Mucinous adenocarcinoma in a neonate with congenital pulmonary malformation

Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract, often diagnosed during routine prenatal ultrasonography. We report a full-term newborn female noted to have a large mass in the left hemithorax during prenatal ultrasound, at 35 weeks...

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Bibliographic Details
Published in:	Journal of pediatric surgery case reports Vol. 75; p. 102079
Main Authors:	Linneman, Tycie, Bhattacharyya, Ratul, Zuberi, Jamshed
Format:	Journal Article
Language:	English
Published:	Elsevier Inc 01-12-2021 Elsevier
Subjects:	Congenital pulmonary airway malformation (CPAM) Mucinous adenocarcinoma Congenital pulmonary airway malformation (CPAM) Mucinous adenocarcinoma
Online Access:	Get full text
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Summary:	Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract, often diagnosed during routine prenatal ultrasonography. We report a full-term newborn female noted to have a large mass in the left hemithorax during prenatal ultrasound, at 35 weeks gestation. A multicystic lesion in the lower left chest was confirmed using a Chest Radiograph and Computed Tomography (CT) angiogram. Her hospital course was next followed by a left lower lobectomy, with resultant pathology of CPAM Type 1 and invasive mucinous adenocarcinoma. Though patients with asymptomatic CPAM are often managed by observation, our case of unexpected malignancy advocates early considerations towards Surgery.
ISSN:	2213-5766 2213-5766
DOI:	10.1016/j.epsc.2021.102079