Search Results - "Launay, D."

Survival and prognosis factors in systemic sclerosis: data of a French multicenter cohort, systematic review, and meta-analysis of the literature by Pokeerbux, M R, Giovannelli, J, Dauchet, L, Mouthon, L, Agard, C, Lega, J C, Allanore, Y, Jego, P, Bienvenu, B, Berthier, S, Mekinian, A, Hachulla, E, Launay, D

“…Data on survival and prognosis factors in incident cohorts are scarce in systemic sclerosis (SStc). To describe survival, standardized mortality ratio (SMR),…”
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Tranexamic acid as maintenance treatment for non‐histaminergic angioedema: analysis of efficacy and safety in 37 patients by Wintenberger, C., Boccon‐Gibod, I., Launay, D., Fain, O., Kanny, G., Jeandel, P. Y., Martin, L., Gompel, A., Bouillet, L.

“…Summary Angioedema (AE) is a clinical syndrome characterized by localised swelling lasting several hours. The swelling is often recurring and can be lethal if…”
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Benefits of progestin contraception in non-allergic angioedema by Saule, C., Boccon-Gibod, I., Fain, O., Kanny, G., Plu-Bureau, G., Martin, L., Launay, D., Bouillet, L., Gompel, A.

“…Summary Background Hereditary angioedema attacks can be induced or worsened by oral contraceptive containing oestrogens. Objectives The purpose of this study…”
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Cardiac magnetic resonance imaging in systemic sclerosis: a cross-sectional observational study of 52 patients by Hachulla, A-L, Launay, D, Gaxotte, V, de Groote, P, Lamblin, N, Devos, P, Hatron, P-Y, Beregi, J-P, Hachulla, E

“…To assess the prevalence and patterns of cardiac abnormalities as detected by cardiac magnetic resonance imaging (MRI) in systemic sclerosis (SSc). Fifty-two…”
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Raising rare disease awareness using red flags, role play simulation and patient educators: results of a novel educational workshop on Raynaud phenomenon and systemic sclerosis by Sanges, S, Farhat, M-M, Assaraf, M, Galland, J, Rivière, E, Roubille, C, Lambert, M, Yelnik, C, Maillard, H, Sobanski, V, Lefèvre, G, Launay, D, Morell-Dubois, S, Hachulla, E

“…As lack of awareness of rare diseases (RDs) among healthcare professionals results in delayed diagnoses, there is a need for a more efficient approach to RD…”
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Combined pulmonary fibrosis and emphysema in systemic sclerosis: A syndrome associated with heavy morbidity and mortality by Champtiaux, N., Cottin, V., Chassagnon, G., Chaigne, B., Valeyre, D., Nunes, H., Hachulla, E., Launay, D., Crestani, B., Cazalets, C., Jego, P., Bussone, G., Bérezné, A., Guillevin, L., Revel, M.P., Cordier, J.F., Mouthon, L.

“…The syndrome of combined pulmonary fibrosis and emphysema (CPFE) primarily due to tobacco smoking has been reported in connective tissue disease, but little is…”
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Efficacy of anti-TNF alpha in severe and refractory major vessel involvement of Behcet's disease: A multicenter observational study of 18 patients by Desbois, A.C., Biard, L., Addimanda, O., Lambert, M., Hachulla, E., Launay, D., Ackermann, F., Pérard, L., Hot, A., Maurier, F., Mausservey, C., Bernard, F., Noel, N., Alric, L., Mirault, T., Cohen, F., Boussouar, S., Resche-Rigon, M., Cacoub, P., Saadoun, D.

“…To describe the outcome and tolerance in patients treated with anti-TNFα in severe and refractory major vessel disease in Behçet's disease (BD). A multicenter…”
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Hereditary angioedema and its new treatments: An update by Launay, D, Bouillet, L, Boccon-Gibod, I, Trumbic, B, Gobert, D, Fain, O

“…Hereditary angioedema, with or without deficient C1 inhibitor level or function, is a rare disease characterized by recurrent attacks of noninflammatory…”
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Persistent triple antiphospholipid antibody positivity as a strong risk factor of first thrombosis, in a long-term follow-up study of patients without history of thrombosis or obstetrical morbidity by Yelnik, C M, Urbanski, G, Drumez, E, Sobanski, V, Maillard, H, Lanteri, A, Morell-Dubois, S, Caron, C, Dubucquoi, S, Launay, D, Duhamel, A, Hachulla, E, Hatron, P Y, Lambert, M

“…Introduction The long-term risk of first thrombosis and benefit of prophylaxis in antiphospholipid antibody (aPL) carriers without history of thrombosis or…”
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Hereditary angioedema with normal C1 inhibitor and factor XII mutation: a series of 57 patients from the French National Center of Reference for Angioedema by Deroux, A., Boccon‐Gibod, I., Fain, O., Pralong, P., Ollivier, Y., Pagnier, A., Djenouhat, K., Du‐Thanh, A., Gompel, A., Faisant, C., Launay, D., Bouillet, L.

