Search Results - "Kemper, Markus J."

New therapies in steroid-sensitive and steroid-resistant idiopathic nephrotic syndrome by van Husen, Michael, Kemper, Markus J.

“…Although many children with idiopathic nephrotic syndrome (INS) respond initially to steroid therapy, repeated courses for patients with relapses often cause…”
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Rapid Response to Cyclosporin A and Favorable Renal Outcome in Nongenetic Versus Genetic Steroid-Resistant Nephrotic Syndrome by Büscher, Anja K, Beck, Bodo B, Melk, Anette, Hoefele, Julia, Kranz, Birgitta, Bamborschke, Daniel, Baig, Sabrina, Lange-Sperandio, Bärbel, Jungraithmayr, Theresa, Weber, Lutz T, Kemper, Markus J, Tönshoff, Burkhard, Hoyer, Peter F, Konrad, Martin, Weber, Stefanie

“…Treatment of congenital nephrotic syndrome (CNS) and steroid-resistant nephrotic syndrome (SRNS) is demanding, and renal prognosis is poor. Numerous causative…”
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Early-Childhood Membranous Nephropathy Due to Cationic Bovine Serum Albumin by Debiec, Hanna, Lefeu, Florence, Kemper, Markus J, Niaudet, Patrick, Deschênes, Georges, Remuzzi, Giuseppe, Ulinski, Tim, Ronco, Pierre

“…BSA ingested in food can escape the intestinal barrier and induce antibovine serum albumin antibodies. The authors of this study identified circulating BSA in…”
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Chest configuration in children and adolescents with infantile nephropathic cystinosis compared with other chronic kidney disease entities and its clinical determinants by Müller, Sophia, Kluck, Rika, Jagodzinski, Celina, Brügelmann, Malina, Hohenfellner, Katharina, Büscher, Anja, Kemper, Markus J., Fröde, Kerstin, Oh, Jun, Billing, Heiko, Thumfart, Julia, Weber, Lutz T., Acham-Roschitz, Birgit, Arbeiter, Klaus, Tönshoff, Burkhard, Hagenberg, Martina, Pavičić, Leo, Haffner, Dieter, Zivicnjak, Miroslav

“…Background Infantile nephropathic cystinosis (INC) is a systemic lysosomal storage disease causing intracellular cystine accumulation, resulting in renal…”
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Human factor H-related protein 2 (CFHR2) regulates complement activation by Eberhardt, Hannes U, Buhlmann, Denise, Hortschansky, Peter, Chen, Qian, Böhm, Sascha, Kemper, Markus J, Wallich, Reinhard, Hartmann, Andrea, Hallström, Teresia, Zipfel, Peter F, Skerka, Christine

“…Mutations and deletions within the human CFHR gene cluster on chromosome 1 are associated with diseases, such as dense deposit disease, CFHR nephropathy or…”
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The influence of gender and sexual hormones on incidence and outcome of chronic kidney disease by Kummer, Sebastian, von Gersdorff, Gero, Kemper, Markus J., Oh, Jun

“…It has long been known that the female sex is associated with a better clinical outcome in chronic renal diseases. Although many experimental, clinical, and…”
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Mutations in TBX18 Cause Dominant Urinary Tract Malformations via Transcriptional Dysregulation of Ureter Development by Vivante, Asaf, Kleppa, Marc-Jens, Schulz, Julian, Kohl, Stefan, Sharma, Amita, Chen, Jing, Shril, Shirlee, Hwang, Daw-Yang, Weiss, Anna-Carina, Kaminski, Michael M., Shukrun, Rachel, Kemper, Markus J., Lehnhardt, Anja, Beetz, Rolf, Sanna-Cherchi, Simone, Verbitsky, Miguel, Gharavi, Ali G., Stuart, Helen M., Feather, Sally A., Goodship, Judith A., Goodship, Timothy H.J., Woolf, Adrian S., Westra, Sjirk J., Doody, Daniel P., Bauer, Stuart B., Lee, Richard S., Adam, Rosalyn M., Lu, Weining, Reutter, Heiko M., Kehinde, Elijah O., Mancini, Erika J., Lifton, Richard P., Tasic, Velibor, Lienkamp, Soeren S., Jüppner, Harald, Kispert, Andreas, Hildebrandt, Friedhelm

