Search Results - "Hofbauer, Peter"

Fatigue properties and material characteristics of additively manufactured AlSi10Mg – Effect of the contour parameter on the microstructure, density, residual stress, roughness and mechanical properties by Beevers, Emilie, Brandão, Ana D., Gumpinger, Johannes, Gschweitl, Michael, Seyfert, Christoph, Hofbauer, Peter, Rohr, Thomas, Ghidini, Tommaso

“…•The fatigue resistance of milled AlSi10Mg samples surpasses conventional Al6061.•Producing samples without contour shows to be beneficial for the fatigue…”
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Virtual development of competitive products made of customized ceramic composites by Hofbauer, Peter J.

“…Ceramic matrix composites (CMCs) are commonly employed in situations where conventional materials face limitations or when they could provide substantial…”
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A spoonful of L‐fucose—an efficient therapy for GFUS‐CDG, a new glycosylation disorder by Feichtinger, René G, Hüllen, Andreas, Koller, Andreas, Kotzot, Dieter, Grote, Valerian, Rapp, Erdmann, Hofbauer, Peter, Brugger, Karin, Thiel, Christian, Mayr, Johannes A, Wortmann, Saskia B

“…Congenital disorders of glycosylation are a genetically and phenotypically heterogeneous family of diseases affecting the co‐ and posttranslational…”
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Impact of low-dose calcipotriol ointment on wound healing, pruritus and pain in patients with dystrophic epidermolysis bullosa: A randomized, double-blind, placebo-controlled trial by Guttmann-Gruber, Christina, Piéón Hofbauer, Josefina, Tockner, Birgit, Reichl, Victoria, Klausegger, Alfred, Hofbauer, Peter, Wolkersdorfer, Martin, Tham, Khek-Chian, Lim, Seong Soo, Common, John E, Diem, Anja, Ude-Schoder, Katharina, Hitzl, Wolfgang, Lagler, Florian, Reichelt, Julia, Bauer, Johann W, Lang, Roland, Laimer, Martin

“…Abstract Background Wound management is a critical factor when treating patients with the inherited skin fragility disease dystrophic epidermolysis bullosa…”
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Effects of oxygen on the Liquid Silicon Infiltration (LSI) process by Hofbauer, Peter Josef, Raether, Friedrich

“…The Liquid Silicon Infiltration (LSI) process has been in use for decades for the series production of components of various SiC materials as well as for…”
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Basal pharmacokinetic parameters of topically applied diacerein in pediatric patients with generalized severe epidermolysis bullosa simplex by Ablinger, Michael, Felder, Thomas K, Wimmer, Monika, Zauner, Roland, Hofbauer, Peter, Lettner, Thomas, Wolkersdorfer, Martin, Lagler, Florian B, Diem, Anja, Bauer, Johann W, Wally, Verena

“…Generalized severe epidermolysis bullosa simplex (EBS-gen sev) is caused by mutations within either the KRT5 or KRT14 gene, phenotypically resulting in…”
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Multi-objective optimization of a free-piston Vuilleumier heat pump using a genetic algorithm by Chen, Hanfei, Hofbauer, Peter, Longtin, Jon P.

“…•A genetic algorithm is used to optimize the thermodynamic performance of VHP.•Nine machine parameters are optimized simultaneously using NSGA-II.•Separate…”
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Multi-objective optimization of thermodynamic and dynamic performance of free-piston Vuilleumier heat pump using NSGA-II by Sun, Jiachen, Guan, Jinhuan, Luo, Baojun, Liu, Jingping, Hofbauer, Peter

“…•Developed a Third-order model for optimization of D-FVHP.•NSGA-II is used to optimize dynamic and thermodynamic performances.•Eight structure parameters for…”
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Finite element modeling of reactive liquid silicon infiltration by Hofbauer, Peter Josef, Raether, Friedrich, Rädlein, Edda

“…The LSI process, i.e. the infiltration of molten silicon into porous structures, is one of the most economical techniques for the production of C/C-SiC and…”
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Fundamental Mechanisms With Reactive Infiltration of Silicon Melt Into Carbon Capillaries by Hofbauer, Peter J., Rädlein, Edda, Raether, Friedrich

“…The LSI process, that is, the infiltration of molten silicon into porous structures, is one of the most economical techniques for the production of dense C/SiC…”
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State-wide comparative analysis of the cost saving potential of Vuilleumier heat pumps in residential houses by Shi, Peng, Wang, Lin-Shu, Schwartz, Paul, Hofbauer, Peter

“…•A heat driven heat pump uncaps the natural gas end-use efficiency of 100%•Annual cost savings analysis shows great potentials for Vuilleumier heat…”
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Effects of temperatures on dynamic parameters of Vuilleumier machine with dwell motion based on developed third-order numerical model by Zhang, Lei, Guan, Jinhuan, Luo, Baojun, Liu, Jingping, Huang, Yuexin, Hofbauer, Peter

