Search Results - "PEIXIANG WANG"

Degradation of salicylhydroxamic acid in mineral beneficiation wastewater by dielectric barrier discharge and La-Fe3O4-doped activated carbon: Parametric optimization, kinetics, activation process, and transformation pathway by Dong, Bingyan, Wang, Peixiang, Li, Zhendong, Tan, Yanwen

“…In this study, the degradation of salicylhydroxamic acid (SHA) in industrial beneficiation wastewater was investigated using dielectric barrier discharge (DBD)…”
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Ppp1r3d deficiency preferentially inhibits neuronal and cardiac Lafora body formation in a mouse model of the fatal epilepsy Lafora disease by Israelian, Lori, Nitschke, Silvia, Wang, Peixiang, Zhao, Xiaochu, Perri, Ami M., Lee, Jennifer P.Y., Verhalen, Brandy, Nitschke, Felix, Minassian, Berge A.

“…Mammalian glycogen chain lengths are subject to complex regulation, including by seven proteins (protein phosphatase‐1 regulatory subunit 3, PPP1R3A through…”
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RAB-10 Promotes EHBP-1 Bridging of Filamentous Actin and Tubular Recycling Endosomes by Wang, Peixiang, Liu, Hang, Wang, Yu, Liu, Ou, Zhang, Jing, Gleason, Adenrele, Yang, Zhenrong, Wang, Hui, Shi, Anbing, Grant, Barth D

“…EHBP-1 (Ehbp1) is a conserved regulator of endocytic recycling, acting as an effector of small GTPases including RAB-10 (Rab10). Here we present evidence that…”
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An EHBP-1-SID-3-DYN-1 axis promotes membranous tubule fission during endocytic recycling by Gao, Jinghu, Zhao, Linyue, Luo, Qian, Liu, Shuyao, Lin, Ziyang, Wang, Peixiang, Fu, Xin, Chen, Juan, Zhang, Hongjie, Lin, Long, Shi, Anbing

“…The ACK family tyrosine kinase SID-3 is involved in the endocytic uptake of double-stranded RNA. Here we identified SID-3 as a previously unappreciated…”
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Laforin targets malin to glycogen in Lafora progressive myoclonus epilepsy by Mitra, Sharmistha, Chen, Baozhi, Wang, Peixiang, Chown, Erin E, Dear, Mathew, Guisso, Dikran R, Mariam, Ummay, Wu, Jun, Gumusgoz, Emrah, Minassian, Berge A

“…Glycogen is the largest cytosolic macromolecule and is kept in solution through a regular system of short branches allowing hydration. This structure was…”
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Skeletal Muscle Glycogen Chain Length Correlates with Insolubility in Mouse Models of Polyglucosan-Associated Neurodegenerative Diseases by Sullivan, Mitchell A., Nitschke, Silvia, Skwara, Evan P., Wang, Peixiang, Zhao, Xiaochu, Pan, Xiao S., Chown, Erin E., Wang, Travis, Perri, Ami M., Lee, Jennifer P.Y., Vilaplana, Francisco, Minassian, Berge A., Nitschke, Felix

“…Lafora disease (LD) and adult polyglucosan body disease (APBD) are glycogen storage diseases characterized by a pathogenic buildup of insoluble glycogen…”
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PTG protein depletion rescues malin-deficient Lafora disease in mouse by Turnbull, Julie, Epp, Jonathan R., Goldsmith, Danielle, Zhao, Xiaochu, Pencea, Nela, Wang, Peixiang, Frankland, Paul W., Ackerley, Cameron A., Minassian, Berge A.

“…Ubiquitin ligases regulate quantities and activities of target proteins, often pleiotropically. The malin ubiquitin E3 ligase is reported to regulate…”
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Glycogen synthase downregulation rescues the amylopectinosis of murine RBCK1 deficiency by Nitschke, Silvia, Sullivan, Mitchell A, Mitra, Sharmistha, Marchioni, Charlotte R, Lee, Jennifer P Y, Smith, Brandon H, Ahonen, Saija, Wu, Jun, Chown, Erin E, Wang, Peixiang, Petković, Sara, Zhao, Xiaochu, DiGiovanni, Laura F, Perri, Ami M, Israelian, Lori, Grossman, Tamar R, Kordasiewicz, Holly, Vilaplana, Francisco, Iwai, Kazuhiro, Nitschke, Felix, Minassian, Berge A

“…Longer glucan chains tend to precipitate. Glycogen, by far the largest mammalian glucan and the largest molecule in the cytosol with up to 55 000 glucoses,…”
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Lafora disease in miniature Wirehaired Dachshunds by Swain, Lindsay, Key, Gill, Tauro, Anna, Ahonen, Saija, Wang, Peixiang, Ackerley, Cameron, Minassian, Berge A, Rusbridge, Clare

“…Lafora disease (LD) is an autosomal recessive late onset, progressive myoclonic epilepsy with a high prevalence in the miniature Wirehaired Dachshund. The…”
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Study on the Polymer Morphology and Electro-Optical Performance of Acrylate/Epoxy Resin-Based Polymer-Stabilized Liquid Crystals Based on Stepwise Photopolymerization by Wu, Yishuo, Shang, Guangyang, Ma, Cong, Shi, Yingjie, Song, Zhexu, Wang, Peixiang, Gao, Yanzi, Wang, Qian, Yu, Meina, Xiao, Jiumei, Zou, Cheng

