Search Results - "DRACHMAN, BRIAN"

Expert Consensus Recommendations for the Suspicion and Diagnosis of Transthyretin Cardiac Amyloidosis by Maurer, Mathew S, Bokhari, Sabahat, Damy, Thibaud, Dorbala, Sharmila, Drachman, Brian M, Fontana, Marianna, Grogan, Martha, Kristen, Arnt V, Lousada, Isabelle, Nativi-Nicolau, Jose, Cristina Quarta, Candida, Rapezzi, Claudio, Ruberg, Frederick L, Witteles, Ronald, Merlini, Giampaolo

“…Cardiomyopathy is a manifestation of transthyretin amyloidosis (ATTR), which is an underrecognized systemic disease whereby the transthyretin protein misfolds…”
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Natural history and therapy of TTR-cardiac amyloidosis: emerging disease-modifying therapies from organ transplantation to stabilizer and silencer drugs by Castaño, Adam, Drachman, Brian M., Judge, Daniel, Maurer, Mathew S.

“…Transthyretin-cardiac amyloidoses (ATTR-CA) are an underdiagnosed but increasingly recognized cause of heart failure. Extracellular deposition of fibrillary…”
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Tafamidis Treatment for Patients with Transthyretin Amyloid Cardiomyopathy by Maurer, Mathew S, Schwartz, Jeffrey H, Gundapaneni, Balarama, Elliott, Perry M, Merlini, Giampaolo, Waddington-Cruz, Marcia, Kristen, Arnt V, Grogan, Martha, Witteles, Ronald, Damy, Thibaud, Drachman, Brian M, Shah, Sanjiv J, Hanna, Mazen, Judge, Daniel P, Barsdorf, Alexandra I, Huber, Peter, Patterson, Terrell A, Riley, Steven, Schumacher, Jennifer, Stewart, Michelle, Sultan, Marla B, Rapezzi, Claudio

“…In this randomized, controlled, phase 3 trial of tafamidis for transthyretin amyloid cardiomyopathy, tafamidis was associated with lower all-cause mortality…”
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Inotersen Treatment for Patients with Hereditary Transthyretin Amyloidosis by Benson, Merrill D, Waddington-Cruz, Márcia, Berk, John L, Polydefkis, Michael, Dyck, Peter J, Wang, Annabel K, Planté-Bordeneuve, Violaine, Barroso, Fabio A, Merlini, Giampaolo, Obici, Laura, Scheinberg, Morton, Brannagan, Thomas H, Litchy, William J, Whelan, Carol, Drachman, Brian M, Adams, David, Heitner, Stephen B, Conceição, Isabel, Schmidt, Hartmut H, Vita, Giuseppe, Campistol, Josep M, Gamez, Josep, Gorevic, Peter D, Gane, Edward, Shah, Amil M, Solomon, Scott D, Monia, Brett P, Hughes, Steven G, Kwoh, T. Jesse, McEvoy, Bradley W, Jung, Shiangtung W, Baker, Brenda F, Ackermann, Elizabeth J, Gertz, Morie A, Coelho, Teresa

“…This phase 3 trial tested inotersen, a modified oligonucleotide that targets TTR messenger RNA, in the treatment of hereditary transthyretin amyloidosis, a…”
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Long-Term Survival With Tafamidis in Patients With Transthyretin Amyloid Cardiomyopathy by Elliott, Perry, Drachman, Brian M., Gottlieb, Stephen S., Hoffman, James E., Hummel, Scott L., Lenihan, Daniel J., Ebede, Ben, Gundapaneni, Balarama, Li, Benjamin, Sultan, Marla B., Shah, Sanjiv J.

