Search Results - "Mager, J."

Second International Guidelines for the Diagnosis and Management of Hereditary Hemorrhagic Telangiectasia by Faughnan, Marie E, Mager, Johannes J, Hetts, Steven W, Palda, Valerie A, Lang-Robertson, Kelly, Buscarini, Elisabetta, Deslandres, Erik, Kasthuri, Raj S, Lausman, Andrea, Poetker, David, Ratjen, Felix, Chesnutt, Mark S, Clancy, Marianne, Whitehead, Kevin J, Al-Samkari, Hanny, Chakinala, Murali, Conrad, Miles, Cortes, Daniel, Crocione, Claudia, Darling, Jama, de Gussem, Els, Derksen, Carol, Dupuis-Girod, Sophie, Foy, Patrick, Geisthoff, Urban, Gossage, James R, Hammill, Adrienne, Heimdal, Ketil, Henderson, Katharine, Iyer, Vivek N, Kjeldsen, Anette D, Komiyama, Masaki, Korenblatt, Kevin, McDonald, Jamie, McMahon, Jack, McWilliams, Justin, Meek, Mary E, Mei-Zahav, Meir, Olitsky, Scott, Palmer, Sara, Pantalone, Rose, Piccirillo, Jay F, Plahn, Beth, Porteous, Mary E M, Post, Marco C, Radovanovic, Ivan, Rochon, Paul J, Rodriguez-Lopez, Josanna, Sabba, Carlo, Serra, Marcelo, Shovlin, Claire, Sprecher, Dennis, White, Andrew J, Winship, Ingrid, Zarrabeitia, Roberto

“…Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant disease with an estimated prevalence of 1 in 5000 that is characterized by the presence of…”
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Pulmonary Vascular Complications in Hereditary Hemorrhagic Telangiectasia and the Underlying Pathophysiology by Bofarid, Sala, Hosman, Anna E, Mager, Johannes J, Snijder, Repke J, Post, Marco C

“…In this review, we discuss the role of transforming growth factor-beta (TGF-β) in the development of pulmonary vascular disease (PVD), both pulmonary…”
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Oral itraconazole for epistaxis in hereditary hemorrhagic telangiectasia: a proof of concept study by Kroon, S., Snijder, R. J., Hosman, A. E., Vorselaars, V. M.M., Disch, F. J.M, Post, M. C., Mager, J. J.

“…The inhibiting effects of itraconazole, an antifungal drug on vascular endothelial growth factor (VEGF) have recently been discovered. By inhibiting VEGF,…”
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Evolution of Pulmonary Arteriovenous Malformations: The Role of Contrast Echocardiography by Hessels, J, Kroon, S, Vorselaars, V V M, Boerman, S, Mager, J J, Post, M C

“…Pulmonary arteriovenous malformations (PAVMs) are direct connections between the pulmonary artery and the pulmonary vein, mostly associated with hereditary…”
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Second International Guidelines for the Diagnosis and Management of Hereditary Hemorrhagic Telangiectasia by Faughnan, Marie E., Mager, Johannes J., Hetts, Steven W., Palda, Valerie A., Ratjen, Felix

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Pulmonary artery pseudoaneurysm after thoracic radiation therapy: A case report and review of the literature by Maessen, Gerdinique G C, Hoffman, Thijs T W, Graat-Verboom, Lidwien L, van Leersum, Marc M, Mager, Hans-Jurgen J J

“…Pulmonary artery pseudoaneurysm (PAP) is a rare cause of hemoptysis. Potential causes include trauma, infection, or medical interventions. There is a risk of…”
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Pulmonary Arterial Hypertension and Hereditary Haemorrhagic Telangiectasia by Vorselaars, Veronique M M, Hosman, Anna E, Westermann, Cornelis J J, Snijder, Repke J, Mager, Johannes J, Goumans, Marie-Jose, Post, Marco C

“…Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant inherited disease characterised by multisystemic vascular dysplasia. Heritable pulmonary…”
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Safety of direct oral anticoagulants in patients with hereditary hemorrhagic telangiectasia by Shovlin, C L, Millar, C M, Droege, F, Kjeldsen, A, Manfredi, G, Suppressa, P, Ugolini, S, Coote, N, Fialla, A D, Geisthoff, U, Lenato, G M, Mager, H J, Pagella, F, Post, M C, Sabbà, C, Sure, U, Torring, P M, Dupuis-Girod, S, Buscarini, E

“…Hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia resulting in visceral arteriovenous malformations and smaller mucocutaneous…”
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Clinical Implications of Pulmonary Shunting on Saline Contrast Echocardiography by Velthuis, Sebastiaan, MD, PhD, Buscarini, Elisabetta, MD, PhD, Gossage, James R., MD, PhD, Snijder, Repke J., MD, Mager, Johannes J., MD, PhD, Post, Martijn C., MD, PhD

“…Pulmonary right-to-left shunting can be encountered using transthoracic contrast echocardiography (TTCE) with agitated saline. Diseases associated with…”
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Thresholds of Endoglin Expression in Endothelial Cells Explains Vascular Etiology in Hereditary Hemorrhagic Telangiectasia Type 1 by Galaris, Georgios, Montagne, Kévin, Thalgott, Jérémy H., Goujon, Geoffroy J. P. E., van den Driesche, Sander, Martin, Sabrina, Mager, Hans-Jurgen J., Mummery, Christine L., Rabelink, Ton J., Lebrin, Franck

“…Hereditary Hemorrhagic Telangiectasia type 1 (HHT1) is an autosomal dominant inherited disease characterized by arteriovenous malformations and hemorrhage…”
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Four-year survival rate in pulmonary sarcoidosis with extensive pulmonary hypertension screening by Huitema, M.P., Mathijssen, H., Bakker, A.L.M., Mager, J.J., van Houten, L., Grutters, J.C., Post, M.C.

