Klippel-Trenaunay-Weber syndrome variant

We describe a patient with soft-tissue and bony hypertrophy of all four limbs. The upper limbs were erythematous, with associated finger deformity. The soft-tissue irregular hypertrophy and engorgement subsided when the limbs were elevated. Retinal examination showed large, dilated, tortuous veins,...

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Bibliographic Details
Published in:	Canadian journal of ophthalmology Vol. 24; no. 5; p. 223
Main Authors:	Kumar, A, Pakrasi, S, Kunte, R
Format:	Journal Article
Language:	English
Published:	England 01-08-1989
Subjects:	Adult Angiomatosis - diagnosis Arteriovenous Malformations - complications Bone Diseases - complications Extremities - pathology Fluorescein Angiography Humans Hypertrophy - complications Klippel-Trenaunay-Weber Syndrome - diagnosis Male Retinal Diseases - complications Syndactyly - complications Syndrome
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Summary:	We describe a patient with soft-tissue and bony hypertrophy of all four limbs. The upper limbs were erythematous, with associated finger deformity. The soft-tissue irregular hypertrophy and engorgement subsided when the limbs were elevated. Retinal examination showed large, dilated, tortuous veins, with no dye leakage on fluorescein angiography. We feel that this case represents an unusual variant of the Klippel-Trenaunay-Weber syndrome.
ISSN:	0008-4182