“…Tafamidis is approved in many countries for the treatment of transthyretin amyloid cardiomyopathy. This study reports data on the long-term efficacy of…”
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Treatment characteristics of patients with hereditary transthyretin amyloidosis: a cohort study by Qarni, Taha N, Jones, Felipe J S, Drachman, Brian, Khella, Sami, Pieretti, Janice, Bustamante, Nicolas Sarmiento, Karam, Chafic

“…There are novel medications approved for the treatment of hereditary transthyretin amyloidosis (ATTRv), classified as transthyretin (TTR) stabilizers or gene…”
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Assessing mNIS+7Ionis and international neurologists' proficiency in a familial amyloidotic polyneuropathy trial by Dyck, Peter J., Kincaid, John C., Dyck, P. James B., Chaudhry, Vinay, Goyal, Namita A., Alves, Christina, Salhi, Hayet, Wiesman, Janice F., Labeyrie, Celine, Robinson‐Papp, Jessica, Cardoso, Márcio, Laura, Matilde, Ruzhansky, Katherine, Cortese, Andrea, Brannagan, Thomas H., Khoury, Julie, Khella, Sami, Waddington‐Cruz, Márcia, Ferreira, João, Wang, Annabel K., Pinto, Marcus V., Ayache, Samar S., Benson, Merrill D., Berk, John L., Coelho, Teresa, Polydefkis, Michael, Gorevic, Peter, Adams, David H., Plante‐Bordeneuve, Violaine, Whelan, Carol, Merlini, Giampaolo, Heitner, Stephen, Drachman, Brian M., Conceição, Isabel, Klein, Christopher J., Gertz, Morie A., Ackermann, Elizabeth J., Hughes, Steven. G., Mauermann, Michelle. L., Bergemann, Rito, Lodermeier, Karen A., Davies, Jenny L., Carter, Rickey E., Litchy, William J.

“…ABSTRACT Introduction Polyneuropathy signs (Neuropathy Impairment Score, NIS), neurophysiologic tests (m+7Ionis), disability, and health scores were assessed…”
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ATTR amyloidosis during the COVID-19 pandemic: insights from a global medical roundtable by Brannagan, 3rd, Thomas H, Auer-Grumbach, Michaela, Berk, John L, Briani, Chiara, Bril, Vera, Coelho, Teresa, Damy, Thibaud, Dispenzieri, Angela, Drachman, Brian M, Fine, Nowell, Gaggin, Hanna K, Gertz, Morie, Gillmore, Julian D, Gonzalez, Esther, Hanna, Mazen, Hurwitz, David R, Khella, Sami L, Maurer, Mathew S, Nativi-Nicolau, Jose, Olugemo, Kemi, Quintana, Luis F, Rosen, Andrew M, Schmidt, Hartmut H, Shehata, Jacqueline, Waddington-Cruz, Marcia, Whelan, Carol, Ruberg, Frederick L

“…The global spread of severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection causing the ongoing coronavirus disease 2019 (COVID-19) pandemic…”
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The Cardiac Amyloidosis Registry Study (CARS): Rationale, Design and Methodology by STERN, LILY K., GRODIN, JUSTIN L., MAURER, MATHEW S., RUBERG, FREDERICK L., PATEL, AYAN R., KHOURI, MICHEL G., ROTH, LORI R., ARAS, MANDAR A., BHARDWAJ, ANJU, BHATTACHARYA, PRIYANKA, BRAILOVSKY, YEVGENIY, DRACHMAN, BRIAN M., EBONG, IMO A., FINE, NOWELL M., GAGGIN, HANNA, GOPAL, DEEPA, GRIFFIN, JAN, JUDGE, DANIEL, KIM, PAUL, MITCHELL, JOSHUA, MITTER, SUMEET S., MOHAN, RAJEEV C., RAMOS, HANNIA, REYENTOVICH, ALEX, SHEIKH, FAROOQ H., SPERRY, BRETT, CARTER, SPENCER, UREY, MARCUS, VAISHNAV, JOBAN, VEST, AMANDA R., KITTLESON, MICHELLE M., PATEL, JIGNESH K.

