Search Results - "Monestrol, Isabelle de"

Impact of lumacaftor/ivacaftor on the bacterial and fungal respiratory pathogens in cystic fibrosis: a prospective multicenter cohort study in Sweden by Al Shakirchi, Mahasin, Sorjonen, Kimmo, Hjelte, Lena, Klingspor, Lena, Bergman, Peter, Ericson, Petrea, Svedberg, Marcus, Lindberg, Ulrika, Hansen, Christine, Monestrol, Isabelle de

“…A significant decline in pulmonary exacerbation rates has been reported in CF patients homozygous for F508del treated with lumacaftor/ivacaftor. However, it is…”
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Clinical characteristics of SARS-CoV-2 infection in children with cystic fibrosis: An international observational study by Bain, Robert, Cosgriff, Rebecca, Zampoli, Marco, Elbert, Alexander, Burgel, Pierre-Régis, Carr, Siobhán B, Castaños, Claudio, Colombo, Carla, Corvol, Harriet, Faro, Albert, Goss, Christopher H, Gutierrez, Hector, Jung, Andreas, Kashirskaya, Nataliya, Marshall, Bruce C, Melo, Joel, Mondejar-Lopez, Pedro, de Monestrol, Isabelle, Naehrlich, Lutz, Padoan, Rita, Pastor-Vivero, Maria Dolores, Rizvi, Samar, Salvatore, Marco, Filho, Luiz Vicente Ribeiro Ferreira da Silva, Brownlee, Keith G, Haq, Iram J, Brodlie, Malcolm

“…The presence of co-morbidities, including underlying respiratory problems, has been identified as a risk factor for severe COVID-19 disease. Information on the…”
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Clinical, economic, and societal burden of cystic fibrosis and the impact of the CFTR modulator, lumacaftor/ivacaftor: an assessment using linked registry data in Sweden by Lindblad, Anders, Monestrol, Isabelle de, Gilljam, Marita, Krantz, Christina, McGarry, Lisa J, Banefelt, Jonas, Aldvén, Martina

“…We aimed to describe the clinical, economic, and societal burdens of cystic fibrosis (CF) and impact of CF transmembrane conductance regulator modulator…”
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A 16-year retrospective study on fungal prevalence and diversity in patients with cystic fibrosis: Candida dubliniensis was associated with a decline in lung function by Al Shakirchi, Mahasin, Klingspor, Lena, Bergman, Peter, Hjelte, Lena, de Monestrol, Isabelle

“…•Fungal prevalence and diversity in the cystic fibrosis (CF) airways increased over time.•Candida dubliniensis in the CF airways was associated with a decline…”
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Effect of allergic bronchopulmonary aspergillosis on FEV1 in children and adolescents with cystic fibrosis: a European Cystic Fibrosis Society Patient Registry analysis by Kaditis, Athanasios G, Miligkos, Michael, Bossi, Anna, Colombo, Carla, Hatziagorou, Elpis, Kashirskaya, Nataliya, de Monestrol, Isabelle, Thomas, Muriel, Mei-Zahav, Meir, Chrousos, George, Zolin, Anna

“…ObjectiveTo evaluate the effect of allergic bronchopulmonary aspergillosis (ABPA) on FEV1 percent predicted in children and adolescents with cystic…”
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Does newborn screening influence the young cystic fibrosis cohort included in national registries? by De Boeck, Kris, Munck, Anne, de Monestrol, Isabelle, Gulmans, Vincent, Lemonnier, Lydie, Middleton, Peter G, Wanyama, Simeon, Thomas, Muriel

“…Cystic fibrosis newborn screening (NBS), has not yet become a reality in all countries. We therefore compared the demographic and clinical characteristics of…”
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The Effects of Aspergillus fumigatus Colonization on Lung Function in Patients with Cystic Fibrosis by Al Shakirchi, Mahasin, Sorjonen, Kimmo, Klingspor, Lena, Bergman, Peter, Hjelte, Lena, de Monestrol, Isabelle

