Search Results - "Mainz, J. G."

Concordant genotype of upper and lower airways P aeruginosa and S aureus isolates in cystic fibrosis by Mainz, J G, Naehrlich, L, Schien, M, Käding, M, Schiller, I, Mayr, S, Schneider, G, Wiedemann, B, Wiehlmann, L, Cramer, N, Pfister, W, Kahl, B C, Beck, J F, Tümmler, B

“…Lower airway (LAW) infection with Pseudomonas aeruginosa and Staphylococcus aureus is the leading cause of morbidity in cystic fibrosis (CF). The upper airways…”
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Importance to question sinonasal symptoms and to perform rhinoscopy and rhinomanometry in cystic fibrosis patients by Bock, J.M., Schien, M., Fischer, C., Naehrlich, L., Kaeding, M., Guntinas‐Lichius, O., Gerber, A., Arnold, C., Mainz, J.G.

“…Summary Objectives Cystic fibrosis (CF) patients almost regularly reveal sinonasal pathology. The purpose of this study was to assess association between…”
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Pulmonary Aspergillosis in People with Cystic Fibrosis by Schwarz, C, Eschenhagen, P N, Mainz, J G, Schmidergall, T, Schuette, H, Romanowska, E

“…In the last decade, fungal respiratory diseases have been increasingly investigated for their impact on the clinical course of people with cystic fibrosis…”
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Chronic rhinosinusitis in people with cystic fibrosis-an up-to-date review from the perspective of otorhinolaryngology by Yılmaz Topçuoğlu, M, Sommerburg, O, Wielpütz, M O, Wucherpfennig, L, Hackenberg, S, Mainz, J G, Baumann, I

“…Cystic fibrosis (CF) is a complex systemic disease involving numerous organ systems. With improved treatment options and increasing life expectancy of persons…”
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Diabetes is associated with increased burden of gastrointestinal symptoms in adults with cystic fibrosis by Caley, L.R., Zagoya, C., Duckstein, F., White, H., Shimmin, D., Jones, A.M., Barrett, J., Whitehouse, J.L., Floto, R.A., Mainz, J.G., Peckham, D.G.

“…•Gastrointestinal symptoms are common in people with cystic fibrosis (pwCF).•Gastrointestinal symptoms are reported in people with diabetes…”
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Cystic fibrosis upper airways primary colonization with Pseudomonas aeruginosa: eradicated by sinonasal antibiotic inhalation by Mainz, J G, Michl, R, Pfister, W, Beck, J F

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ECFS standards of care on CFTR-related disorders: Identification and care of the disorders by Simmonds, N.J., Southern, K.W., De Wachter, E., De Boeck, K., Bodewes, F., Mainz, J.G., Middleton, P.G., Schwarz, C., Vloeberghs, V., Wilschanski, M., Bourrat, E., Chalmers, J.D., Ooi, C.Y., Debray, D., Downey, D.G., Eschenhagen, P., Girodon, E., Hickman, G., Koitschev, A., Nazareth, D., Nick, J.A., Peckham, D., VanDevanter, D., Raynal, C., Scheers, I., Waller, M.D., Sermet-Gaudelus, I., Castellani, C.

“…•CFTR-related disorders (RD) are a group of conditions caused by CFTR protein dysfunction, but to a level of dysfuncton not satisfying the diagnostic crtieria…”
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Respiratory Fungal Infections in Cystic Fibrosis: Diagnostic and Therapeutic Challenges by Schwarz, C., Mainz, J. G., Romanowska, E., Rosseau, S., Schuette, H., Martin-Souto, L., Ramirez-Garcia, A., Eschenhagen, P.

“…   Purpose of Review In cystic fibrosis (CF), the main focus in bronchopulmonary infections is on bacterial pathogens, as they significantly influence lung…”
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Use of a mobile application for self-management of pancreatic enzyme replacement therapy is associated with improved gastro-intestinal related quality of life in children with Cystic Fibrosis by Boon, M., Calvo-Lerma, J., Claes, I., Havermans, T., Asseiceira, I., Bulfamante, A., Garriga, M., Masip, E., van Schijndel, B.A.M., Fornes, V., Barreto, C., Colombo, C., Crespo, P., Vicente, S., Janssens, H., Hulst, J., Witters, P., Nobili, R., Pereira, L., Ruperto, M., Van der Wiel, E., Mainz, J.G., De Boeck, K., Ribes-Koninckx, C.

