Search Results - "Jadot, M."
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A microglial cell model for acyl-CoA oxidase 1 deficiency
Published in Biochimica et biophysica acta. Molecular and cell biology of lipids (01-04-2019)“…Acyl-CoA oxidase 1 (ACOX1) deficiency is a rare and severe peroxisomal leukodystrophy associated with a very long-chain fatty acid (VLCFA) β–oxidation defect…”
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Identification of HE1 as the Second Gene of Niemann-Pick C Disease
Published in Science (American Association for the Advancement of Science) (22-12-2000)“…Niemann-Pick type C2 disease (NP-C2) is a fatal hereditary disorder of unknown etiology characterized by defective egress of cholesterol from lysosomes. Here…”
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3
A method to assess the lysosomal residence of proteins in cultured cells
Published in Analytical biochemistry (01-03-2008)“…Analytical subcellular fractionation is playing an increasingly important role in proteomic studies to identify and validate components of cellular organelles…”
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Characterization of the signal for rapid internalization of the bovine mannose 6-phosphate/insulin-like growth factor-II receptor
Published in The Journal of biological chemistry (05-06-1992)“…The signal for rapid internalization of the mannose 6-phosphate/insulin-like growth factor II receptor has been localized to the sequence…”
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A microglial cell model for acyl-CoA oxidase 1 deficiency
Published in Biochimica et biophysica acta. Molecular and cell biology of lipids (01-04-2019)Get full text
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Uptake of Exogenous DNA by Rat-Liver: Effect of Cationic Lipids
Published in Biochemical and biophysical research communications (04-08-1995)“…We have investigated by using centrifugation methods, the uptake and the intracellular fate of 35S DNA by rat liver and the effect on these processes of…”
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Intralysosomal hydrolysis of glycyl-L-phenylalanine 2-naphthylamide
Published in Biochemical journal (01-05-1984)“…Glycyl-L-phenylalanine 2-naphthylamide (Gly-L-Phe-2-NNap), a cathepsin C substrate, induces an increase of the free and unsedimentable activities of this…”
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8
Protein insertion into the endoplasmic reticulum of permeabilized cells
Published in FEBS letters (04-09-1995)“…We have established efficient translocation of newly synthesized proteins into the endoplasmic reticulum of permeabilized Mel Juso cells. By site-specific…”
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Cholesterol Depletion Upregulates Involucrin Expression in Epidermal Keratinocytes Through Activation of p38
Published in Journal of investigative dermatology (01-09-2004)“…Cholesterol has been recently suggested to regulate the early steps of keratinocyte differentiation through lipid rafts. In many cell types, depletion of…”
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Chloroquine allows to distinguish between hepatocyte lysosomes and sinusoidal cell lysosomes
Published in Biochemical and biophysical research communications (15-02-1993)“…We have examined the effect of chloroquine on rat liver lysosomal enzyme distributions after isopycnic centrifugation in a sucrose gradient. Chloroquine…”
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Endosomes, lysosomes: their implication in gene transfer
Published in Advanced drug delivery reviews (30-03-2000)“…Plasmid DNA, naked or bound to a non-viral vector, is taken up by endocytosis. As a result, it has to travel through the intracellular endocytic pathway…”
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Effect of glycyl-L-phenylalanine 2-naphthylamide on invertase endocytosed by rat liver
Published in Biochemical journal (01-02-1985)“…The release by glycyl-L-phenylalanine 2-naphthylamide (Gly-L-Phe-2-NNap) of endocytosed invertase associated with the MLP fraction (sum of the M, L and P…”
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13
Detection of bovine beta-lactoglobulin genomic variants by the polymerase chain reaction method and molecular hybridization
Published in Animal genetics (01-01-1992)Get more information
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14
The permeability of lysosomes to sugars. Effect of diethylstilbestrol on the osmotic activation of lysosomes induced by glucose
Published in Biochemical journal (15-09-1989)“…We have investigated the effect on the osmotic activation of rat liver lysosomes, by glucose penetration, of different substances known to inhibit the glucose…”
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Endolysosomal transport of newly-synthesized cathepsin D in a sucrose model of lysosomal storage
Published in Experimental cell research (01-10-2005)“…Newly-synthesized soluble lysosomal enzymes are transported from the trans-Golgi network to lysosomes by a mannose 6-phosphate receptor-mediated pathway…”
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Hydrodynamics-based transfection of the liver: entrance into hepatocytes of DNA that causes expression takes place very early after injection
Published in The journal of gene medicine (01-08-2004)“…Background The mechanism of gene transfer into hepatocytes by the hydrodynamics‐based transfection procedure is not clearly understood. It has been shown that,…”
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Characterization of endocytic components of liver nonparenchymal cells
Published in Sub-cellular biochemistry (1993)Get more information
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18
An immunohistochemical study for testicular biopsies in cases of male infertility
Published in Andrologia (01-03-1980)“…Immunohistochemical and morphological examination of 50 bilateral testicular biopsies of infertile men shows the presence of immunoglobulin in 20% of the…”
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Biochemical Characterization of a Lysosomal Protease Deficient in Classical Late Infantile Neuronal Ceroid Lipofuscinosis (LINCL) and Development of an Enzyme‐Based Assay for Diagnosis and Exclusion of LINCL in HUman Specimens and Animal Models
Published in Journal of neurochemistry (01-08-1999)“…: Classical late‐infantile neuronal ceroid lipofuscinosis (LINCL), a progressive and fatal neurodegenerative disease of childhood, results from mutations in a…”
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Uptake and Intracellular Fate of Polyethylenimine in Vivo
Published in Biochemical and biophysical research communications (19-11-2000)“…Branched polyamines are extensively used as nonviral vectors for plasmid DNA in transfection experiments. Moreover, recently it has been shown that these…”
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