“…Summary Hereditary angioedema (HAE) is a rare disease associated with either a quantitative or qualitative deficiency in C1‐inhibitor (C1‐INH) or normal…”
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Safety and efficacy of rituximab in nonviral cryoglobulinemia vasculitis: Data from the French Autoimmunity and Rituximab registry by Terrier, B., Launay, D., Kaplanski, G., Hot, A., Larroche, C., Cathébras, P., Combe, B., de Jaureguiberry, J. P., Meyer, O., Schaeverbeke, T., Somogyi, A., Tricot, L., Zénone, T., Ravaud, P., Gottenberg, J. E., Mariette, X., Cacoub, P.

“…Objective Management of nonviral cryoglobulinemia vasculitis has yet to be defined. Rituximab has emerged as a novel and promising therapeutic alternative, but…”
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Efficacy of rituximab in primary Sjogren's syndrome with peripheral nervous system involvement: results from the AIR registry by Mekinian, A, Ravaud, P, Hatron, P Y, Larroche, C, Leone, J, Gombert, B, Hamidou, M, Cantagrel, A, Marcelli, C, Rist, S, Breban, M, Launay, D, Fain, O, Gottenberg, J E, Mariette, X

“…To evaluate rituximab (RTX) in primary Sjögren's syndrome (pSS) with peripheral nervous system (PNS) involvement. Patients with pSS and PNS involvement who…”
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Pulmonary hypertension in connective tissue diseases: What every CTD specialist should know - but is afraid to ask by Sanges, S, Sobanski, V, Lamblin, N, Hachulla, E, Savale, L, Montani, D, Launay, D

“…Pulmonary hypertension (PH) is a possible complication of connective tissue diseases (CTDs), especially systemic sclerosis (SSc), systemic lupus erythematosus…”
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HYPNOSTRESS study: Interest of medical hypnosis in the evaluation of perceived stress and the experience of hospitalization in an internal medicine department by Chikhoune, L, Morell Dubois, S, Ledoult, E, Launay, D, Hachulla, E, Lambert, M, Yelnik, C, Maillard, H, Terriou, L, Nicolas, A, Cebrian, R, Despre, M, Sobanski, V, Farhat, M-M

“…Patients with chronic illnesses, especially rare autoimmune and/or systemic diseases associated with significant diagnostic uncertainty, have a representation…”
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A descriptive and prognostic study of systemic sclerosis-associated myopathies by Ranque, B, Authier, F-J, Le-Guern, V, Pagnoux, C, Berezne, A, Allanore, Y, Launay, D, Hachulla, E, Kahan, A, Cabane, J, Gherardi, R, Guillevin, L, Mouthon, L

“…To describe the clinical characteristics and muscle pathological features of patients with systemic sclerosis (SSc) and myopathy and analyse their impact on…”
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Atteintes coronariennes et artérite a cellules géantes : à propos de 2 cas et revue de la littérature by Penet, T, Pokeerbux, M R, Morell-Dubois, S, Sanges, S, Maillard, H, Ledoult, E, Lambert, M, Yelnik, C, Sobanski, V, Launay, D, Hachulla, E, Farhat, M M

“…Coronaritis is a rare but serious complication of giant-cell arteritis (GCA), with an estimated prevalence of less than 1%, however difficult to establish, and…”
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Bleeding complications and antithrombotic treatment in 264 pregnancies in antiphospholipid syndrome by Yelnik, C M, Lambert, M, Drumez, E, Le Guern, V, Bacri, J-L, Guerra, M M, Laskin, C A, Branch, D W, Sammaritano, L R, Morel, N, Guettrot-Imbert, G, Launay, D, Hachulla, E, Hatron, P-Y, Salmon, J E, Costedoat-Chalumeau, N

“…Purpose The purpose of this study was to evaluate the safety of antithrombotic treatments prescribed during pregnancy in patients with antiphospholipid…”
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Acquired angioedema due to C1-inhibitor deficiency: CREAK recommendations for diagnosis and treatment by Gobert, D, Bouillet, L, Armengol, G, Coppo, P, Defendi, F, Du-Thanh, A, Hardy, G, Javaud, N, Jeandel, P-Y, Launay, D, Panayotopoulos, V, Pelletier, F, Boccon-Gibod, I, Fain, O

“…Acquired angioedema with C1-inhibitor deficiency is a rare and peculiar entity belonging to the spectrum of bradykinin angioedemas. It usually occurs in…”
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A descriptive study of IgG4-related disease in children and young adults by de Sainte Marie, B., Ebbo, M., Grados, A., Rebours, V., Reumaux, H., Briantais, A., Urbina, D., Cury, J., Morel, N., Lhote, F., Rohmer, B., Lazaro, E., Agbo-Kpati, K.P., Deroux, A., Domont, F., Delacroix, I., Lavigne, C., Perlat, A., Kahn, J.E., Godeau, B., Hamidou, M., Launay, D., Bader-Meunier, B., Schleinitz, N.

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Immunological profile in primary Sjögren syndrome: clinical significance, prognosis and long-term evolution to other auto-immune disease by Fauchais, A L, Martel, C, Gondran, G, Lambert, M, Launay, D, Jauberteau, M O, Hachulla, E, Vidal, E, Hatron, P Y

“…To study evolution of pSS immunological profile, impact on pSS activity and the long-term evolution of patients with atypical auto-antibodies in a bicentric…”
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