Search Results - "Hauw, J.‐J."

Plasma total prion protein as a potential biomarker for neurodegenerative dementia: diagnostic accuracy in the spectrum of prion diseases by Llorens, F., Villar‐Piqué, A., Schmitz, M., Diaz‐Lucena, D., Wohlhage, M., Hermann, P., Goebel, S., Schmidt, I., Glatzel, M., Hauw, J.‐J., Sikorska, B., Liberski, P. P., Riggert, J., Ferrer, I., Zerr, I.

“…Aims In the search for blood‐based biomarkers of neurodegenerative diseases, we characterized the concentration of total prion protein (t‐PrP) in the plasma of…”
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Dyslipidemia is a protective factor in amyotrophic lateral sclerosis by DUPUIS, L, CORCIA, P, MEININGER, V, FERGANI, A, GONZALEZ DE AGUILAR, J.-L, BONNEFONT-ROUSSELOT, D, BITTAR, R, SEILHEAN, D, HAUW, J.-J, LACOMBLEZ, L, LOEFFLER, J.-P

“…Amyotrophic lateral sclerosis (ALS) is the most serious form of degenerative motor neuron disease in adults, characterized by upper and lower motor neuron…”
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Transcriptomic and genetic studies identify IL-33 as a candidate gene for Alzheimer's disease by Chapuis, J, Hot, D, Hansmannel, F, Kerdraon, O, Ferreira, S, Hubans, C, Maurage, C A, Huot, L, Bensemain, F, Laumet, G, Ayral, A M, Fievet, N, Hauw, J J, DeKosky, S T, Lemoine, Y, Iwatsubo, T, Wavrant-Devrièze, F, Dartigues, J F, Tzourio, C, Buée, L, Pasquier, F, Berr, C, Mann, D, Lendon, C, Alpérovitch, A, Kamboh, M I, Amouyel, P, Lambert, J C

“…The only recognized genetic determinant of the common forms of Alzheimer's disease (AD) is the ɛ4 allele of the apolipoprotein E gene (APOE). To identify new…”
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Synapse and primary cilia dysfunctions in Autism Spectrum Disorders. Avenues to normalize these functions by Hauw, J.-J., Hausser-Hauw, C., Barthélémy, C.

“…An update on the plasticity of the brain networks involved in autism (autism spectrum disorders [ASD]), and the increasing role of their synapses and primary…”
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Measles Sclerosing Subacute PanEncephalitis (SSPE), an intriguing and ever-present disease: Data, assumptions and new perspectives by Lebon, P., Gelot, A., Zhang, S.-Y., Casanova, J.-L., Hauw, J.-J.

“…Subacute sclerosing panencephalitis (SSPE) is a rare, non-treatable and fatal neurological complication of measles, still present due to the return of the…”
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Predictors for malignant middle cerebral artery infarctions : A postmortem analysis by JARAMILLO, A, GONGORA-RIVERA, F, LABREUCHE, J, HAUW, J.-J, AMARENCO, P

“…Early detection of malignant infarction of the middle cerebral artery (MI-MCA) is important because of possible treatment by hemicraniectomy. To investigate…”
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Corrigendum to “Measles Sclerosing Subacute PanEncephalitis (SSPE), an intriguing and ever-present disease: Data, Assumptions and new Perspectives” [Rev. Neurol. 177 (2021) 1059–68] by Lebon, P., Gelot, A., Zhang, S.-Y., Casanova, J.-L., Hauw, J.-J.

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The significance of cortical pathology in progressive supranuclear palsy : Clinico-pathological data in 10 cases by VERNY, M, DUYCKAERTS, C, AGID, Y, HAUW, J.-J

“…Several observations suggest that the cortical lesions of progressive supranuclear palsy (PSP) play a role in the clinical symptoms and signs of the disease,…”
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Preliminary NINDS neuropathologic criteria for Steele-Richardson-Olszewski syndrome (progressive supranuclear palsy) by Hauw, J J, Daniel, S E, Dickson, D, Horoupian, D S, Jellinger, K, Lantos, P L, McKee, A, Tabaton, M, Litvan, I

“…We present the preliminary neuropathologic criteria for progressive supranuclear palsy (PSP) as proposed at a workshop held at the National Institutes of…”
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Olig2 expression, GFAP, p53 and 1p loss analysis contribute to glioma subclassification by Mokhtari, K., Paris, S., Aguirre-Cruz, L., Privat, N., Crinière, E., Marie, Y., Hauw, J.-J., Kujas, M., Rowitch, D., Hoang-Xuan, K., Delattre, J.-Y., Sanson, M.

