Search Results - "Lopez‐Fernandez, M. F."

Practical aspects of factor concentrate use in patients with von Willebrand disease undergoing invasive procedures: a European survey by Windyga, J., Dolan, G., Altisent, C., Katsarou, O., López Fernández, M.-F., Zülfikar, B.

“…Introduction The bleeding propensity in von Willebrand disease (VWD) is usually moderate or mild and patients with VWD do not need continuous treatment, but do…”
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Efficacy and safety of long-acting recombinant fusion protein linking factor IX with albumin in haemophilia B patients undergoing surgery by Négrier, C., Abdul Karim, F., Lepatan, L. M., Lienhart, A., López-Fernández, M. F., Mahlangu, J., Pabinger, I., Li, Y., Wolko, D., Voigt, C., Jacobs, I., Santagostino, E.

“…Introduction Recombinant factor IX fusion protein (rIX‐FP) has been developed to improve the pharmacokinetic (PK) profile of factor IX (FIX), allowing…”
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Non-genetic risk factors and the development of inhibitors in haemophilia: a comprehensive review and consensus report by ASTERMARK, J., ALTISENT, C., BATOROVA, A., DINIZ, M. J., GRINGERI, A., HOLME, P. A., KARAFOULIDOU, A., LOPEZ-FERNÁNDEZ, M. F., REIPERT, B. M., ROCINO, A., SCHIAVONI, M., Von DEPKA, M., WINDYGA, J., FIJNVANDRAAT, K.

“…The development of inhibitors to the infused factor in patients with haemophilia is a serious clinical problem. Recent evidence suggests that alongside the…”
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Sequential combined bypassing therapy is safe and effective in the treatment of unresponsive bleeding in adults and children with haemophilia and inhibitors by GRINGERI, A., FISCHER, K., KARAFOULIDOU, A., KLAMROTH, R., LÓPEZ-FERNÁNDEZ, M. F., MANCUSO, E.

“…Some 10–20% of bleeding events in haemophilia patients with high‐responding inhibitors cannot be controlled with bypassing agents. However, sequential combined…”
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Efficacy and safety of pegylated full-length recombinant factor VIII with extended half-life for perioperative haemostasis in haemophilia A patients by Brand, B., Gruppo, R., Wynn, T. T., Griskevicius, L., Lopez Fernandez, M. F., Chapman, M., Dvorak, T., Pavlova, B. G., Abbuehl, B. E.

“…Introduction BAX 855 is a pegylated full‐length recombinant factor VIII (rFVIII) with an extended half‐life, built on a licensed rFVIII (ADVATE®). BAX 855…”
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Diagnosis of inherited von Willebrand disease: comparison of two methodologies and analysis of the discrepancies by Costa-Pinto, J., Pérez-Rodríguez, A., Goméz-del-Castillo, M. del C., Lourés, E., Rodríguez-Trillo, Á., Batlle, J., López-Fernández, M. F.

“…Diagnostics of von Willebrand disease (VWD) includes assessment of factor VIII (FVIII) coagulant activity, von Willebrand factor (VWF) antigen (VWF:Ag) and VWF…”
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P1647: CONTRIBUTION OF NEXT GENERATION FLOW (NGF) CYTOMETRY IN PRIMARY IMMUNE THROMBOCYTOPENIA (ITP): UTILITY FOR THE DIFFERENTIAL DIAGNOSIS WITH MYELODYSPLASTIC SYNDROMES by Gonzalez‐Lopez, T. J., Matarraz, S., Caparros, I., Lopez‐Fernandez, M. F., Mingot‐Castellano, M. E., Jimenez Martin, A., Fernandez‐Fuertes, F., Sánchez Gallego, J. I., Leoz, P., Cuevas Ruiz, B., Cuevas Ruiz, M. V., Martin Marín, C., Olazabal Herrero, J., Vicente Cámara, P., Orfao, A.

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Replacement therapy in inherited factor VII deficiency: occurrence of adverse events and relation with surgery by Napolitano, M., Dolce, A., Batorova, A., Giansily-Blaizot, M., Ingerslev, J., Mirbehbahani, N., Di Minno, M. N. D., Lopez Fernandez, M. F., Karimi, M., Charoenkwan, P., Kavakli, K., Mariani, G.

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Further evidence for recessive inheritance of von Willebrand disease with abnormal binding of von Willebrand factor to factor VIII by López-Fernández, M F, Blanco-López, M J, Castiñeira, M P, Batlle, J

“…A new family with a bleeding diathesis and FVIII deficiency secondary to abnormal binding of von Willebrand factor (vWF) to factor VIII (FVIII) is described…”
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Immune tolerance induction in patients with haemophilia a and inhibitors: effectiveness and cost analysis in an European Cohort (The ITER Study) by Rocino, A., Cortesi, P. A., Scalone, L., Mantovani, L. G., Crea, R., Gringeri, A.

