Search Results - "LIN, WENLANG"

Adult‐onset cerebello‐brainstem dominant form of X‐linked adrenoleukodystrophy presenting as multiple system atrophy: case report and literature review by Ogaki, Kotaro, Koga, Shunsuke, Aoki, Naoya, Lin, Wenlang, Suzuki, Kinuko, Ross, Owen A., Dickson, Dennis W.

“…X‐linked adrenoleukodystrophy (X‐ALD) is the most common peroxisomal disorder and is caused by ABCD1 mutations. A cerebello‐brainstem dominant form that mainly…”
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Ultrastructure of ubiquitin-positive, TDP-43-negative neuronal inclusions in cerebral cortex of C9ORF72-linked frontotemporal lobar degeneration/amyotrophic lateral sclerosis by Lin, Wenlang, Dickson, Dennis W.

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Matrix metalloproteinase-9 contributes to brain extravasation and edema in fulminant hepatic failure mice by Nguyen, Justin H., Yamamoto, Satoshi, Steers, Jeffery, Sevlever, Daniel, Lin, Wenlang, Shimojima, Naoki, Castanedes-Casey, Monica, Genco, Petrina, Golde, Todd, Richelson, Elliott, Dickson, Dennis, McKinney, Michael, Eckman, Christopher B.

“…Fulminant hepatic failure (FHF) can be dreadful. When coma sets in, brain edema develops taking FHF into a lethal course. Mechanisms of brain extravasation…”
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Frontal Lobe Dementia With Novel Tauopathy: Sporadic Multiple System Tauopathy With Dementia by BIGIO, EILEEN H, LIPTON, ANNE M, YEN, SHU-HUI, HUTTON, MIKE L, BAKER, MATT, NACHARAJU, PARIMALA, WHITE, CHARLES L, DAVIES, PETER, LIN, WENLANG, DICKSON, DENNIS W

“…We present a novel tauopathy in a patient with a 10-yr history of progressive frontal lobe dementia and a negative family history. Autopsy revealed mild…”
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Loss of TMEM106B leads to myelination deficits: implications for frontotemporal dementia treatment strategies by Zhou, Xiaolai, Nicholson, Alexandra M, Ren, Yingxue, Brooks, Mieu, Jiang, Peizhou, Zuberi, Aamir, Phuoc, Hung Nguyen, Perkerson, Ralph B, Matchett, Billie, Parsons, Tammee M, Finch, NiCole A, Lin, Wenlang, Qiao, Wenhui, Castanedes-Casey, Monica, Phillips, Virginia, Librero, Ariston L, Asmann, Yan, Bu, Guojun, Murray, Melissa E, Lutz, Cathleen, Dickson, Dennis W, Rademakers, Rosa

“…Genetic variants that define two distinct haplotypes at the TMEM106B locus have been implicated in multiple neurodegenerative diseases and in healthy brain…”
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TDP-43 FILAMENT ASSEMBLY IS INHIBITED BY HEAT SHOCK PROTEINS by DeTure, Michael, Carlomagno, Yari, Zhang, Yongjie, Davis, Mary, Lin, Wenlang, Petrucelli, Leonard

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AGE-RELATED WHITE MATTER PATHOGENESIS IN A MOUSE MODEL OF TAUOPATHY by Sahara, Naruhiko, Lin, Wenlang, Pablo, Perez, Higuchi, Makoto, Suhara, Tetsuya, Febo, Marcelo

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O1‐08‐02: AGE‐RELATED WHITE MATTER PATHOGENESIS IN A MOUSE MODEL OF TAUOPATHY by Sahara, Naruhiko, Lin, Wenlang, Pablo, Perez, Higuchi, Makoto, Suhara, Tetsuya, Febo, Marcelo

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P3‐004: TDP‐43 FILAMENT ASSEMBLY IS INHIBITED BY HEAT SHOCK PROTEINS by DeTure, Michael, Carlomagno, Yari, Zhang, Yongjie, Davis, Mary, Lin, Wenlang, Petrucelli, Leonard

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Pick's disease caused by a novel MAPT mutation (P1.216) by Wszolek, Zbigniew, Tacik, Pawel, DeTure, Michael, Ross, Kelly, Lin, Wenlang, Sanchez Contreras, Monica, Wojtas, Aleksandra, Baker, Matthew, Carlomango, Yari, Brown, Patricia, Strongosky, Audrey, Labbe, Catherine, Fujioka, Shinsuke, Kouri, Naomi, Murray, Melissa, Rademakers, Rosa, Ross, Owen, Dickson, Dennis

