocolitis is associated with earlier achievement of enteral autonomy in children with short bowel syndrome by Sparks, Eric A, Khan, Faraz A, Fisher, Jeremy G, Fullerton, Brenna S, Hall, Amber, Raphael, Bram P, Duggan, Christopher, Modi, Biren P, Jaksic, Tom

“…Abstract Purpose Necrotizing enterocolitis (NEC) remains one of the most common underlying diagnoses of short bowel syndrome (SBS) in children. The…”
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Virtual Telemedicine Visits in Pediatric Home Parenteral Nutrition Patients: A Quality Improvement Initiative by Raphael, Bram P, Schumann, Caitlin, Garrity-Gentille, Sara, McClelland, Jennifer, Rosa, Carolyn, Tascione, Christina, Gallotto, Mary, Takvorian-Bené, Melissa, Carey, Alexandra N, McCarthy, Patrick, Duggan, Christopher, Ozonoff, Al

“…Despite being less costly than prolonged hospitalization, home parenteral nutrition (HPN) is associated with high rates of post-discharge complications,…”
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