“…Aspergillus fumigatus is commonly isolated from CF airways. However, the impact on CF lung progression is not completely understood. In this study, using a…”
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Telemedicine and home spirometry in cystic fibrosis: A prospective multicenter study by Medbo, Jakob, Imberg, Henrik, Hansen, Christine, Krantz, Christina, Monestrol, Isabelle, Svedberg, Marcus

“…Objectives Telehealth and home spirometry feasibility for children has been established, but their impact on cystic fibrosis (CF) disease progression remains…”
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Development and clinical implementation of an LC-HRMS method for ivacaftor, lumacaftor, tezacaftor and elexacaftor in human plasma and breast milk by Hansson, Anna B., Wadström, Hjalmar, Eliasson, Erik, Al Shakirchi, Mahasin, de Monestrol, Isabelle, Barclay, Victoria

“…The four cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators, ivacaftor, lumacaftor, tezacaftor, and elexacaftor, have revolutionised…”
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Antibiotic hypersensitivity in cystic fibrosis – Low frequency of anaphylaxis over 16 000 courses by Kowalik, Aleksandra, Monestrol, Isabelle, Sorjonen, Kimmo, Brockow, Knut, Gülen, Theo

“…Aims Drug hypersensitivity reactions (DHR) to antibiotics are common and a substantial issue in managing patients with cystic fibrosis (CF). This study aimed…”
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Changing epidemiology of the respiratory bacteriology of patients with cystic fibrosis–data from the European cystic fibrosis society patient registry by Hatziagorou, Elpis, Orenti, Annalisa, Drevinek, Pavel, Kashirskaya, Nataliya, Mei-Zahav, Meir, De Boeck, Kris

“…AbstractBackgroundMonitoring changes in the epidemiology of cystic fibrosis (CF) pathogens is essential for clinical research, quality improvement, and…”
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Ursodeoxycholic acid and liver disease associated with cystic fibrosis: A multicenter cohort study by Colombo, Carla, Alicandro, Gianfranco, Oliver, Mark, Lewindon, Peter J, Ramm, Grant A, Ooi, Chee Y., Alghisi, Federico, Kashirskaya, Nataliya, Kondratyeva, Elena, Corti, Fabiola, Padoan, Rita, Asherova, Irina, Evans, Helen, de Monestrol, Isabelle, Strandvik, Birgitta, Lindblad, Anders

“…•Incidence of liver outcome evaluated in UDCA prescribing vs. non-prescribing centers.•No significant difference in cumulative incidence of portal hypertension…”
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Experiences of Individuals Awaiting Lung Transplantation by Skogeland, Ulrika, de Monestrol, Isabelle, Godskesen, Tove E

“…Lung transplantation is an established intervention for patients with advanced and life-threatening respiratory disease. Unfortunately, the shortage of organ…”
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WS18.1 Waiting for lung transplant, manifold experiences: a literature review by Skogeland, U., de Monestrol, I., Godskesen, T.

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Characterization of CFTR mutations in people with cystic fibrosis and severe liver disease who are not eligible for CFTR modulators by Colombo, Carla, Ramm, Grant A, Lindblad, Anders, Corti, Fabiola, Porcaro, Luigi, Alghisi, Federico, Asherova, Irina, Evans, Helen, Kashirskaya, Nataliya, Kondratyeva, Elena, Lewindon, Peter J, de Monestrol, Isabelle, Oliver, Mark, Ooi, Chee Y., Padoan, Rita, Shankar, Sahana, Alicandro, Gianfranco

“…•Among 171 patients with severe CFLD, 19 (11.1%) were not eligible for CFTR modulators.•All ineligible patients carried at least one mutation leading to…”
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Effect of allergic bronchopulmonary aspergillosis on FEV 1 in children and adolescents with cystic fibrosis: a European Cystic Fibrosis Society Patient Registry analysis by Kaditis, Athanasios G, Miligkos, Michael, Bossi, Anna, Colombo, Carla, Hatziagorou, Elpis, Kashirskaya, Nataliya, de Monestrol, Isabelle, Thomas, Muriel, Mei-Zahav, Meir, Chrousos, George, Zolin, Anna

