Search Results - "Hubert, Jean‐François"

Contrast-Matched Isotropic Bicelles: A Versatile Tool to Specifically Probe the Solution Structure of Peripheral Membrane Proteins Using SANS by Dos Santos Morais, Raphael, Delalande, Olivier, Pérez, Javier, Mouret, Liza, Bondon, Arnaud, Martel, Anne, Appavou, Marie-Sousai, Le Rumeur, Elisabeth, Hubert, Jean-François, Combet, Sophie

“…Obtaining structural information on integral or peripheral membrane proteins is currently arduous due to the difficulty of their solubilization, purification,…”
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Dystrophin: More than just the sum of its parts by Le Rumeur, Elisabeth, Winder, Steve J., Hubert, Jean-François

“…Dystrophin is one of a number of large cytoskeleton associated proteins that connect between various cytoskeletal elements and often are tethered to the…”
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Dystrophin's central domain forms a complex filament that becomes disorganized by in-frame deletions by Delalande, Olivier, Molza, Anne-Elisabeth, Dos Santos Morais, Raphael, Chéron, Angélique, Pollet, Émeline, Raguenes-Nicol, Céline, Tascon, Christophe, Giudice, Emmanuel, Guilbaud, Marine, Nicolas, Aurélie, Bondon, Arnaud, Leturcq, France, Férey, Nicolas, Baaden, Marc, Perez, Javier, Roblin, Pierre, Piétri-Rouxel, France, Hubert, Jean-François, Czjzek, Mirjam, Le Rumeur, Elisabeth

“…Dystrophin, encoded by the DMD gene, is critical for maintaining plasma membrane integrity during muscle contraction events. Mutations in the DMD gene…”
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The spectrin family of proteins: A unique coiled-coil fold for various molecular surface properties by Nicolas, Aurélie, Delalande, Olivier, Hubert, Jean-François, Le Rumeur, Elisabeth

“…The spectrin superfamily is composed of proteins involved in cytolinker functions. Their main structural feature is a large central subdomain with numerous…”
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A new twist to coiled coil by Le Rumeur, Elisabeth, Hubert, Jean-François, Winder, Steve J.

“…Spectrin repeats have been largely considered as passive linkers or spacers with little functional role other than to convey flexibility to a protein. Whilst…”
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Dystrophin Hot-Spot Mutants Leading to Becker Muscular Dystrophy Insert More Deeply into Membrane Models than the Native Protein by Ameziane-Le Hir, Sarah, Paboeuf, Gilles, Tascon, Christophe, Hubert, Jean-François, Le Rumeur, Elisabeth, Vié, Véronique, Raguénès-Nicol, Céline

“…Dystrophin (DYS) is a membrane skeleton protein whose mutations lead to lethal Duchenne muscular dystrophy or to the milder Becker muscular dystrophy (BMD)…”
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Structure and mechanism of action of a de novo antimicrobial detergent-like peptide by Legrand, Baptiste, Laurencin, Mathieu, Sarkis, Joe, Duval, Emilie, Mouret, Liza, Hubert, Jean-François, Collen, Murielle, Vié, Véronique, Zatylny-Gaudin, Céline, Henry, Joël, Baudy-Floc'h, Michèle, Bondon, Arnaud

“…The K4 peptide (KKKKPLFGLFFGLF) was recently demonstrated to display good antimicrobial activities against various bacterial strains and thus represents a…”
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Novel Mutation in Spectrin-like Repeat 1 of Dystrophin Central Domain Causes Protein Misfolding and Mild Becker Muscular Dystrophy by Acsadi, Gyula, Moore, Steven A., Chéron, Angélique, Delalande, Olivier, Bennett, Lindsey, Kupsky, William, El-Baba, Mohammad, Le Rumeur, Elisabeth, Hubert, Jean-François

“…Mutations in the dystrophin gene without disruption of the reading frame often lead to Becker muscular dystrophy, but a genotype/phenotype correlation is…”
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Dystrophin and Spectrin, Two Highly Dissimilar Sisters of the Same Family by Delalande, Olivier, Czogalla, Aleksander, Hubert, Jean-François, Sikorski, Aleksander, Le Rumeur, Elisabeth

“…Dystrophin and Spectrin are two proteins essential for the organization of the cytoskeleton and for the stabilization of membrane cells. The comparison of…”
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The Art of Champa by Hubert, Jean-François

“…From 12 October 2005 to 9 January 2006, the Musee Guimet in Paris will play host to an exceptional exhibition: ?Treasures of Vietnamese Art? Champa Sculpture?…”
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Fine mapping of hydrophobic contacts reassesses the organization of the first three dystrophin coiled‐coil repeats by Mias‐Lucquin, Dominique, Chéron, Angélique, Le Rumeur, Elisabeth, Hubert, Jean‐François, Delalande, Olivier