“…•Developed a third-order model for Hofbauer cycle machine.•Model is validated by experiments.•Damping coefficient Cd and spring coefficient K are obtained at…”
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A simplified dynamic model for the prediction of displacer's free stroke in Hofbauer cycle machine by Guan, Jinhuan, Zhang, Lei, Yang, Jiayao, Liu, Jingping, Luo, Baojun, Huang, Yuexin, Hofbauer, Peter

“…•A simplified dynamic model is developed for prediction of displacer's free stroke.•Experiments on Hofbauer cycle machine is carried out.•A simplified method…”
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Analytical model for Vuilleumier cycle by Guo, Tao, Jiang, Tao, Zou, Peng, Luo, Baojun, Hofbauer, Peter, Liu, Jingping, Huang, Yuexin

“…The Coefficient of Performance of Vuilleumier cycle with ideal reversible changes is much higher than those obtained in practical machines. In this paper, an…”
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Simplified model and analysis for the performance of Hofbauer–Vuilleumier heat pump by Liao, Cheng, Jiang, Tao, Hofbauer, Peter, Ye, Wenlin, Liu, Jingping, Luo, Baojun, Huang, Yuexin

“…Vuilleumier heat pumps can reduce the consumption of fossil combustion and thus have huge potential for applications in heating systems. However, it receives…”
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Diacerein orphan drug development for epidermolysis bullosa simplex: A phase 2/3 randomized, placebo-controlled, double-blind clinical trial by Wally, Verena, Hovnanian, Alain, Ly, Juliette, Buckova, Hana, Brunner, Victoria, Lettner, Thomas, Ablinger, Michael, Felder, Thomas K., Hofbauer, Peter, Wolkersdorfer, Martin, Lagler, Florian B., Hitzl, Wolfgang, Laimer, Martin, Kitzmüller, Sophie, Diem, Anja, Bauer, Johann W.

“…Epidermolysis bullosa simplex (EBS) is a rare genetic, blistering skin disease for which there is no cure. Treatments that address the pathophysiology of EBS…”
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A method of analyzing the respective performances of hypothetical stirling engine and stirling cooler in Vuilleumier machine by Zou, Peng, Gao, Qun, Wang, Shengli, Yang, Jiayao, Luo, Baojun, Hofbauer, Peter, Liu, Jingping, Huang, Yuexin, Ren, Chengqin

“…The respective performances of hypothetical Stirling engine and Stirling cooler in Vuilleumier machines are usually unclear. In this paper, a method of…”
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Repurposing empagliflozin in individuals with glycogen storage disease Ib: A value‐based healthcare approach and systematic benefit‐risk assessment by Derks, Terry G. J., Venema, Annieke, Köller, Clara, Bos, Eline, Overduin, Ruben J., Stolwijk, Nina N., Hofbauer, Peter, Bolhuis, Mathieu S., Eenennaam, Fred, Groen, Henk, Hollak, Carla E. M., Wortmann, Saskia B.

“…Off‐label repurposing of empagliflozin allows pathomechanism‐based treatment of neutropenia/neutrophil‐dysfunction in glycogen storage disease type Ib (GSDIb)…”
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Treatment recommendations for glycogen storage disease type IB- associated neutropenia and neutrophil dysfunction with empagliflozin: Consensus from an international workshop by Grünert, Sarah C., Derks, Terry G.J., Mundy, Helen, Dalton, R. Neil, Donadieu, Jean, Hofbauer, Peter, Jones, Neil, Uçar, Sema Kalkan, LaFreniere, Jamas, Contreras, Enrique Landelino, Pendyal, Surekha, Rossi, Alessandro, Schneider, Blair, Spiegel, Ronen, Stepien, Karolina M., Wesol-Kucharska, Dorota, Veiga-da-Cunha, Maria, Wortmann, Saskia B.

“…Glycogen storage disease type Ib (GSD Ib, biallelic variants in SLC37A4) is a rare disorder of glycogen metabolism complicated by neutropenia/neutrophil…”
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Low-dose calcipotriol can elicit wound closure, anti-microbial, and anti-neoplastic effects in epidermolysis bullosa keratinocytes by Guttmann-Gruber, Christina, Tockner, Birgit, Scharler, Cornelia, Hüttner, Clemens, Common, John E., Tay, Angeline S. L., Denil, Simon L. I. J., Klausegger, Alfred, Trost, Andrea, Breitenbach, Jenny, Schnitzhofer, Peter, Hofbauer, Peter, Wolkersdorfer, Martin, Diem, Anja, Laimer, Martin, Strunk, Dirk, Bauer, Johann W., Reichelt, Julia, Lang, Roland, Piñón Hofbauer, Josefina

“…Recessive dystrophic epidermolysis bullosa (RDEB) patients suffer from chronic and repeatedly infected wounds predisposing them to the development of…”
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