“…To evaluate the effect of allergic bronchopulmonary aspergillosis (ABPA) on FEV percent predicted in children and adolescents with cystic fibrosis…”
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COVID-19 vaccine prioritisation for people with cystic fibrosis by Carr, Siobhán B, Cosgriff, Rebecca, Harutyunyan, Satenik, Middleton, Peter G, Ruseckaite, Rasa, Ahern, Susannah, Daneau, Géraldine, Filho, Luiz Vicente R F da Silva, Stephenson, Anne L, Cheng, Stephanie Y, Melo, Joel, Corvol, Harriet, Burgel, Pierre-Régis, Nährlich, Lutz, McKone, Edward, Colombo, Carla, Salvatore, Marco, Padoan, Rita, Abdrakhmanov, Olzhas, Gulmans, Vincent, Byrnes, Catherine A, Amelina, Elena, Kondratyeva, Elena, Zhekayte, Elena, Kashirskaya, Nataliya, Zampoli, Marco, Pastor-Vivero, M Dolores, Mondejar-Lopez, Pedro, de Monestrol, Isabelle, Jung, Andeas, McClenaghan, Elliot, Brownlee, Keith, Rizvi, Samar, Goss, Christopher H, Elbert, Alexander, Faro, Albert, Gutierrez, Hector, Marshall, Bruce C

“…Cystic fibrosis (CF) is a rare genetic disease that affects several organs, but lung disease is the major cause of morbidity and mortality. The gene…”
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Factors for severe outcomes following SARS-CoV-2 infection in people with cystic fibrosis in Europe by Jung, Andreas, Orenti, Annalisa, Dunlevy, Fiona, Aleksejeva, Elina, Bakkeheim, Egil, Bobrovnichy, Vladimir, Carr, Siobhán B, Colombo, Carla, Corvol, Harriet, Cosgriff, Rebecca, Daneau, Géraldine, Dogru, Deniz, Drevinek, Pavel, Vukic, Andrea Dugac, Fajac, Isabelle, Fox, Alice, Fustik, Stojka, Gulmans, Vincent, Harutyunyan, Satenik, Hatziagorou, Elpis, Kasmi, Irena, Kayserová, Hana, Kondratyeva, Elena, Krivec, Uroš, Makukh, Halyna, Malakauskas, Kestutis, McKone, Edward F, Mei-Zahav, Meir, de Monestrol, Isabelle, Olesen, Hanne Vebert, Padoan, Rita, Parulava, Tsitsino, Pastor-Vivero, Maria Dolores, Pereira, Luísa, Petrova, Guergana, Pfleger, Andreas, Pop, Liviu, van Rens, Jacqui G, Rodic, Milan, Schlesser, Marc, Storms, Valérie, Turcu, Oxana, Woz Niacki, Lukasz, Yiallouros, Panayiotis, Zolin, Anna, Downey, Damian G, Naehrlich, Lutz

“…Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection in people with cystic fibrosis (pwCF) can lead to severe outcomes. In this observational…”
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Risk factors for forced expiratory volume in 1 s decline in European patients with cystic fibrosis: data from the European Cystic Fibrosis Society Patient Registry by Hatziagorou, Elpis, Fieuws, Steffen, Orenti, Annalisa, Naehrlich, Lutz, Krivec, Uros, Mei-Zahav, Meir, Jung, Andreas, De Boeck, Kris

“…To examine the trajectory of forced expiratory volume in 1 s (FEV ) using data from the European Cystic Fibrosis Society patient registry (ECFPR) collected…”
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Parental support for newborn screening for cystic fibrosis by de Monestrol, Isabelle, Brucefors, Agneta Bergsten, Sjöberg, Birgitta, Hjelte, Lena

“…Aim:  To describe the attitudes among parents towards including cystic fibrosis (CF) in the newborn screening programme and towards the potential knowledge of…”
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