“…Congenital anomalies of the kidneys and urinary tract (CAKUT) are the most common cause of chronic kidney disease in the first three decades of life…”
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The centrosomal protein nephrocystin-6 is mutated in Joubert syndrome and activates transcription factor ATF4 by Hildebrandt, Friedhelm, Sayer, John A, Otto, Edgar A, O'Toole, John F, Nurnberg, Gudrun, Kennedy, Michael A, Becker, Christian, Hennies, Hans Christian, Helou, Juliana, Attanasio, Massimo, Fausett, Blake V, Utsch, Boris, Khanna, Hemant, Liu, Yan, Drummond, Iain, Kawakami, Isao, Kusakabe, Takehiro, Tsuda, Motoyuki, Ma, Li, Lee, Hwankyu, Larson, Ronald G, Allen, Susan J, Wilkinson, Christopher J, Nigg, Erich A, Shou, Chengchao, Lillo, Concepcion, Williams, David S, Hoppe, Bernd, Kemper, Markus J, Neuhaus, Thomas, Parisi, Melissa A, Glass, Ian A, Petry, Marianne, Kispert, Andreas, Gloy, Joachim, Ganner, Athina, Walz, Gerd, Zhu, Xueliang, Goldman, Daniel, Nurnberg, Peter, Swaroop, Anand, Leroux, Michel R

“…The molecular basis of nephronophthisis, the most frequent genetic cause of renal failure in children and young adults, and its association with retinal…”
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Treatment of Genetic Forms of Nephrotic Syndrome by Kemper, Markus J, Lemke, Anja

“…Idiopathic steroid-resistant nephrotic syndrome (SRNS) is most frequently characterized by focal segmental glomerulosclerosis (FSGS) but also other…”
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Immunohistochemical and serological characterization of membranous nephropathy in children and adolescents by Dettmar, Anne K., Wiech, Thorsten, Kemper, Markus J., Soave, Armin, Rink, Michael, Oh, Jun, Stahl, Rolf A. K., Hoxha, Elion

“…Background Membranous nephropathy (MN) is a common cause of nephrotic syndrome in adults, but is less frequent in children. Antibodies against four antigens…”
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Epidemiology and Morbidity of Epstein-Barr Virus Infection in Pediatric Renal Transplant Recipients: A Multicenter, Prospective Study by Höcker, Britta, Fickenscher, Helmut, Delecluse, Henri-Jacques, Böhm, Stephan, Küsters, Uta, Schnitzler, Paul, Pohl, Martin, John, Ulrike, Kemper, Markus J., Fehrenbach, Henry, Wigger, Marianne, Holder, Martin, Schröder, Monika, Billing, Heiko, Fichtner, Alexander, Feneberg, Reinhard, Sander, Anja, Köpf-Shakib, Sabine, Süsal, Caner, Tönshoff, Burkhard

“…Background. The epidemiology and morbidity of Epstein-Barr virus (EBV) infection in pediatric renal transplant recipients have been characterized…”
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Response to cyclosporine in steroid-resistant nephrotic syndrome: discontinuation is possible by Klaassen, Ilka, Özgören, Bünyamin, Sadowski, Carolin E., Möller, Kristina, van Husen, Michael, Lehnhardt, Anja, Timmermann, Kirsten, Freudenberg, Folke, Helmchen, Udo, Oh, Jun, Kemper, Markus J.