“…Sarcoidosis is a systemic disease of unknown aetiology with significant morbidity and mortality. The PULSAR study prospectively performed cardiac analysis…”
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Intranasal Efudix reduces epistaxis in hereditary hemorrhagic telangiectasia by de Jel, D. V. C., Disch, F. J. M., Kroon, S., Mager, J. J., Verdam, F. J.

“…Background Local application of fluorouracil (Efudix, 5-FU) induces sclerosis in patients with sinonasal tumors and superficial basocellular skin carcinoma. As…”
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Decreased Expression of Vascular Endothelial Growth Factor Receptor 1 Contributes to the Pathogenesis of Hereditary Hemorrhagic Telangiectasia Type 2 by Thalgott, Jérémy H, Dos-Santos-Luis, Damien, Hosman, Anna E, Martin, Sabrina, Lamandé, Noël, Bracquart, Diane, Srun, Samly, Galaris, Georgios, de Boer, Hetty C, Tual-Chalot, Simon, Kroon, Steven, Arthur, Helen M, Cao, Yihai, Snijder, Repke J, Disch, Frans, Mager, Johannes J, Rabelink, Ton J, Mummery, Christine L, Raymond, Karine, Lebrin, Franck

“…BACKGROUND:Hereditary Hemorrhagic Telangiectasia type 2 (HHT2) is an inherited genetic disorder characterized by vascular malformations and hemorrhage. HHT2…”
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Follow-up of pulmonary right-to-left shunt in hereditary haemorrhagic telangiectasia by Vorselaars, Veronique M M, Velthuis, Sebastiaan, Snijder, Repke J, Westermann, Cornelis J J, Vos, Jan A, Mager, Johannes J, Post, Martijn C

“…Pulmonary arteriovenous malformations (PAVMs) are associated with severe neurological complications in hereditary haemorrhagic telangiectasia (HHT)…”
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BMP Receptor Inhibition Enhances Tissue Repair in Endoglin Heterozygous Mice by Bakker, Wineke, Dingenouts, Calinda K E, Lodder, Kirsten, Wiesmeijer, Karien C, de Jong, Alwin, Kurakula, Kondababu, Mager, Hans-Jurgen J, Smits, Anke M, de Vries, Margreet R, Quax, Paul H A, Goumans, Marie José T H

“…Hereditary hemorrhagic telangiectasia type 1 (HHT1) is a severe vascular disorder caused by mutations in the TGFβ/BMP co-receptor . Endoglin haploinsufficiency…”
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Safety and efficacy of balloon pulmonary angioplasty in chronic thromboembolic pulmonary hypertension in the Netherlands by van Thor, M. C. J., Lely, R. J., Braams, N. J., ten Klooster, L., Beijk, M. A. M., Heijmen, R. H., van den Heuvel, D. A. F., Rensing, B. J. W. M., Snijder, R. J., Vonk Noordegraaf, A., Nossent, E. J., Meijboom, L. J., Symersky, P., Mager, J. J., Bogaard, H. J., Post, M. C.

“…Background Balloon pulmonary angioplasty (BPA) is an emerging treatment in patients with chronic thromboembolic pulmonary hypertension (CTEPH) and chronic…”
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Long-term real world clinical outcomes of macitentan therapy in chronic thromboembolic pulmonary hypertension by van Thor, M.C.J., ten Klooster, L., Snijder, R.J., Mager, J.J., Post, M.C.

“…Macitentan treatment for chronic thromboembolic pulmonary hypertension (CTEPH) in the routine clinical setting is increasing. However, ‘real world’ macitentan…”
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Bosentan or Macitentan Therapy in Chronic Thromboembolic Pulmonary Hypertension? by van Thor, M. C. J., ten Klooster, L., Snijder, R. J., Kelder, J. C., Mager, J. J., Post, M. C.

“…Objective Research comparing bosentan and macitentan in chronic thromboembolic pulmonary hypertension (CTEPH) is scarce, although macitentan might have…”
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Idiopathic and hereditary haemorrhagic telangiectasia associated pulmonary arteriovenous malformations: comparison of clinical and radiographic characteristics by Kroon, S., van den Heuvel, D.A.F., Vos, J.A., van Leersum, M., van Strijen, M.J.L., Post, M.C., Mager, J.J., Snijder, R.J.

“…To determine whether there are differences between idiopathic and hereditary haemorrhagic telangiectasia (HHT) associated pulmonary arteriovenous malformations…”
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Life expextancy of parents with Hereditary Haemorrhagic Telangiectasia by de Gussem, E M, Edwards, C P, Hosman, A E, Westermann, C J J, Snijder, R J, Faughnan, M E, Mager, J J

“…Hereditary Haemorrhagic Telangiectasia (HHT) is an autosomal dominant disease associated with epistaxis, arteriovenous malformations and telangiectasias…”
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