“…•There are currently no guidelines for optimal dosing of pancreatic enzyme replacement therapy.•A mobile application, the MyCyfAPP, was developed to help…”
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Sinonasal persistence of Pseudomonas aeruginosa after lung transplantation by Mainz, J.G, Hentschel, J, Schien, C, Cramer, N, Pfister, W, Beck, J.F, Tümmler, B

“…ABSTRACT We report on two CF patients who received double lung transplantation (LTX) due to Pseudomonas aeruginosa related pulmonary destruction. Prior to LTX…”
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Smell in cystic fibrosis by Lindig, J., Steger, C., Beiersdorf, N., Michl, R., Beck, J. F., Hummel, T., Mainz, J. G.

“…In cystic fibrosis (CF), the most frequent life threatening inherited disease in Caucasians, sinonasal mucosa is regularly affected by defective mucociliary…”
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Rhinosinusitis in cystic fibrosis by Mainz, J G, Gerber, A, Arnold, C, Baumann, J, Baumann, I, Koitschev, A

“…In cystic fibrosis (CF) mucociliary clearance of the entire respiratory system is impaired. This allows pathogens, such as Pseudomonas aeruginosa to persist…”
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CF Lung Disease - a German S3 Guideline: Module 2: Diagnostics and Treatment in Chronic Infection with Pseudomonas aeruginosa by Schwarz, C, Schulte-Hubbert, B, Bend, J, Abele-Horn, M, Baumann, I, Bremer, W, Brunsmann, F, Dieninghoff, D, Eickmeier, O, Ellemunter, H, Fischer, R, Grosse-Onnebrink, J, Hammermann, J, Hebestreit, H, Hogardt, M, Hügel, C, Hug, M, Illing, S, Jung, A, Kahl, B, Koitschev, A, Mahlberg, R, Mainz, J G, Mattner, F, Mehl, A, Möller, A, Muche-Borowski, C, Nüßlein, T, Puderbach, M, Renner, S, Rietschel, E, Ringshausen, F C, Schmidt, S, Sedlacek, L, Sitter, H, Smaczny, C, Tümmler, B, Vonberg, R, Wielpütz, M O, Wilkens, H, Wollschläger, B, Zerlik, J, Düesberg, U, van Koningsbruggen-Rietschel, S

“…Cystic Fibrosis (CF) is the most common autosomal-recessive genetic disease affecting approximately 8000 people in Germany. The disease is caused by mutations…”
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Coincident diagnosis of a pulmonary abscess and ascaris lumbricoides infection: a possible causal connection? by Gerber, A, Franz, C, Mainz, J G

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Pregnancy and cystic fibrosis - an overview by Michl, R K, Mues, S, Mainz, J G, Markert, U R

“…Life expectancy and quality of life of cystic fibrosis (CF) patients have been steadily increasing for many decades, due to intensified therapy and research…”
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A patient nicknamed 'saline': atypical course with cystic fibrosis by Michl, R K, Mentzel, H-J, Gerber, A, Beck, J F, Mainz, J G

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A rare differential diagnosis of acute chest pain after long-distance airplane flight by Stenzel, M, Hennig, B, Mainz, J G, Mentzel, H-J

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Acute lymphoblastic leukemia in a 10-year-old boy with cystic fibrosis - improvement of pulmonary function during chemotherapy in spite of intermittent Pseudomonas aeruginosa colonisation by Dopfer, C, Kentouche, K, Gruhn, B, Dopfer, R, Becker, S, Mentzel, H-J, Beck, J F, Mainz, J G

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Update zur Therapie der CF bei Kindern und Jugendlichen by Mainz, J. G., Schwarz, C., Jagdhuhn, M., Kurzidim, L., Eschenhagen, P.

“…Zusammenfassung Bei Erstbeschreibung der Mukoviszidose (CF) in den 1930er-Jahren verstarben die Betroffenen in der Regel im Vorschulalter an der angeborenen…”
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Atypische Mukoviszidose: Erst durch chronische Rhinosinusitis diagnostiziert by Mainz, J.G., Dornaus, S., Dopfer, C., Beck, J.F., Müller, A.

“…Zusammenfassung Wir berichten über einen 44-jährigen Ringer, der an persistierenden bronchitischen Symptomen und einer therapierefraktären chronischen…”
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