“…Background Steroid-resistant nephrotic syndrome (SRNS) is still regarded as a serious disease although treatment with cyclosporine (CSA) has improved outcome…”
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Transmission of Glomerular Permeability Factor Soluble Urokinase Plasminogen Activator Receptor (suPAR) From a Mother to Child by Kemper, Markus J., MD, Wei, Changli, MD, PhD, Reiser, Jochen, MD, PhD

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Long-term outcome after combined or sequential liver and kidney transplantation in children with infantile and juvenile primary hyperoxaluria type 1 by Loos, Sebastian, Kemper, Markus J, Schmaeschke, Kaja, Herden, Uta, Fischer, Lutz, Hoppe, Bernd, Levart, Tanja Kersnik, Grabhorn, Enke, Schild, Raphael, Oh, Jun, Brinkert, Florian

“…Combined or sequential liver and kidney transplantation (CLKT/SLKT) restores kidney function and corrects the underlying metabolic defect in children with…”
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Long-Term Transplantation Outcomes in Patients With Primary Hyperoxaluria Type 1 Included in the European Hyperoxaluria Consortium (OxalEurope) Registry by Metry, Elisabeth L., Garrelfs, Sander F., Peters-Sengers, Hessel, Hulton, Sally-Anne, Acquaviva, Cecile, Bacchetta, Justine, Beck, Bodo B., Collard, Laure, Deschênes, Georges, Franssen, Casper, Kemper, Markus J., Lipkin, Graham W., Mandrile, Giorgia, Mohebbi, Nilufar, Moochhala, Shabbir H., Oosterveld, Michiel J.S., Prikhodina, Larisa, Hoppe, Bernd, Cochat, Pierre, Groothoff, Jaap W.

“…In primary hyperoxaluria type 1 (PH1), oxalate overproduction frequently causes kidney stones, nephrocalcinosis, and kidney failure. As PH1 is caused by a…”
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Urinary tract infections in children after renal transplantation by John, Ulrike, Kemper, Markus J.

“…Urinary tract infections (UTI) after pediatric kidney transplantation (KTX) are an important clinical problem and occur in 15–33% of patients. Febrile UTI,…”
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Clinical and Laboratory Consequences of Platelet Transfusion in Shiga Toxin–Mediated Hemolytic Uremic Syndrome by Beneke, Jan, Sartison, Aleksej, Kielstein, Jan T., Haller, Hermann, Nitschke, Martin, Kunzendorf, Ulrich, Loos, Sebastian, Kemper, Markus J., Stahl, Rolf A.K., Menne, Jan

“…Recent studies suggest that platelet transfusions are harmful in patients with thrombotic thrombocytopenic purpura, an entity of thrombotic microangiopathies…”
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Effect of the Dialysis Fluid Buffer on Peritoneal Membrane Function in Children by Schmitt, Claus Peter, Nau, Barbara, Gemulla, Gita, Bonzel, Klaus E, Hölttä, Tuula, Testa, Sara, Fischbach, Michel, John, Ulrike, Kemper, Markus J, Sander, Anja, Arbeiter, Klaus, Schaefer, Franz

“…Double-chamber peritoneal dialysis fluids exert less toxicity by their neutral pH and reduced glucose degradation product content. The role of the buffer…”
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Pathogenesis, diagnosis and management of hyperkalemia by Lehnhardt, Anja, Kemper, Markus J.

“…Hyperkalemia is a potentially life-threatening condition in which serum potassium exceeds 5.5 mmol/l. It can be caused by reduced renal excretion, excessive…”
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CTLA4 Polymorphisms in Minimal Change Nephrotic Syndrome in Children: A Case-Control Study by Ohl, Kim, PhD, Eberhardt, Christiane, MD, Spink, Clemens, MD, Zahn, Katharina, MD, Wagner, Norbert, MD, Eggermann, Thomas, MD, Kemper, Markus J., MD, Querfeld, Uwe, MD, Hoppe, Bernd, MD, Harendza, Sigrid, MD, Tenbrock, Klaus, MD

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