Large Congenital Corneal Dermoid With Spontaneous Partial Regression: The First Report

PURPOSE:To report a spontaneous partial regression of a large congenital corneal dermoid in a newborn. MATERIALS AND METHODS:Review and follow-up of the medical records of a female newborn presenting with a tumor mass of her right eye and no other congenital abnormalities. The child presented on the...

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Bibliographic Details
Published in:	Cornea Vol. 30; no. 2; pp. 219 - 221
Main Authors:	Rončević, Mirjana Bjeloš, Dorešić, Jelena Petrinović, MD, Ljubica Dorn
Format:	Journal Article
Language:	English
Published:	United States Lippincott Williams & Wilkins, Inc 01-02-2011
Subjects:	Corneal Diseases - congenital Corneal Diseases - diagnostic imaging Corneal Diseases - pathology Corneal Diseases - physiopathology Dermoid Cyst - congenital Dermoid Cyst - diagnostic imaging Dermoid Cyst - pathology Dermoid Cyst - physiopathology Female Follow-Up Studies Humans Infant, Newborn Remission, Spontaneous Ultrasonography
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Summary:	PURPOSE:To report a spontaneous partial regression of a large congenital corneal dermoid in a newborn. MATERIALS AND METHODS:Review and follow-up of the medical records of a female newborn presenting with a tumor mass of her right eye and no other congenital abnormalities. The child presented on the first day of life with a mushroom-shaped mass of 15 × 15 mm in diameter that involved the most of the cornea leaving a small clear portion superiorly. The mass protruded through the palpebral aperture. A diagnosis of corneal dermoid was made based on clinical presentation of the mass and radiographic and ultrasound findings. Enucleation of the right eye was discussed, but declined by parents. RESULTS:During the first month of life, a spontaneous partial regression of the mass occurred, so that the patient was able to close the lids completely above the mass. This dermoid is the third type according to Mannʼs classification. Characterized by involvement of the entire anterior segment and lack of lens. CONCLUSIONS:To the best of our knowledge, the case reported is the first documented spontaneous partial regression of a large corneal dermoid. Surgical excision at an early age may be recommended to avoid development of amblyopia and dramatic growth of the tumor. In our case the tumor regressed and surgical excision would have no impact on visual outcome. Future management of type III corneal dermoid needs to consider whether to perform surgery at an early stage or to recommend conservative management.
Bibliography:	ObjectType-Case Study-2 SourceType-Scholarly Journals-1 ObjectType-Feature-4 content type line 23 ObjectType-Report-1 ObjectType-Article-3
ISSN:	0277-3740 1536-4798
DOI:	10.1097/ICO.0b013e3181d1429c