Search Results - "LIEPNIEKS, J"

Progression of transthyretin amyloid neuropathy after liver transplantation by LIEPNIEKS, Juris J, ZHANG, Lucy Q, BENSON, Merrill D

“…To biochemically characterize peripheral nerve amyloid in subjects with transthyretin (TTR) amyloidosis and assess effect of orthotopic liver transplantation…”
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Hereditary systemic immunoglobulin light-chain amyloidosis by Benson, Merrill D., Liepnieks, Juris J., Kluve-Beckerman, Barbara

“…Several members of a family died from renal failure as a result of systemic amyloidosis. Extensive studies to detect previously documented gene mutations…”
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Leukocyte chemotactic factor 2: A novel renal amyloid protein by Benson, Merrill D., James, Sam, Scott, Katherine, Liepnieks, Juris J., Kluve-Beckerman, Barbara

“…Renal amyloid deposits can often be seen in primary amyloidosis (immunoglobulin light chain disease) or in secondary forms such as reactive amyloidosis as well…”
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Carbamylation of the amino‐terminal residue (Gly1) of mouse serum amyloid A promotes amyloid formation in a cell culture model by Kluve‐Beckerman, Barbara, Liepnieks, Juris J., Benson, Merrill D., Lai, Xianyin, Qi, Guihong, Wang, Mu

“…Amyloid A (AA) amyloidosis is a fatal protein deposition disease afflicting a small percentage of patients with chronic inflammation. Factors other than…”
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Progression of cardiac amyloid deposition in hereditary transthyretin amyloidosis patients after liver transplantation by Liepnieks, Juris J., Benson, Merrill D.

“…It has been hypothesized that transthyretin (TTR) amyloidosis may progress after orthotopic liver transplantation (OLT) as a result of continued amyloid fibril…”
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A New Human Hereditary Amyloidosis: The Result of a Stop-Codon Mutation in the Apolipoprotein AII Gene by Benson, Merrill D., Liepnieks, Juris J., Yazaki, Masahide, Yamashita, Taro, Hamidi Asl, Kamran, Guenther, Brian, Kluve-Beckerman, Barbara

“…Hereditary systemic amyloidosis may be caused by mutations in a number of plasma proteins including transthyretin, apolipoprotein AI, fibrinogen Aα-chain,…”
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Biochemical characterization of vitreous amyloid formed after liver transplantation by Liepnieks, Juris J., Phan, Anh-Danh T., Wise, Ryan J., Hrisomalos, Frank N., Benson, Merrill D.

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Hereditary Amyloid Cardiomyopathy Caused by a Variant Apolipoprotein A1 by Hamidi Asl, Ladan, Liepnieks, Juris J., Hamidi Asl, Kamran, Uemichi, Tomoyuki, Moulin, Georges, Desjoyaux, Emmanuel, Loire, Robert, Delpech, Marc, Grateau, Gilles, Benson, Merrill D.

“…Autosomal dominant hereditary amyloidosis with a unique cutaneous and cardiac presentation and death from heart failure by the sixth or seventh decade was…”
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A cell culture system for the study of amyloid pathogenesis : Amyloid formation by peritoneal macrophages cultured with recombinant serum amyloid A by KLUVE-BECKERMAN, B, LIEPNIEKS, J. J, WANG, L, BENSON, M. D

“…A murine macrophage culture system that is both easy to employ and amenable to manipulation has been developed to study the cellular processes involved in AA…”
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Biochemical characterization of vitreous and cardiac amyloid in Ile84Ser transthyretin amyloidosis by Liepnieks, Juris J., Wilson, Donald L., Benson, Merrill D.

“…Plasma transthyretin (TTR) is synthesized in the liver and is the source for visceral amyloid deposits in TTR amyloidosis. However, TTR is also synthesized in…”
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Aging in Heterozygous Dnmt1-Deficient Mice: Effects on Survival, the DNA Methylation Genes, and the Development of Amyloidosis by Ray, Donna, Wu, Ailing, Wilkinson, J. Erby, Murphy, Hedwig S., Lu, Qianjin, Kluve-Beckerman, Barbara, Liepnieks, Juris J., Benson, Merrill, Yung, Raymond, Richardson, Bruce

“…We previously reported that heterozygous DNA methyltransferase 1-deficient (Dnmt1+/−) mice maintain T-cell immune function and DNA methylation levels with…”
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Contribution of wild-type transthyretin to hereditary peripheral nerve amyloid by Yazaki, Masahide, Liepnieks, Juris J., Kincaid, John C., Benson, Merrill D.

“…To elucidate the contribution of wild‐type transthyretin (TTR) to amyloid polyneuropathy in TTR amyloidosis, we biochemically investigated amyloid fibrils…”
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A new transthyretin mutation associated with leptomeningeal amyloidosis by Liepnieks, J. J., Dickson, D. W., Benson, M. D.

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Hereditary systemic amyloidosis associated with a new apolipoprotein AII stop codon mutation Stop78Arg by Yazaki, Masahide, Liepnieks, Juris J., Barats, Mark S., Cohen, Arthur H., Benson, Merrill D.

“…Hereditary systemic amyloidosis associated with a new apolipoprotein AII stop codon mutation Stop78Arg. Mutations in the gene for apolipoprotein AII (apoAII)…”
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Organ-Specific (Localized) Synthesis of Ig Light Chain Amyloid by Hamidi Asl, Kamran, Liepnieks, Juris J, Nakamura, Masaaki, Benson, Merrill D

“…Ig amyloidosis is usually a systemic disease with multisystem involvement. However, in a significant number of cases amyloid deposition is limited to one…”
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The x-ray crystal structure refinements of normal human transthyretin and the amyloidogenic Val-30-->Met variant to 1.7-A resolution by HAMILTON, J. A, STEINRAUF, L. K, BRADEN, B. C, LIEPNIEKS, J, BENSON, M. D, HOLMGREN, G, SANDGREN, O, STEEN, L

“…The x-ray crystal structures of normal human transthyretin (prealbumin) and the amyloidogenic Val-30-Met variant have been refined at 1.7-A resolution to…”
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Protein aging hypothesis of Alzheimer disease by Orpiszewski, Jozef, Schormann, Norbert, Kluve-Beckerman, Barbara, Liepnieks, Juris J., Benson, Merrill D.

“…ABSTRACT Alzheimer disease (AD), the most common form of aging‐related neurodegenerative disorders, is associated with formation of fibrillar deposits of…”
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A Novel Apolipoprotein A-1 Variant, Arg173Pro, Associated with Cardiac and Cutaneous Amyloidosis by Hamidi Asl, Kamran, Liepnieks, Juris J., Nakamura, Masaaki, Parker, Frank, Benson, Merrill D.

“…An American kindred was found to have hereditary amyloidosis with cutaneous and cardiac involvement. Characterization of fibrils isolated from skin identified…”
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A transgenic mouse model of human systemic ApoA2 amyloidosis by Benson, M. D., Kalopissis, A. -D., Charbert, M., Liepnieks, J. J., Kluve-Beckerman, B.

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Rapidly progressive AA cardiomyopathy by Ishii, W., Kluve-Beckerman, B., Liepnieks, J. J., Vakili, S. T., Benson, M. D.

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