Search Results - "Harmatz, D"

Optical properties of bilirubin-serum albumin complexes in aqueous solution. A comparison among albumins from different species by Harmatz, D, Blauer, G

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Reactions of photoexcited methylene blue by Harmatz, D, Blauer, G

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A simple experimental model for hydrophobic interactions in proteins by Lawson, E Q, Sadler, A J, Harmatz, D, Brandau, D T, Micanovic, R, MacElroy, R D, Middaugh, C R

“…The compound N-cyclohexyl-2-pyrrolidone contains a substantial apolar region as well as a peptide bond-like moiety. This solvent, therefore, provides a useful…”
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Circular dichroism of bilirubin-human serum albumin complexes in aqueous solution by Blauer, G., Harmatz, D., Naparstek, A.

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Aggregation state of the gonadotropin receptor by Harmatz, D, Ji, T H, Middaugh, C R

“…The aggregation state of the gonadotropin receptor has been examined by coupling fluorescence energy transfer donor and acceptor fluorophores to hCG and LH…”
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Effect of cationic detergents on ferrimyoglobin by Blauer, G., Harmatz, D., Zvilichovsky, B.

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Optical activity of human serum in the visible region compared with that of the complex bilirubin—serum albumin by Blauer, G., Blondheim, S.H., Harmatz, D., Kapitulnik, J., Kaufmann, N.A., Zvilichovsky, B.

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Enzyme Replacement Therapies and Immunogenicity in Lysosomal Storage Diseases: Is There a Pattern? by Harmatz, Paul, MD

“…Abstract Lysosomal storage diseases arise because of genetic mutations that result in nonfunctioning or dysfunctional lysosomal enzymes responsible for…”
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Outcomes of a Physician Survey on the Type, Progression, Assessment, and Treatment of Neurological Disease in Mucopolysaccharidoses by Scarpa, Maurizio, Harmatz, Paul R., Meesen, Bianca, Giugliani, Roberto

“…The mucopolysaccharidosis (MPS) disorders are a group of rare, inherited lysosomal storage disorders. In each of the 11 MPS (sub)types, deficiency in a…”
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Long-Term Immunogenicity of Elosulfase Alfa in the Treatment of Morquio A Syndrome: Results From MOR-005, a Phase III Extension Study by Long, Brian, PhD, Tompkins, Troy, BS, Decker, Celeste, MD, Jesaitis, Lynne, PhD, Khan, Shahid, MBBS, Slasor, Peter, ScD, Harmatz, Paul, MD, O’Neill, Charles A., PhD, Schweighardt, Becky, PhD

“…Abstract Purpose Elosulfase alfa is an enzyme replacement therapy for the treatment of Morquio A syndrome (mucopolysaccharidosis IVA), a lysosomal storage…”
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Optical properties of bilirubin-serum albumin complexes in aqueous solution. II. Effects of electrolytes and of concentration by Blauer, G, Harmatz, D

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Efficacy of Sapropterin Dihydrochloride in Increasing Phenylalanine Tolerance in Children with Phenylketonuria: A Phase III, Randomized, Double-Blind, Placebo-Controlled Study by Trefz, Friedrich K., MD, Burton, Barbara K., MD, Longo, Nicola, MD, PhD, Casanova, Mercedes Martinez-Pardo, MD, Gruskin, Daniel J., MD, Dorenbaum, Alex, MD, Kakkis, Emil D., MD, PhD, Crombez, Eric A., MD, Grange, Dorothy K., MD, Harmatz, Paul, MD, Lipson, Mark H., MD, Milanowski, Andrzej, MD, PhD, Randolph, Linda Marie, MD, Vockley, Jerry, MD, PhD, Whitley, Chester B., MD, PhD, Wolff, Jon A., MD, Bebchuk, Judith, ScD, Christ-Schmidt, Heidi, MSE, Hennermann, Julia B., MD

“…Objective To evaluate the ability of sapropterin dihydrochloride (pharmaceutical preparation of tetrahydrobiopterin) to increase phenylalanine (Phe) tolerance…”
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Long-Term Galsulfase Treatment Associated With Improved Survival of Patients With Mucopolysaccharidosis VI (Maroteaux-Lamy Syndrome) by Quartel Adrian, Harmatz, Paul R, Lampe, Christina, Guffon Nathalie, Ketteridge, David, Leão-Teles Elisa, Jones, Simon A, Giugliani Roberto

“…Mucopolysaccharidosis VI (MPS VI) is a progressive lysosomal storage disorder with multiorgan and multisystemic pathology. Currently, galsulfase enzyme…”
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Health Related Quality of Life, Disability, and Pain in Alpha Mannosidosis by Borgwardt Line, Guffon Nathalie, Amraoui Yasmina, Jones, Simon A, De Meirleir Linda, Lund, Allan M, Gil-Campos, Mercedes, Van den Hout Johanna M P, Tylki-Szymanska Anna, Geraci, Silvia, Ardigò Diego, Cattaneo Federica, Harmatz, Paul, Phillips, Dawn

“…Alpha-mannosidosis, a rare lysosomal storage disorder caused by deficiency of the lysosomal enzyme alpha-mannosidase, results in accumulation of mannose-rich…”
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Local Anesthetics: Uses and Toxicities by Harmatz, Alan, MD, FACS, ASPS

“…Surgeons are asked to do more and larger procedures as outpatient procedures as the economics of medicine evolve. Indeed, we all carry out procedures on an…”
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An experimental method correcting for absorption flattening and scattering in suspensions of absorbing particles: circular dichroism and absorption spectra of hemoglobin in situ in red blood cells by Schneider, Allan S, Harmatz, David

“…An experimental approach to interpretation of the anomalous absorption and circular dichroism (CD) spectra of hemoglobin in situ in red blood cells is…”
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Optical properties of bilirubin-serum albumin complexes in aqueous solution. I. Dependence on pH by Blauer, G, Harmatz, D, Snir, J

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Expert Opinions on Managing Fertility and Pregnancy in Patients With Mucopolysaccharidosis by Stewart, Fiona, Bentley, Andrew, Burton, Barbara K, Guffon, Nathalie, Hale, Susan L., Harmatz, Paul R., Kircher, Susanne G., Kochhar, Pavan K., Mitchell, John J., Plöckinger, Ursula, Semotok, Jennifer, Graham, Sue, Sande, Stephen, Sisic, Zlatko, Johnston, Tracey A.

“…The mucopolysaccharidosis (MPS) disorders are rare genetic diseases caused by deficiencies in lysosomal enzymes involved in the degradation of…”
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Near-infrared photoacoustic spectroscopy of proteins by Sadler, A J, Horsch, J G, Lawson, E Q, Harmatz, D, Brandau, D T, Middaugh, C R

“…A major problem encountered with the use of electronic spectroscopy in the analysis of biological materials in the ultraviolet, visible, and infrared region…”
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