“…Stepwise photopolymerization is a miraculous strategy modulating the polymer skeleton and electro-optical properties of light modulators based on liquid…”
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Abnormal glycogen chain length pattern, not hyperphosphorylation, is critical in Lafora disease by Nitschke, Felix, Sullivan, Mitchell A, Wang, Peixiang, Zhao, Xiaochu, Chown, Erin E, Perri, Ami M, Israelian, Lori, Juana‐López, Lucia, Bovolenta, Paola, Rodríguez de Córdoba, Santiago, Steup, Martin, Minassian, Berge A

“…Lafora disease (LD) is a fatal progressive epilepsy essentially caused by loss‐of‐function mutations in the glycogen phosphatase laforin or the ubiquitin E3…”
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Early-onset Lafora body disease by TURNBULL, Julie, GIRARD, Jean-Marie, TYAGI, Atul, YAN LIU, PENCEA, Nela, XIAOCHU ZHAO, SCHERER, Stephen W, ACKERLEY, Cameron A, MINASSIAN, Berge A, LOHI, Hannes, CHAN, Elayne M, PEIXIANG WANG, TIBERIA, Erica, OMER, Salah, AHMED, Mushtaq, BENNETT, Christopher, CHAKRABARTY, Aruna

“…The most common progressive myoclonus epilepsies are the late infantile and late infantile-variant neuronal ceroid lipofuscinoses (onset before the age of 6…”
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PTG depletion removes Lafora bodies and rescues the fatal epilepsy of Lafora disease by Turnbull, Julie, DePaoli-Roach, Anna A, Zhao, Xiaochu, Cortez, Miguel A, Pencea, Nela, Tiberia, Erica, Piliguian, Mark, Roach, Peter J, Wang, Peixiang, Ackerley, Cameron A, Minassian, Berge A

“…Lafora disease is the most common teenage-onset neurodegenerative disease, the main teenage-onset form of progressive myoclonus epilepsy (PME), and one of the…”
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Glycogen hyperphosphorylation underlies lafora body formation by Turnbull, Julie, Wang, Peixiang, Girard, Jean-Marie, Ruggieri, Alessandra, Wang, Tony J., Draginov, Arman G., Kameka, Alexander P., Pencea, Nela, Zhao, Xiaochu, Ackerley, Cameron A., Minassian, Berge A.

“…Objective: Glycogen, the largest cytosolic macromolecule, acquires solubility, essential to its function, through extreme branching. Lafora bodies are…”
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Ghrelin Through GHSR1a and OX1R Heterodimers Reveals a Gαs-cAMP-cAMP Response Element Binding Protein Signaling Pathway in Vitro by Xue, Qingjie, Bai, Bo, Ji, Bingyuan, Chen, Xiaoyu, Wang, Chunmei, Wang, Peixiang, Yang, Chunqing, Zhang, Rumin, Jiang, Yunlu, Pan, Yanyou, Cheng, Baohua, Chen, Jing

“…Growth hormone secretagogue receptor 1α (GHSR1a) and Orexin 1 receptor (OX1R) are involved in various important physiological processes, and have many similar…”
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Canine Lafora Disease: An Unstable Repeat Expansion Disorder by von Klopmann, Thilo, Ahonen, Saija, Espadas-Santiuste, Irene, Matiasek, Kaspar, Sanchez-Masian, Daniel, Rupp, Stefan, Vandenberghe, Helene, Rose, Jeremy, Wang, Travis, Wang, Peixiang, Minassian, Berge Arakel, Rusbridge, Clare

“…Canine Lafora disease is a recessively inherited, rapidly progressing neurodegenerative disease caused by the accumulation of abnormally constructed insoluble…”
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Increased Laforin and Laforin Binding to Glycogen Underlie Lafora Body Formation in Malin-deficient Lafora Disease by Tiberia, Erica, Turnbull, Julie, Wang, Tony, Ruggieri, Alessandra, Zhao, Xiao-Chu, Pencea, Nela, Israelian, Johan, Wang, Yin, Ackerley, Cameron A., Wang, Peixiang, Liu, Yan, Minassian, Berge A.

“…Background: Laforin deficiency causes glycogen hyperphosphorylation, which converts glycogen to aggregate-prone poorly branched polyglucosans. Malin deficiency…”
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Correction to: Nationwide genetic testing towards eliminating Lafora disease from Miniature Wirehaired Dachshunds in the United Kingdom by Ahonen, Saija, Seath, Ian, Rusbridge, Clare, Holt, Susan, Key, Gill, Wang, Travis, Wang, Peixiang, Minassian, Berge A

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GYS1 or PPP1R3C deficiency rescues murine adult polyglucosan body disease by Chown, Erin E., Wang, Peixiang, Zhao, Xiaochu, Crowder, Justin J., Strober, Jordan W., Sullivan, Mitchell A., Xue, Yunlin, Bennett, Cody S., Perri, Ami M., Evers, Bret M., Roach, Peter J., Depaoli‐Roach, Anna A., Akman, H. Orhan, Pederson, Bartholomew A., Minassian, Berge A.

“…Objective Adult polyglucosan body disease (APBD) is an adult‐onset neurological variant of glycogen storage disease type IV. APBD is caused by recessive…”
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POU Homeodomain Protein Oct-1 Functions as a Sensor for Cyclic AMP by Wang, Peixiang, Wang, Qinghua, Sun, Jane, Wu, Jing, Li, Hang, Zhang, Nina, Huang, Yachi, Su, Brenda, Li, Ren-ke, Liu, Ling, Zhang, Yi, Elsholtz, Harry P., Hu, Jim, Gaisano, Herbert Y., Jin, Tianru

“…Cyclic AMP is a fundamentally important second messenger for numerous peptide hormones and neurotransmitters that control gene expression, cell proliferation,…”
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