“…Introduction Although immune tolerance induction (ITI) is considered the first choice treatment to eradicate inhibitors in haemophilia A patients, little is…”
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PB2307: A MULTICENTER, RANDOMIZED, OPEN‐LABEL STUDY OF ROMIPLOSTIM PLUS DEXAMETHASONE VS DEXAMETHASONE IN PATIENTS WITH NEWLY DIAGNOSED PRIMARY IMMUNE THROMBOCYTOPENIA by Mingot Castellano, M. E., Bradbury, C. A., Rosso Fernández, C., Thomas, I., Alvarez‐Román, M. T., Canaro, M., Caparrós Miranda, I. S., Cappechi, M., Carpenedo, M., Evans, G., González‐Lopéz, J. T., González‐Porras, J. R., Jarque Ramos, I., Lozano‐Almela, M. L., Lopez Fernandez, M. F., Lowe, G., Lyall, H., Pascual Izquierdo, C., Pavord, S., Rayment, R., Roberts, P., Rosique Cortina, P., Sánchez‐González, B., Santoro, C., Talks, K., Valcarcel‐Ferreiras, D., Zaja, F.

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Practical aspects of DDAVP use in patients with von Willebrand Disease undergoing invasive procedures: a European survey by Windyga, J., Dolan, G., Altisent, C., Katsarou, O., López Fernández, M.-F., Zülfikar, B.

“…Introduction Desamino D‐arginine vasopressin (DDAVP or desmopressin) is a useful and effective haemostatic treatment for patients with von Willebrand Disease…”
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Abnormal proteolytic degradation of von Willebrand factor after desmopressin infusion in a new subtype of von Willebrand disease (ID) by Lopez-Fernandez, M F, Gonzalez-Boullosa, R, Blanco-Lopez, M J, Perez, M, Batlle, J

“…We describe two members of a single family, father and son, with mild factor XII deficiency associated to von Willebrand disease (vWD) with aberrant structure…”
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The Heterogeneity of Type IIA von Willebrand’s Disease: Studies With Protease Inhibitors by Batlle, J., Fernandez, M.F. Lopez, Campos, M., Justica, B., Berges, C., Navarro, J.L., Cremades, J.M. Diaz, Kasper, C.K., Dent, J.A., Ruggeri, Z.M., Zimmerman, T.S.

“…The absence of large von Willebrand factor (vWF) multimers from plasma is a characteristic of Type HA von Willebrand’s disease (vWD) and is thought to…”
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Prevalence, follow-up and clinical significance of the anticardiolipin antibodies in normal subjects by Vila, P, Hernández, M C, López-Fernández, M F, Batlle, J

“…To date very few studies that analyze the prevalence of anticardiolipin antibodies (ACA) in healthy subjects have been reported. No data based on a systematic…”
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Proteolytic Degradation of von Willebrand Factor After DDAVP Administration in Normal Individuals by Javier, Batlle, Maria Fernanda, Lopez-Fernandez, A., Lopez-Borrasca, Consuelo, Lopez-Berges, Judith A., Dent, Scott D., Berkowitz, Zaverio M., Ruggeri, Theodore S., Zimmerman

“…The infusion of 1-deamino-8-D-arginine vasopressin (DDAVP) in normal individuals is followed by an increase in factor VIII/von Willebrand factor (vWF) in…”
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Further Specificity Characterization of von Willebrand Factor Inhibitors Developed in Two Patients With Severe von Willebrand Disease by López-Fernández, Maria Fermanda, Martin, Ramón, López-Berges, Consuelo, Ramos, Fernando, Bosch, Norma, Batlle, Javier

“…Circulating inhibitors against von Willebrand factor (vWF) that show the properties of heterologous IgG antibodies have been described in a few patients with…”
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Pharmacogenetics of acenocoumarol in patients with extreme dose requirements by PÉREZ‐ANDREU, V., ROLDÁN, V., LÓPEZ‐FERNÁNDEZ, M. F., ANTÓN, A. I., ALBERCA, I., CORRAL, J., MONTES, R., GARCÍA‐BARBERÁ, N., FERRANDO, F., VICENTE, V., GONZÁLEZ‐CONEJERO, R.

“…Background: There is currently intense debate as to whether pharmacogenetic algorithms for estimating the initial dose of coumarins provide a more accurate…”
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Abnormal structure of von Willebrand factor in myeloproliferative syndrome is associated to either thrombotic or bleeding diathesis by López-Fernández, M F, López-Berges, C, Martín, R, Pardo, A, Ramos, F J, Batlle, J

“…The multimeric and subunit patterns of plasma von Willebrand factor (vWF) were analyzed in eight patients with myeloproliferative syndrome (MS) in order to…”
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Hemophilia A or von Willebrand disease? by BATLLE, J, BLANCO-LOPEZ, M. J, DOMENECH, M, BAIGET, M, ROCHA, R, LOPEZ-FERNANDEZ, M. F

“…Seven members of the same family were studied on several occasions due to a history of hemorrhages. The propositus, a 12-year-old boy, his sister, one brother,…”
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