Large aplasia cutis congenita of the vertex conservative management

Background Aplasia cutis congenita (ACC) of the vertex with bone defect is a rare and begnin anomaly that can involve the epidermis, dermis, and subcutaneous tissues of the scalp with significant bone defect Bajpai and Pal (J Pediatr Surg 38(2):e4, 2003). When associated with skull defect, this rare...

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Bibliographic Details
Published in:	Child's nervous system Vol. 40; no. 2; pp. 285 - 292
Main Authors:	Bouali, Sofiene, Charfeddine, Sarah Houimli, Ghedira, Khalil, Mechergui, Haifa, Abderrahmen, Khansa, Kallel, Jalel
Format:	Journal Article
Language:	English
Published:	Berlin/Heidelberg Springer Berlin Heidelberg 01-02-2024
Subjects:	Case-based Review Medicine Medicine & Public Health Neurosciences Neurosurgery Acutis dermal dysplasia Scalp defects Bone defect Conservative treatment
Online Access:	Get full text
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Summary:	Background Aplasia cutis congenita (ACC) of the vertex with bone defect is a rare and begnin anomaly that can involve the epidermis, dermis, and subcutaneous tissues of the scalp with significant bone defect Bajpai and Pal (J Pediatr Surg 38(2):e4, 2003). When associated with skull defect, this rare malformation carries the risk of severe complications such as rupture of the superior sagittal sinus or infections. Methods and results We report a case of aplasia cutis congenita of the scalp with skull defect measuring 9 × 10 cm and an exposed sagittal sinus in a newborn. Both conservative and surgical methods have been proposed to treat this condition. In our case, conservative treatment was planned led to complete epithelization and the patient was healing well at 5 years of follow-up. Conclusions ACC of the vertex with a large scalp defects present a management dilemma Rocha et al. (Clin Case Rep 3(10):841–4, 2015). Based on a review of the literature, we report this case to demonstrate that even for the largest skin and bone defects, an initial conservative approach may allow for complete wound closure without the need for early surgical intervention.
Bibliography:	ObjectType-Case Study-2 SourceType-Scholarly Journals-1 ObjectType-Review-3 content type line 23 ObjectType-Feature-5 ObjectType-Article-4 ObjectType-Report-1
ISSN:	0256-7040 1433-0350
DOI:	10.1007/s00381-023-06190-x