Search Results - "Himes, Ryan W."

Evidence of Chronic Allograft Injury in Liver Biopsies From Long-term Pediatric Recipients of Liver Transplants by Feng, Sandy, Bucuvalas, John C., Demetris, Anthony J., Burrell, Bryna E., Spain, Katherine M., Kanaparthi, Sai, Magee, John C., Ikle, David, Lesniak, Andrew, Lozano, Juan J., Alonso, Estella M., Bray, Robert A., Bridges, Nancy E., Doo, Edward, Gebel, Howard M., Gupta, Nitika A., Himes, Ryan W., Jackson, Annette M., Lobritto, Steven J., Mazariegos, George V., Ng, Vicky L., Rand, Elizabeth B., Sherker, Averell H., Sundaram, Shikha, Turmelle, Yumirle P., Sanchez-Fueyo, Alberto

“…A substantial proportion of pediatric liver transplant recipients develop subclinical chronic allograft injury. We studied whether there are distinct patterns…”
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Efficacy and Safety of Immunosuppression Withdrawal in Pediatric Liver Transplant Recipients: Moving Toward Personalized Management by Feng, Sandy, Bucuvalas, John C., Mazariegos, George V., Magee, John C., Sanchez‐Fueyo, Alberto, Spain, Katharine M., Lesniak, Andrew, Kanaparthi, Sai, Perito, Emily, Venkat, Veena L., Burrell, Bryna E., Alonso, Estella M., Bridges, Nancy D., Doo, Edward, Gupta, Nitika A., Himes, Ryan W., Ikle, David, Jackson, Annette M., Lobritto, Steven J., Jose Lozano, Juan, Martinez, Mercedes, Ng, Vicky L., Rand, Elizabeth B., Sherker, Averell H., Sundaram, Shikha S., Turmelle, Yumirle P., Wood‐Trageser, Michele, Demetris, Anthony J.

“…Background and Aims Tolerance is transplantation’s holy grail, as it denotes allograft health without immunosuppression and its toxicities. Our aim was to…”
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Autoimmune Pancreatitis in Children: Characteristic Features, Diagnosis, and Management by Scheers, Isabelle, Palermo, Joseph J, Freedman, Steven, Wilschanski, Michael, Shah, Uzma, Abu-El-Haija, Maisam, Barth, Bradley, Fishman, Douglas S, Gariepy, Cheryl, Giefer, Matthew J, Heyman, Melvin B, Himes, Ryan W, Husain, Sohail Z, Lin, Tom K, Liu, Quin, Lowe, Mark, Mascarenhas, Maria, Morinville, Veronique, Ooi, Chee Y, Perito, Emily R, Piccoli, David A, Pohl, John F, Schwarzenberg, Sarah J, Troendle, David, Werlin, Steven, Zimmerman, Bridget, Uc, Aliye, Gonska, Tanja

“…Autoimmune pancreatitis (AIP) is an increasingly recognized disease entity, but data in children are limited. AIP presentation and outcome in children might…”
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Regional citrate anticoagulation for continuous renal replacement therapy in pediatric patients with liver failure by Rodriguez, Keila, Srivaths, Poyyapakkam R, Tal, Leyat, Watson, Mary N, Riley, Alyssa A, Himes, Ryan W, Desai, Moreshwar S, Braun, Michael C, Akcan Arikan, Ayse

“…Pediatric liver failure patients frequently develop multiple organ failure and require continuous renal replacement therapy (CRRT) as part of supportive…”
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Undifferentiated Embryonal Sarcoma of the Liver (UESL): A Single-Center Experience and Review of the Literature by Techavichit, Piti, Masand, Prakash M, Himes, Ryan W, Abbas, Rana, Goss, John A, Vasudevan, Sanjeev A, Finegold, Milton J, Heczey, Andras

“…Undifferentiated embryonal sarcoma of the liver (UESL) is a rare and aggressive pediatric malignancy. The purpose of this study was to review the clinical,…”
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Development and rescue of human familial hypercholesterolaemia in a xenograft mouse model by Bissig-Choisat, Beatrice, Wang, Lili, Legras, Xavier, Saha, Pradip K., Chen, Leon, Bell, Peter, Pankowicz, Francis P., Hill, Matthew C., Barzi, Mercedes, Leyton, Claudia Kettlun, Leung, Hon-Chiu Eastwood, Kruse, Robert L., Himes, Ryan W., Goss, John A., Wilson, James M., Chan, Lawrence, Lagor, William R., Bissig, Karl-Dimiter

