Search Results - "LONGONI, Daniela"
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Paroxysmal nocturnal hemoglobinuria clones in children with acquired aplastic anemia: a multicentre study
Published in PloS one (09-07-2014)“…A multicentre study evaluating the presence of glycosil phosphatidyl-inositol (GPI)-negative populations was performed in 85 children with acquired aplastic…”
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Diagnosis and management of acquired aplastic anemia in childhood. Guidelines from the Marrow Failure Study Group of the Pediatric Haemato-Oncology Italian Association (AIEOP)
Published in Blood cells, molecules, & diseases (01-06-2015)“…Acquired aplastic anemia (AA) is a rare heterogeneous disease characterized by pancytopenia and hypoplastic bone marrow. The incidence is 2–3/million…”
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Somatic, hematologic phenotype, long‐term outcome, and effect of hematopoietic stem cell transplantation. An analysis of 97 Fanconi anemia patients from the Italian national database on behalf of the Marrow Failure Study Group of the AIEOP (Italian Association of Pediatric Hematology–Oncology)
Published in American journal of hematology (01-07-2016)“…We analyzed 97 Fanconi anemia patients from a clinic/biological database for genotype, somatic, and hematologic phenotype, adverse hematological events, solid…”
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Risk factors and severe outcome in thrombotic microangiopathy after allogeneic hematopoietic stem cell transplantation
Published in Transplantation (01-09-2006)“…Thrombotic microangiopathy (TMA) has been described as severe complication after hematopoietic stem cell transplantation (HSCT). The principal aim of this…”
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Diamond-Blackfan anemia: genotype-phenotype correlations in Italian patients with RPL5 and RPL11 mutations
Published in Haematologica (Roma) (01-02-2010)“…Diamond-Blackfan anemia is a rare, pure red blood cell aplasia of childhood due to an intrinsic defect in erythropoietic progenitors. About 40% of patients…”
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Endothelial Fate and Angiogenic Properties of Human CD34+ Progenitor Cells in Zebrafish
Published in Arteriosclerosis, thrombosis, and vascular biology (01-07-2011)“…OBJECTIVE—The vascular competence of human-derived hematopoietic progenitors for postnatal vascularization is still poorly characterized. It is unclear…”
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The outcome of children with Fanconi anemia given hematopoietic stem cell transplantation and the influence of fludarabine in the conditioning regimen: a report from the Italian pediatric group
Published in Haematologica (Roma) (01-10-2007)“…From Oncoematologia Pediatrica, Fondazione IRCCS Policlinico San Matteo, Università di Pavia, Pavia, Italy (FL, MZ, MEB); Clinica Pediatrica, Università di…”
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Ubiquitin-proteasome-rich cytoplasmic structures in neutrophils of patients with Shwachman-Diamond syndrome
Published in Haematologica (Roma) (01-07-2012)“…Shwachman-Diamond syndrome is an autosomal recessive disorder in which severe bone marrow dysfunction causes neutropenia and an increased risk of leukemia…”
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Changes in cytokine profile pre- and post-immunosuppression in acquired aplastic anemia
Published in Haematologica (Roma) (01-12-2009)“…Cytokine expression assessed by flow cytometry in 53 acquired aplastic anemia patients before and after combined immunosuppression (EBMT WPSAA protocols)…”
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Morbidity and Mortality Due to Liver Disease in Children Undergoing Allogeneic Bone Marrow Transplantation: A 10-Year Prospective Study
Published in Blood (01-11-1997)“…We have conducted a long-term prospective study of children undergoing bone marrow transplantation (BMT) to assess morbidity and mortality for liver disease…”
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Interleukin-17-Producing T-Helper Cells as New Potential Player Mediating Graft-Versus-Host Disease in Patients Undergoing Allogeneic Stem-Cell Transplantation
Published in Transplantation (15-12-2009)“…Graft-versus-host disease (GVHD) is a major obstacle to safe allogeneic hematopoietic stem-cell transplantation, leading to significant mortality. Recently,…”
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Incidence of Shwachman-Diamond syndrome
Published in Pediatric blood & cancer (15-12-2012)Get full text
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p38 mitogen-activated protein kinase inhibition enhances in vitro erythropoiesis of Fanconi anemia, complementation group A–deficient bone marrow cells
Published in Experimental hematology (01-04-2015)“…Bone marrow failure in Fanconi anemia (FA) has been linked in part to overproduction of inflammatory cytokines, to which FA stem and progenitor cells are…”
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Cyclosporin A response and dependence in children with acquired aplastic anaemia: a multicentre retrospective study with long‐term observation follow‐up
Published in British journal of haematology (01-01-2008)“…Summary Immunosuppressive therapy (IST) with antithymocyte globulin and cyclosporin A (CyA) is the standard treatment for children with acquired aplastic…”
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Molecular analysis of Fanconi anemia: the experience of the Bone Marrow Failure Study Group of the Italian Association of Pediatric Onco-Hematology
Published in Haematologica (Roma) (01-06-2014)“…Fanconi anemia is an inherited disease characterized by congenital malformations, pancytopenia, cancer predisposition, and sensitivity to cross-linking agents…”
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IL‐10 prevents the differentiation of monocytes to dendritic cells but promotes their maturation to macrophages
Published in European journal of immunology (01-01-1998)“…Human monocytes cultured with granulocyte‐macrophage colony‐stimulating factor (GM‐CSF) and IL‐13 for 7 days differentiate into cells with the morphology and…”
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Treatment of Graft versus Host Disease with Mesenchymal Stromal Cells: A Phase I Study on 40 Adult and Pediatric Patients
Published in Biology of blood and marrow transplantation (01-03-2014)“…Abstract This phase I multicenter study was aimed at assessing the feasibility and safety of intravenous administration of third party bone marrow–derived…”
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Phenotypical and Functional Characterization of Mesenchymal Stem Cells Derived From Patients Affected by Schwachman-Diamond Syndrome
Published in Blood (18-11-2011)“…Abstract 1336 Shwachman-Diamond syndrome (SDS) is a rare autosomal recessive disorder with an incidence of 1 in 50.000 births. In 2001, the genetic defect of…”
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