“…ABSTRACT Coiled‐coil domain is a structural motif found in proteins crucial for achievement of central biological processes, such as cellular cohesion or…”
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Structural Basis of Neuronal Nitric-oxide Synthase Interaction with Dystrophin Repeats 16 and 17 by Molza, Anne-Elisabeth, Mangat, Khushdeep, Le Rumeur, Elisabeth, Hubert, Jean-François, Menhart, Nick, Delalande, Olivier

“…Duchenne muscular dystrophy is a lethal genetic defect that is associated with the absence of dystrophin protein. Lack of dystrophin protein completely…”
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Becker muscular dystrophy severity is linked to the structure of dystrophin by Nicolas, Aurélie, Raguénès-Nicol, Céline, Ben Yaou, Rabah, Ameziane-Le Hir, Sarah, Chéron, Angélique, Vié, Véronique, Claustres, Mireille, Leturcq, France, Delalande, Olivier, Hubert, Jean-François, Tuffery-Giraud, Sylvie, Giudice, Emmanuel, Le Rumeur, Elisabeth

“…In-frame exon deletions of the Duchenne muscular dystrophy (DMD) gene produce internally truncated proteins that typically lead to Becker muscular dystrophy…”
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The Art of Champa by Hubert, Jean-François

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How the central domain of dystrophin acts to bridge F-actin to sarcolemmal lipids by Mias-Lucquin, Dominique, Dos Santos Morais, Raphael, Chéron, Angélique, Lagarrigue, Mélanie, Winder, Steve J., Chenuel, Thomas, Pérez, Javier, Appavou, Marie-Sousai, Martel, Anne, Alviset, Guillaume, Le Rumeur, Elisabeth, Combet, Sophie, Hubert, Jean-François, Delalande, Olivier

“…[Display omitted] •Repeats R11/R12 and R15 from dystrophin interact with filamentous actin.•A single lipid interacting domain is present in repeat…”
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Human Dystrophin Structural Changes upon Binding to Anionic Membrane Lipids by Dos Santos Morais, Raphael, Delalande, Olivier, Pérez, Javier, Mias-Lucquin, Dominique, Lagarrigue, Mélanie, Martel, Anne, Molza, Anne-Elisabeth, Chéron, Angélique, Raguénès-Nicol, Céline, Chenuel, Thomas, Bondon, Arnaud, Appavou, Marie-Sousai, Le Rumeur, Elisabeth, Combet, Sophie, Hubert, Jean-François

“…Scaffolding proteins play important roles in supporting the plasma membrane (sarcolemma) of muscle cells. Among them, dystrophin strengthens the sarcolemma…”
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Pore selectivity analysis of an aquaglyceroporin by stopped-flow spectrophotometry on bacterial cell suspensions by Hubert, Jean-François, Duchesne, Laurence, Delamarche, Christian, Vaysse, Amaury, Gueuné, Hervé, Raguénès-Nicol, Céline

“…Background information. Transport of water and small neutral solutes across plasma membranes is facilitated by AQP (aquaporin) and aquaglyceroporin channels,…”
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Functional characterization of a microbial aquaglyceroporin by Froger, Alexandrine, Rolland, Jean-Paul, Bron, Patrick, Lagree, Valerie, Caherec, Francoise Le, Deschamps, Stephane, Hubert, Jean-Francois, Pellerin, Isabelle, Thomas, Daniel, Delamarche, Christian

“…UMR CNRS, Interactions Cellulaires et Moléculaires, Equipe Canaux et Récepteurs Membranaires, Université de Rennes 1, Campus de Beaulieu, 35042 Rennes cedex,…”
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Resisting sarcolemmal rupture: dystrophin repeats increase membrane‐actin stiffness by Sarkis, Joe, Vié, Véronique, Winder, Steve J., Renault, Anne, Le Rumeur, Elisabeth, Hubert, Jean‐François

“…Dystrophin is an essential part of a membrane protein complex that provides flexible support to muscle fiber membranes. Loss of dystrophin function leads to…”
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Mapping of the Lipid-Binding and Stability Properties of the Central Rod Domain of Human Dystrophin by Legardinier, Sébastien, Raguénès-Nicol, Céline, Tascon, Christophe, Rocher, Chantal, Hardy, Serge, Hubert, Jean-François, Le Rumeur, Elisabeth

“…Dystrophin is a cytoskeletal protein that confers resistance to the sarcolemma against the stress of contraction–relaxation cycles by interacting with…”
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