“…CARS (Cardiac Amyloidosis Registry Study) is a multicenter registry established in 2019 that includes patients with transthyretin (ATTR, wild-type and variant)…”
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Age- and Sex-Related Differences in Patients With Wild-Type Transthyretin Amyloidosis: Insights From THAOS by Mora-Ayestaran, Nerea, Dispenzieri, Angela, Kristen, Arnt V, Maurer, Mathew S, Diemberger, Igor, Drachman, Brian M, Grogan, Martha, Gupta, Pritam, Glass, Oliver, Amass, Leslie, Garcia-Pavia, Pablo

“…Wild-type transthyretin amyloidosis (ATTRwt amyloidosis) is primarily diagnosed in elderly men but diagnoses in younger patients and women have recently…”
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Rationale and design of a randomized trial of automated hovering for post-myocardial infarction patients: The HeartStrong program by Troxel, Andrea B., ScD, Asch, David A., MD, MBA, Mehta, Shivan J., MD, MBA, MSHP, Norton, Laurie, MA, Taylor, Devon, BS, Calderon, Tirza A., MPH, Lim, Raymond, MA, Zhu, Jingsan, MS, MBA, Kolansky, Daniel M., MD, Drachman, Brian M., MD, Volpp, Kevin G., MD, PhD

“…Background Coronary artery disease is the single leading cause of death in the United States, and medications can significantly reduce the rate of repeat…”
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Long-term survival in people with transthyretin amyloid cardiomyopathy who took tafamidis: A Plain Language Summary by Elliott, Perry, Drachman, Brian M, Gottlieb, Stephen S, Hoffman, James E, Hummel, Scott L, Lenihan, Daniel J, Ebede, Ben, Gundapaneni, Balarama, Li, Benjamin, Sultan, Marla B, Shah, Sanjiv J

“…This summary presents the results from an ongoing, long-term extension study that followed an earlier study called ATTR-ACT. People who took part in this…”
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Avoiding misdiagnosis: expert consensus recommendations for the suspicion and diagnosis of transthyretin amyloidosis for the general practitioner by Gertz, Morie, Adams, David, Ando, Yukio, Beirão, João Melo, Bokhari, Sabahat, Coelho, Teresa, Comenzo, Raymond L, Damy, Thibaud, Dorbala, Sharmila, Drachman, Brian M, Fontana, Marianna, Gillmore, Julian D, Grogan, Martha, Hawkins, Philip N, Lousada, Isabelle, Kristen, Arnt V, Ruberg, Frederick L, Suhr, Ole B, Maurer, Mathew S, Nativi-Nicolau, Jose, Quarta, Candida Cristina, Rapezzi, Claudio, Witteles, Ronald, Merlini, Giampaolo

“…Transthyretin amyloidosis (also known as ATTR amyloidosis) is a systemic, life-threatening disease characterized by transthyretin (TTR) fibril deposition in…”
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Assessing mNIS+7 Ionis and international neurologists' proficiency in a familial amyloidotic polyneuropathy trial by Dyck, Peter J, Kincaid, John C, Dyck, P James B, Chaudhry, Vinay, Goyal, Namita A, Alves, Christina, Salhi, Hayet, Wiesman, Janice F, Labeyrie, Celine, Robinson-Papp, Jessica, Cardoso, Márcio, Laura, Matilde, Ruzhansky, Katherine, Cortese, Andrea, Brannagan, 3rd, Thomas H, Khoury, Julie, Khella, Sami, Waddington-Cruz, Márcia, Ferreira, João, Wang, Annabel K, Pinto, Marcus V, Ayache, Samar S, Benson, Merrill D, Berk, John L, Coelho, Teresa, Polydefkis, Michael, Gorevic, Peter, Adams, David H, Plante-Bordeneuve, Violaine, Whelan, Carol, Merlini, Giampaolo, Heitner, Stephen, Drachman, Brian M, Conceição, Isabel, Klein, Christopher J, Gertz, Morie A, Ackermann, Elizabeth J, Hughes, Steven G, Mauermann, Michelle L, Bergemann, Rito, Lodermeier, Karen A, Davies, Jenny L, Carter, Rickey E, Litchy, William J

