Search Results - "Morell, G."
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Experimental characterization of a self-adaptive shape memory alloy cooling approach to regulate temperature under varying heat loads
Published in International journal of heat and mass transfer (01-08-2019)“…•Self-adaptive cooling fins based on two-way trained Shape Memory Alloys (SMA).•The set of conditions for proper operation are defined analytically.•The impact…”
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Field emission properties of carbon nanowalls prepared by RF magnetron sputtering
Published in Applied physics. A, Materials science & processing (01-05-2019)“…Carbon nanowalls were prepared on silicon substrates by radio frequency magnetron sputtering under an argon–hydrogen mixture, at different hydrogen fluxes and…”
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Fabry disease and the skin: data from FOS, the Fabry outcome survey
Published in British journal of dermatology (1951) (01-08-2007)“…Summary Background Fabry disease (also known as Anderson–Fabry disease) is a rare, X‐linked lysosomal storage disorder that is characterized by accumulation…”
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Fabry disease in children and response to enzyme replacement therapy: results from the Fabry Outcome Survey
Published in Clinical genetics (01-05-2012)“…Ramaswami U, Parini R, Pintos‐Morell G, Kalkum G, Kampmann C, Beck M, on behalf of the FOS Investigators. Fabry disease in children and response to enzyme…”
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Enzyme replacement therapy with agalsidase alfa in children with Fabry disease
Published in Acta Paediatrica (01-01-2007)“…Aim: To assess the effects of enzyme replacement therapy (ERT) in children with Fabry disease. Methods: Safety and efficacy of ERT with agalsidase alfa, 0.2…”
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Graphene/semiconductor silicon modified BiFeO3/indium tin oxide ferroelectric photovoltaic device for transparent self-powered windows
Published in Applied physics letters (10-08-2015)“…We report photovoltaic response of highly transparent graphene/BiFe0.95Si0.05O3 (BFSiO)/ITO/glass derived from bottom-up spin coating technique. The device…”
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Wettability of hydrogenated tetrahedral amorphous carbon
Published in Diamond and related materials (2009)“…The wettability and surface energy of hydrogenated amorphous carbon films (a-C:H) elaborated by distributed electron cyclotron resonance plasma were studied by…”
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Standardising clinical outcomes measures for adult clinical trials in Fabry disease: A global Delphi consensus
Published in Molecular genetics and metabolism (01-04-2021)“…Recent years have witnessed a considerable increase in clinical trials of new investigational agents for Fabry disease (FD). Several trials investigating…”
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Synthesis, Optical, and Magnetic Properties of Graphene Quantum Dots and Iron Oxide Nanocomposites
Published in Advances in materials science and engineering (01-01-2018)“…The combination of nanomaterial graphene quantum dots (GQDs) with magnetic nanoparticles offers a unique set of optical and magnetic properties for future…”
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Bactericide and bacterial anti-adhesive properties of the nanocrystalline diamond surface
Published in Diamond and related materials (01-02-2012)“…We performed a systematic study of the bactericide and bacterial anti-adhesive properties of nanocrystalline diamond (NCD) and microcrystalline diamond (MCD)…”
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Carbon nanotubes coated with diamond nanocrystals and silicon carbide by hot-filament chemical vapor deposition below 200°C substrate temperature
Published in Carbon (New York) (01-08-2014)“…Multi-walled carbon nanotubes (MWCNTs) dispersed onto a silicon substrate have been coated with diamond nanocrystals (DNC) and silicon carbide (SiC) from solid…”
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Synthesis of diamond at sub 300 °C substrate temperature
Published in Diamond and related materials (01-11-2007)“…Sulfur-assisted hot-filament chemical vapor deposition (HFCVD) was employed to grow nanocrystalline diamond at low substrate temperature, ∼ 300 °C, on…”
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Fabry disease in Spain: description of Spanish patients and a comparison with other European countries using data from the Fabry Outcome Survey (FOS)
Published in International journal of clinical practice (Esher) (01-08-2011)“…Fabry disease (FD) is an X-chromosome-linked transmitted lysosomal storage disorder as a result of the deficient activity of enzyme α-galactosidase A. This…”
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Clinical manifestations of Fabry disease in children : Data from the Fabry Outcome Survey
Published in Acta pædiatrica (Oslo) (2006)“…Fabry disease is a rare X-linked disorder caused by deficient activity of the enzyme alpha-galactosidase A. This produces progressive lysosomal accumulation of…”
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Training competencies in adult metabolic medicine: A survey of working adult metabolic medicine physicians
Published in JIMD reports (01-09-2022)“…The rapid expansion of the number of adult patients with inherited metabolic diseases (IMDs) has created demand for physicians with expertise in the field of…”
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Studies of photovoltaic properties of nanocrystalline thin films of CdS–CdTe
Published in Journal of alloys and compounds (13-10-2011)“…Quenching of room temperature photoluminescence of CdS–CdTe thin film as compared to CdTe nanocrystals. [Display omitted] ► Nanocrystals of CdS and CdTe of 7…”
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Conformal coating of ferroelectric oxides on carbon nanotubes
Published in Europhysics letters (01-01-2012)“…Nano-size barium strontium titanate Ba0.7Sr0.3TiO3 (BST) maize-bead–like structures were conformally coated on bamboo-like carbon nanotubes (BCNTs) grown on…”
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Therapeutic goals in the treatment of Fabry disease
Published in Genetics in medicine (01-11-2010)“…Fabry disease is a progressive multiorgan, multisystem disorder that is caused by a deficiency in the lysosomal enzyme α-galactosidase A. Serious renal,…”
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Synthesis, structure, and field emission properties of sulfur-doped nanocrystalline diamond
Published in Journal of materials science. Materials in electronics (01-06-2006)“…Issue Title: Special Issue: Carbon Based Electronics The synthesis and properties of sulfur-doped nanocrystalline diamond films were investigated. The films…”
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Genesis of diamond nanotubes from carbon nanotubes
Published in Europhysics letters (01-07-2011)“…We synthesized sp3-rich crystalline tubular structures, referred to as diamond nanotubes (DNTs), by hot-filament chemical vapor deposition and characterized…”
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