Search Results - "Naehrlich, L"

Drug desensitization to lumacaftor/ivacaftor: A fast lane to drug tolerance by Westhoff, J, Barth, S, Naehrlich, L

“…We present the case of a girl (now 11 years and 9 months old) with cystic fibrosis (F508del homozygote), who developed pruritic rash and urticaria six days…”
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Isolated heart transplantation in an adolescent with cystic fibrosis-A case report by Westhoff, J, Barth, S, Bagheri-Potthoff, A, Skrzypek, S, Naehrlich, L

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Be flexible when unscrewing: Screw aspiration in a 15‐year‐old girl by Westhoff, J., Alexanidou, E., Hofmann, J., Laffolie, J., Naehrlich, L.

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Chronic inhaled antibiotic therapy in people with cystic fibrosis with Pseudomonas aeruginosa infection in Germany by Naehrig, S., Schulte-Hubbert, B., Hafkemeyer, S., Hammermann, J., Dumke, M., Sieber, S., Naehrlich, L.

“…Several clinical guidelines recommend chronic inhaled therapy for pwCF (people with cystic fibrosis) and chronic Pseudomonas aeruginosa infection of the lungs…”
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Risk factors for cystic fibrosis arthropathy: Data from the German cystic fibrosis registry by Grehn, Claudia, Dittrich, A.-M., Wosniok, J., Holz, F., Hafkemeyer, S., Naehrlich, L., Schwarz, C.

“…•Cystic fibrosis arthropathy prevalence increases with age, 8.4 % of ≥18 years have cystic fibrosis arthropathy.•Cystic fibrosis arthropathy is associated with…”
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Concordant genotype of upper and lower airways P aeruginosa and S aureus isolates in cystic fibrosis by Mainz, J G, Naehrlich, L, Schien, M, Käding, M, Schiller, I, Mayr, S, Schneider, G, Wiedemann, B, Wiehlmann, L, Cramer, N, Pfister, W, Kahl, B C, Beck, J F, Tümmler, B

“…Lower airway (LAW) infection with Pseudomonas aeruginosa and Staphylococcus aureus is the leading cause of morbidity in cystic fibrosis (CF). The upper airways…”
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ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals by De Wachter, E, De Boeck, K, Sermet-Gaudelus, I, Simmonds, NJ, Munck, A, Naehrlich, L, Barben, J, Boyd, C, Veen, SJ, Carr, SB, Fajac, I, Farrell, PM, Girodon, E, Gonska, T, Grody, WW, Jain, M, Jung, A, Kerem, E, Raraigh, KS, van Koningsbruggen-Rietschel, S, Waller, MD, Southern, KW, Castellani, C

“…•Advantages and challenges of a dedicated patient registry for people with CFTR-RD.•The CFTR-RD risk for infants with a CRMS/CFSPID designation.•Peculiarities…”
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WS10.5 Influence of tobacco smoke on CFTR function by Bagheri-Hanson, A, Rueckes-Nilges, C, Naehrlich, L

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Importance to question sinonasal symptoms and to perform rhinoscopy and rhinomanometry in cystic fibrosis patients by Bock, J.M., Schien, M., Fischer, C., Naehrlich, L., Kaeding, M., Guntinas‐Lichius, O., Gerber, A., Arnold, C., Mainz, J.G.

“…Summary Objectives Cystic fibrosis (CF) patients almost regularly reveal sinonasal pathology. The purpose of this study was to assess association between…”
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Sweat testing practices in German cystic fibrosis centres by Naehrlich, L

“…Surveys in USA and UK have shown inconsistencies between practice of sweat testing and guidelines of the National Committee for Clinical Laboratory Standards…”
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325 Isolated heart transplantation for left heart failure in a CF patient by Barth, S, Bagheri-Hanson, A, Mazhari, N, Naehrlich, L

“…Background Myocardial fibrosis (MF) and necrosis of the left heart has been reported as CF-related complication, especially in postmortem case series (Witt et…”
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EPS5.2 Genetic epidemiology of CFTR nonsense mutations across Europe by McKone, E.F, Jackson, A, Zolin, A, De Boeck, K, van Rens, J, Ariti, C, Keogh, R, Naehrlich, L

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Sweat testing in CF by Naehrlich, Lutz

“…[...]only 2 of the 10 patients (sweat chloride levels of 34 and 45 mmol/l) fulfilled the clinical criteria and laboratory evidence of CFTR dysfunction,…”
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WS17.5 Patients with cystic fibrosis and the R117H mutation: The European experience by Naehrlich, L, Zolin, A, Colombo, C, De Boeck, K, Kashirskaya, N, Olesen, H.V

“…Objectives The R117H mutation is common among CF-patients in Europe and a CFTR modulating therapy has been investigated. Methods To describe clinical…”
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WS11.3 Cystic fibrosis survival and socioeconomic status across Europe by McKone, E.F, Ariti, C, Jackson, A, Zolin, A, Carr, S.B, van Rens, J, Colomb, V, Lemonnier, L, Keogh, R, Naehrlich, L

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WS3.4 Clostridium difficile, but not Giardia lamblia, is a frequent finding in the stool of CF-patients by Bagheri-Behrouzi, A, Zimmermann, A, Naehrlich, L

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294 Individualized vitamin A supplementation for patients with cystic fibrosis by Naehrlich, L, Simon, A, Brei, C, Krawinkel, M

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271 Iodine deficiency and subclinical hyperthyroidism are common in cystic fibrosis patients by Naehrlich, L, Dorr, H.-G, Bagheri-Behrouzi, A, Rauch, M

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P063 Survival analysis of the German Cystic Fibrosis Registry by Naehrlich, L.

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WS6.2 Anti-inflammatory pulmonal therapy of CF patients with amitriptyline and placebo – a randomised, double-blind, placebo-controlled Phase IIb multicenter cohort study by Adams, C, Mainz, J.G, Naehrlich, L, Engel, C, Herrmann, G, Icheva, V, Graepler-Mainka, U, Heyder, S, Stern, M, Döring, G, Gulbins, E, Riethmueller, J

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