“…Abstract only…”
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The novel p.K317N mutation in MAPT gene with clinicopathological phenotype of globular glial tauopathy (P2.161) by Wszolek, Zbigniew, Tacik, Pawel, DeTure, Michael, Lin, Wenlang, Sanchez Contreras, Monica, Wojtas, Aleksandra, Fujioka, Shinsuke, Baker, Matthew, Walton, Ronald, Carlomango, Yari, Brown, Patricia, Strongosky, Audrey, Kouri, Naomi, Murray, Melissa, Josephs, Keith, Rademakers, Rosa, Ross, Owen, Dickson, Dennis

“…Abstract only…”
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Clinicopathologic phenotypes of four cases with MAPT P301L mutation (P2.164) by Wszolek, Zbigniew, Tacik, Pawel, Sanchez Contreras, Monica, Wojtas, Aleksandra, Ross, Kelly, Fujioka, Shinsuke, DeTure, Michael, Lin, Wenlang, Baker, Matthew, Brown, Patricia, Strongosky, Audrey, Kouri, Naomi, Murray, Melissa, Josephs, Keith, Rademakers, Rosa, Ross, Owen, Dickson, Dennis

“…Abstract only…”
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Hereditary diffuse leukoencephalopathy with spheroids: clinical, pathologic and genetic studies of a new kindred by Baba, Yasuhiko, Ghetti, Bernardino, Baker, Matthew C, Uitti, Ryan J, Hutton, Michael L, Yamaguchi, Keiji, Bird, Thomas, Lin, Wenlang, DeLucia, Michael W, Dickson, Dennis W, Wszolek, Zbigniew K

“…Hereditary diffuse leukoencephalopathy with spheroids (HDLS) is a rare autosomal dominant disorder characterized by cerebral white matter degeneration with…”
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O1‐04‐04: TDP‐43 mouse models: Tools toward understanding the normal and disease roles for TDP‐43 by Lewis, Jada, Xu, Yafei, Cannon, Ashley, Zhang, Yongjie, Lin, WenLang, Hutton, Mike, McGowan, Eileen, Dickson, Dennis W., Petrucelli, Len

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P3‐006: Neurons during early development are highly vulnerable to TDP‐43 dysregulation by Cannon, Ashley, Yang, Baoli, Knight, Joshua, Farnham, Mackenzie, Zhang, Yongjie, Wuertzer, Charles, D'Alton, Simon, Howard, John, Lin, Wenlang, Scott, Brittany, Jurasic, Michael, Yu, Xin, Bailey, Rachel, Dickson, Dennis, Petrucelli, Leonard, Lewis, Jada

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Neurons during early development are highly vulnerable to TDP-43 dysregulation by Cannon, Ashley, Yang, Baoli, Knight, Joshua, Farnham, Mackenzie, Zhang, Yongjie, Wuertzer, Charles, D'Alton, Simon, Howard, John, Lin, Wenlang, Scott, Brittany, Jurasic, Michael, Yu, Xin, Bailey, Rachel, Dickson, Dennis, Petrucelli, Leonard, Lewis, Jada

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Altered Expression of Zonula Occludens-2 Precedes Increased Blood-Brain Barrier Permeability in a Murine Model of Fulminant Hepatic Failure by Shimojima, Naoki, Eckman, Christopher B., McKinney, Michael, Sevlever, Daniel, Yamamoto, Satoshi, Lin, Wenlang, Dickson, Dennis W., Nguyen, Justin H.

“…Brain edema secondary to increased blood-brain barrier (BBB) permeability is a lethal complication in fulminant hepatic failure (FHF). Intact tight junctions…”
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TDP-43 mouse models: Tools toward understanding the normal and disease roles for TDP-43 by Lewis, Jada, Xu, Yafei, Cannon, Ashley, Zhang, Yongjie, Lin, WenLang, Hutton, Mike, McGowan, Eileen, Dickson, Dennis W, Petrucelli, Len

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Familial frontotemporal dementia with a novel tau exon-10 splice site mutation: Nature confirms a theoretic construct by Dickson, Dennis W., Le, Tien V., Lin, Wenlang, Nacharaju, Parimala, Yen, Shu-Hui, Baker, Matthew, Hutton, Michael L., Relkin, Norman

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Adult-onset cerebello-brainstem dominant form of X-linked adrenoleukodystrophy presenting as multiple system atrophy: case report and literature review by Ogaki, Kotaro, Koga, Shunsuke, Aoki, Naoya, Lin, Wenlang, Suzuki, Kinuko, Ross, Owen A., Dickson, Dennis W.

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