Pulmonary hypertension associated with portal thrombosis

Pulmonary hypertension accompanying portal hypertension is a rare cause of plexogenic pulmonary arteriopathy, which etiopathogenesis is still unknown. The case report presented is that of a young man who underwent surgery at age 8 for ruptured esophageal varices associated with portal thrombosis, an...

Full description

Saved in:

Bibliographic Details
Published in:	European journal of respiratory diseases Vol. 66; no. 3; p. 224
Main Authors:	Flemale, A, Sabot, J P, Popijn, M, Procureur, M, Urbain, G, Dierckx, J P, Delmez, J P
Format:	Journal Article
Language:	English
Published:	Denmark 01-03-1985
Subjects:	Adult Esophageal and Gastric Varices - pathology Gastrointestinal Hemorrhage - pathology Humans Hypertension, Portal - complications Hypertension, Portal - physiopathology Hypertension, Pulmonary - etiology Hypertension, Pulmonary - physiopathology Portal Vein Thrombosis - complications Thrombosis - physiopathology
Online Access:	Get more information
Tags:	Add Tag No Tags, Be the first to tag this record!

Description
Summary:	Pulmonary hypertension accompanying portal hypertension is a rare cause of plexogenic pulmonary arteriopathy, which etiopathogenesis is still unknown. The case report presented is that of a young man who underwent surgery at age 8 for ruptured esophageal varices associated with portal thrombosis, and who later developed pulmonary hypertension which led to death at age 21. Hepatic filtration shunt and similarity of this syndrome to pulmonary hypertension subsequent to ingestion of the appetite depressant Aminorex suggest the hypothesis that pressor substances, not detoxified by the liver, are released into the pulmonary circulation.
ISSN:	0106-4339