“…The expression of Olig2, a basic helix–loop–helix (bHLH) transcription factor involved in oligodendroglial specification, was investigated by…”
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BSE transmission to macaques by Lasmezas, C.I, Deslys, J.P, Demaimay, R, Adjou, I.T, Lamoury, F, Dormont, D, Robain, O, Ironside, J, Hauw, J.J

“…The recent description in the United Kingdom of a new variant of Creutzfeldt-Jacob disease (vCJD) with a unique clinicopathological presentation has raised…”
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Validity and Reliability of the Preliminary NINDS Neuropathologic Criteria for Progressive Supranuclear Palsy and Related Disorders by Litvan, I, Hauw, J J, Bartko, J J, Lantos, P L, Daniel, S E, Horoupian, D S, McKee, A, Dickson, D, Bancher, C, Tabaton, M, Jellinger, K, Anderson, D W

“…We investigated the validity and reliability of diagnoses made by eight neuropathologists who used the preliminary NINDS neuropathologic diagnostic criteria…”
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Doctor Francoise Cathala and history of prions diseases by Court, L, Hauw, J-J

“…Doctor Françoise Cathala Pagesy, MD, MS, born on July 7, 1921 in Paris, passed away peacefully at home on November 5, 2012. Unconventional, passionate and…”
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Spreading of protein misfolding: A new paradigm in neurology by Hauw, J-J, Haïk, S, Duyckaerts, C

“…Protein misfolding and spreading ("transconformation") are being better understood. Described in Prions diseases, this new paradigm in the field of…”
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Accumulation of flotillin-1 in tangle-bearing neurones of Alzheimer's disease by Girardot, N., Allinquant, B., Langui, D., Laquerrière, A., Dubois, B., Hauw, J.-J., Duyckaerts, C.

“…The protein flotillin‐1 is associated with the ‘lipid rafts’, that is, membrane microdomains that are enriched in cholesterol and sphingolipids. We compared…”
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Sporadic Creutzfeldt-Jakob disease mimicking nonconvulsive status epilepticus by LAPERGUE, B, DEMERET, S, BOLGERT, F, BRANDEL, J. P, NAVARRO, V, DENYS, V, LAPLANCHE, J. L, GALANAUD, D, VERNY, M, SAZDOVITCH, V, BAULAC, M, HAÏK, S, HAUW, J. J

“…Nonconvulsive status epilepticus (NCSE) in patients with confusion may be difficult to distinguish from nonepileptic (metabolic/toxic, postanoxic, and…”
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Preservation of midbrain catecholaminergic neurons in very old human subjects by Kubis, N., Faucheux, B. A., Ransmayr, G., Damier, P., Duyckaerts, C., Henin, D., Forette, B., Le Charpentier, Y., Hauw, J.-J., Agid, Y., Hirsch, E. C.

“…Parkinson's disease is characterized by a progressive degeneration of dopaminergic neurons in the midbrain, yet the cause of this neuronal loss is still…”
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The relationship between Bunina bodies, skein-like inclusions and neuronal loss in amyotrophic lateral sclerosis by VAN WELSEM, M. E, HOGENHUIS, J. A, MEININGER, V, METSAARS, W. P, HAUW, J.-J, SEILHEAN, D

“…Specific pathological hallmarks have been described in amyotrophic lateral sclerosis (ALS), which include motor neuronal loss, Bunina bodies (BBs) and skein…”
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Prevalence of nephroangiosclerosis in patients with fatal stroke by ABBOUD, H, LABREUCHE, J, DUYCKAERTS, C, HAUW, J.-J, AMARENCO, P

“…Glomerular filtration rate and decline in renal function can be improved by global cardiovascular prevention. However, the prevalence of nephroangiosclerosis…”
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Transmission of the BSE agent to mice in the absence of detectable abnormal prion protein by Lasmezas, C.I. (Commissariat a l'Energie Atomique, Fontenay-aux-Roses, France.), Deslys, J.P, Robain, I, Jaegly, A, Beringue, V, Peyrin, J.M, Fournier, J.G, Hauw, J.J, Rossier, J, Dormont, D

“…The agent responsible for transmissible spongiform encephalopathies (TSEs) is thought to be a malfolded, protease-resistant version (PrPres) of the normal…”
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