“…Polyneuropathy signs (Neuropathy Impairment Score, NIS), neurophysiologic tests (m+7 ), disability, and health scores were assessed in baseline evaluations of…”
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A prospective study of continuous intravenous milrinone therapy for status IB patients awaiting heart transplant at home by Brozena, Susan C, Twomey, Carol, Goldberg, Lee R, Desai, Shashank S, Drachman, Brian, Kao, Andrew, Popjes, Eric, Zimmer, Ross, Jessup, Mariell

“…We performed a prospective study to determine the feasibility and safety of continuous intravenous milrinone therapy administered at home in patients listed as…”
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Genotype and Phenotype of Transthyretin Cardiac Amyloidosis by Maurer, Mathew S., MD, Hanna, Mazen, MD, Grogan, Martha, MD, Dispenzieri, Angela, MD, Witteles, Ronald, MD, Drachman, Brian, MD, Judge, Daniel P., MD, Lenihan, Daniel J., MD, Gottlieb, Stephen S., MD, Shah, Sanjiv J., MD, Steidley, D. Eric, MD, Ventura, Hector, MD, Murali, Srinivas, MD, Silver, Marc A., MD, Jacoby, Daniel, MD, Fedson, Savitri, MD, Hummel, Scott L., MD, Kristen, Arnt V., MD, Damy, Thibaud, MD, PhD, Planté-Bordeneuve, Violaine, MD, PhD, Coelho, Teresa, MD, Mundayat, Rajiv, MS, Suhr, Ole B., MD, Waddington Cruz, Márcia, MD, Rapezzi, Claudio, MD

“…Abstract Background Transthyretin amyloidosis (ATTR) is a heterogeneous disorder with multiorgan involvement and a genetic or nongenetic basis. Objectives The…”
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A new transthyretin variant (Glu61Gly) associated with cardiomyopathy by Rosenzweig, Michael, Skinner, Martha, Prokaeva, Tatiana, Théberge, Roger, Costello, Catherine, Drachman, Brian M., Connors, Lawreen H.

“…We report the identification of a new transthyretin (TTR) gene mutation and variant protein, Glu61Gly, in a 55-year-old man with progressive cardiomyopathy,…”
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Treatment characteristics in a cohort of patients with hereditary transthyretin amyloidosis (S7.010) by Qarni, Taha, Bustamante, Nicolas Sarmiento, Jones, Felipe Simoes, Khella, Sami, Drachman, Brian, Pieretti, Janice, Karam, Chafic

“…Abstract only…”
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Characteristics of a single-center cohort of patients with hereditary transthyretin amyloidosis (P13-8.015) by Bustamante, Nicolas Sarmiento, Qarni, Taha, Jones, Felipe Simoes, Khella, Sami, Drachman, Brian, Pieretti, Janice, Karam, Chafic

“…Abstract only…”
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Genotype and Phenotype of Transthyretin Cardiac Amyloidosis: THAOS (Transthyretin Amyloid Outcome Survey) by Maurer, Mathew S, Hanna, Mazen, Grogan, Martha, Dispenzieri, Angela, Witteles, Ronald, Drachman, Brian, Judge, Daniel P, Lenihan, Daniel J, Gottlieb, Stephen S, Shah, Sanjiv J, Steidley, D Eric, Ventura, Hector, Murali, Srinivas, Silver, Marc A, Jacoby, Daniel, Fedson, Savitri, Hummel, Scott L, Kristen, Arnt V, Damy, Thibaud, Planté-Bordeneuve, Violaine, Coelho, Teresa, Mundayat, Rajiv, Suhr, Ole B, Waddington Cruz, Márcia, Rapezzi, Claudio

“…Transthyretin amyloidosis (ATTR) is a heterogeneous disorder with multiorgan involvement and a genetic or nongenetic basis. The goal of this study was to…”
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