Propriospinal Myoclonus in a Child

Propriospinal Myoclonus in a Child

A 6-year-old girl was experiencing repetitive involuntary and massive jerks immediately involving limbs and trunk. The first motor events appeared approximately at 1 year old and only 5 months after a back trauma. Myoclonus became progressively more frequent and more violent, causing episodes of fal...

Full description

Saved in:
Bibliographic Details
Published in:Journal of child neurology Vol. 25; no. 7; pp. 912 - 915
Main Authors: Aydin, Oemer Faruk, Temucin, Cari Mesut, Kayacik, Oezlem Erolu, Tuerker, Hande, Oezyuerek, Hamit
Format: Journal Article
Language:English
Published: Los Angeles, CA SAGE Publications 01-07-2010
Subjects:
Child
Electromyography
Female
Humans
Muscle, Skeletal - physiopathology
Myoclonus - drug therapy
Myoclonus - physiopathology
propriospinal myoclonus
spinal myoclonus
stimulo-sensitive
electromyography
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:A 6-year-old girl was experiencing repetitive involuntary and massive jerks immediately involving limbs and trunk. The first motor events appeared approximately at 1 year old and only 5 months after a back trauma. Myoclonus became progressively more frequent and more violent, causing episodes of falls. Neurological examination showed jerks characterized by upper limb abduction, lower limb abduction, and head—body hyperextension. Apart from these motor events, the neurological examination was normal. The results of vitamin B12 and folate, antinuclear antibody, anti-DNA, anti-Tiroglobulin, anti-thyroid peroxidase antibody, lupus anticoagulant, anti-cardiolipin antibody, rheumatoid factor, and C3 and C4 were unexceptional. Electroencephalography and brain and spinal magnetic resonance imaging were unremarkable. Electromyographic records with surface electrodes showed that duration of myoclonic jerks was ranging from 100 to 300 ms. We thought she had propriospinal myoclonus because of presence of the spreading through the shoulder, upper limbs, and lower limbs in addition to thoracolumbar paraspinal muscles.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
content type line 23
ObjectType-Report-1
ObjectType-Article-3
ObjectType-Article-2
ObjectType-Feature-1
ISSN:0883-0738
1708-8283
DOI:10.1177/0883073809343610