“…Diseases of lipid metabolism are a major cause of human morbidity, but no animal model entirely recapitulates human lipoprotein metabolism. Here we develop a…”
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Transmission of Hepatitis A Virus through Combined Liver-Small Intestine-Pancreas Transplantation by Foster, Monique A, Weil, Lauren M, Jin, Sherry, Johnson, Thomas, Hayden-Mixson, Tonya R, Khudyakov, Yury, Annambhotla, Pallavi D, Basavaraju, Sridhar V, Kamili, Saleem, Ritter, Jana M, Nelson, Noele, Mazariegos, George, Green, Michael, Himes, Ryan W, Kuhar, David T, Kuehnert, Matthew J, Miller, Jeffrey A, Wiseman, Rachel, Moorman, Anne C

“…Although transmission of hepatitis A virus (HAV) through blood transfusion has been documented, transmission through organ transplantation has not been…”
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Pediatric Liver Transplantation Across the ABO Blood Group Barrier: Is it an Obstacle in the Modern Era? by Rana, Abbas, MD, Kueht, Michael L., MD, Nicholas, Sarah K., MD, Jindra, Peter T., PhD, Himes, Ryan W., MD, Desai, Moreshwar S., MD, Cotton, Ronald T., MD, N. Galvan, N. Thao, MD, O’Mahony, Christine A., MD, Goss, John A., MD, FACS

“…Abstract Background The initial experience with ABO incompatible (ABOi) liver transplants (OLT) was dismal. In the present study, we investigated whether ABOi…”
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Tlr2 is critical for diet-induced metabolic syndrome in a murine model by Himes, Ryan W, Smith, C. Wayne

“…Obesity and its associated comorbidities, termed metabolic syndrome, are increasingly prevalent, and they pose a serious threat to the health of individuals…”
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Diagnostic challenges and disease management in patients with a mild Zellweger spectrum disorder phenotype by Enns, Gregory M., Ammous, Zineb, Himes, Ryan W., Nogueira, Janaina, Palle, Sirish, Sullivan, Meghan, Ramirez, Charina

“…Peroxisome Biogenesis Disorders-Zellweger spectrum disorder (PBD-ZSD) is a rare, autosomal recessive peroxisome biogenesis disorder that presents with variable…”
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NR1H4-related Progressive Familial Intrahepatic Cholestasis 5: Further Evidence for Rapidly Progressive Liver Failure by Himes, Ryan W., Mojarrad, Majid, Eslahi, Atieh, Finegold, Milton J., Maroofian, Reza, Moore, David D.

“…ABSTRACTPathogenic sequence variants in the nuclear bile acid receptor FXR, encoded by NR1H4, have been reported in a small number of children with low-GGT…”
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NR1H4-related Progressive Familial Intrahepatic Cholestasis 5: Further Evidence for Rapidly Progressive Liver Failure by Himes, Ryan W, Mojarrad, Majid, Eslahi, Atieh, Finegold, Milton J, Maroofian, Reza, Moore, David D

“…Pathogenic sequence variants in the nuclear bile acid receptor FXR, encoded by NR1H4, have been reported in a small number of children with low-γ-glutamyl…”
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Diagnostic and therapeutic role of endoscopic retrograde cholangiopancreatography in biliary rhabdomyosarcoma by Himes, Ryan W, Raijman, Isaac, Finegold, Milton J, Russell, Heidi V, Fishman, Douglas S

“…Biliary rhabdomyosarcoma （BRMS） is an uncommon childhood malignancy which has been managed surgically. We present a case of a 3-year-old boy with BRMS, in whom…”
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Features of Hepatitis in Hepatitis-associated Aplastic Anemia: Clinical and Histopathologic Study by Patel, Kalyani R, Bertuch, Alison, Sasa, Ghadir S, Himes, Ryan W, Wu, Hao

“…Hepatitis-associated aplastic anemia (HAA) is a rare variant of aplastic anemia in which patients present with severe pancytopenia after an episode of acute…”
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Lysosomal Acid Lipase Deficiency Unmasked in Two Children With Nonalcoholic Fatty Liver Disease by Himes, Ryan W, Barlow, Sarah E, Bove, Kevin, Quintanilla, Norma M, Sheridan, Rachel, Kohli, Rohit

“…Lysosomal acid lipase deficiency (LAL-D) is a classic lysosomal storage disorder characterized by accumulation of cholesteryl ester and triglyceride. Although…”
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SCYL1 variants cause a syndrome with low γ-glutamyl-transferase cholestasis, acute liver failure, and neurodegeneration (CALFAN) by Lenz, Dominic, McClean, Patricia, Kansu, Aydan, Bonnen, Penelope E, Ranucci, Giusy, Thiel, Christian, Straub, Beate K, Harting, Inga, Alhaddad, Bader, Dimitrov, Bianca, Kotzaeridou, Urania, Wenning, Daniel, Iorio, Raffaele, Himes, Ryan W, Kuloğlu, Zarife, Blakely, Emma L, Taylor, Robert W, Meitinger, Thomas, Kölker, Stefan, Prokisch, Holger, Hoffmann, Georg F, Haack, Tobias B, Staufner, Christian

“…Purpose Biallelic mutations in SCYL1 were recently identified as causing a syndromal disorder characterized by peripheral neuropathy, cerebellar atrophy,…”
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Hybrid Extracorporeal Therapies as a Bridge to Pediatric Liver Transplantation by Akcan Arikan, Ayse, Srivaths, Poyyapakkam, Himes, Ryan W, Tufan Pekkucuksen, Naile, Lam, Fong, Nguyen, Trung, Miloh, Tamir, Braun, Michael, Goss, John, Desai, Moreshwar S

“…Standard intensive care treatment is inadequate to keep children with liver failure alive without catastrophic complications to ensure successful transplant,…”
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Frailty in Children with Liver Disease: A Prospective Multicenter Study by Lurz, Eberhard, Quammie, Claudia, Englesbe, Michael, Alonso, Estella M., Lin, Henry C., Hsu, Evelyn K., Furuya, Katryn N., Gupta, Nitika A., Venkat, Veena L., Daniel, James F., Leonis, Mike A., Miloh, Tamir, Telega, Grzegorz W., Yap, Jason, Menendez, Jerome, Book, Linda S., Himes, Ryan W., Sundaram, Shikha S., Parekh, Rulan, Sonnenday, Chris, Bucuvalas, John, Ng, Vicky L., Kamath, Binita M.

“…To assess frailty, a measure of physiologic declines in multiple organ systems, in children with chronic liver disease using a novel pediatric frailty tool. We…”
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Gastrointestinal Hemorrhage: A Manifestation of the Telomere Biology Disorders by Himes, Ryan W., Chiou, Eric H., Queliza, Karen, Shouval, Dror S., Somech, Raz, Agarwal, Suneet, Jajoo, Kunal, Ziegler, David S., Kratz, Christian P., Huang, James, Lucas, Tiffany L., Myers, Kasiani C., Nelson, Adam S., DiNardo, Courtney D., Alter, Blanche P., Giri, Neelam, Khincha, Payal P., McReynolds, Lisa J., Dufour, Carlo, Pierri, Filomena, Goldman, Frederick D., Sherif, Youmna, Savage, Sharon A., Miloh, Tamir, Bertuch, Alison A.

“…To describe the clinical features, therapeutic interventions, and patient outcomes of gastrointestinal (GI) hemorrhage in individuals with a telomere biology…”
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Recommendations for Diagnosis and Management of Autoimmune Pancreatitis in Childhood: Consensus From INSPPIRE by Scheers, Isabelle, Palermo, Joseph J, Freedman, Steven, Wilschanski, Michael, Shah, Uzma, Abu-El-Haija, Maisam, Barth, Bradley, Fishman, Douglas S, Gariepy, Cheryl, Giefer, Matthew J, Heyman, Melvin B, Himes, Ryan W, Husain, Sohail Z, Lin, Tom K, Liu, Quin, Lowe, Mark, Mascarenhas, Maria, Morinville, Veronique, Ooi, Chee Y, Perito, Emily R, Piccoli, David A, Pohl, John F, Schwarzenberg, Sarah J, Troendle, David, Werlin, Steven, Zimmerman, Bridget, Uc, Aliye, Gonska, Tanja

“…OBJECTIVES:Autoimmune pancreatitis (AIP) represents a complex immune-mediated pancreas disorder. Pediatric AIP (P-AIP) is rare. We have recently summarized the…”
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