Role of maxillofacial surgery in patients with neurofibromatosis type I

Role of maxillofacial surgery in patients with neurofibromatosis type I

Neurofibromas are a clinical manifestation of neurofibromatos is type I (NF1). Management of these tumors remains a challenge for the clinician. The goal of the present study is to point out treatment guidelines for these lesions. Eighteen patients diagnosed with NF1 and presenting lesions of the cr...

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Bibliographic Details
Published in:The Journal of craniofacial surgery Vol. 18; no. 3; pp. 489 - 496
Main Authors: Fadda, Maria Teresa, Giustini, Sandra S, Verdino, Giuseppe G, Bartoli, Davina D, Mustazza, Maria Cristina, Iannetti, Giorgio G, Calvieri, Stefano S
Format: Journal Article
Language:English
Published: United States 01-05-2007
Subjects:
Adolescent
Adult
Cheek - surgery
Child
Child, Preschool
Clinical Protocols
Dentistry
Disease Progression
Esthetics
Facial Neoplasms - surgery
Female
Follow-Up Studies
Frontal Bone - surgery
Humans
Male
Middle Aged
Neurofibromatosis 1 - surgery
Orbital Neoplasms - surgery
Palatal Neoplasms - surgery
Patient Care Planning
Patient Satisfaction
Skull Neoplasms - surgery
Temporal Bone - surgery
Treatment Outcome
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Summary:Neurofibromas are a clinical manifestation of neurofibromatos is type I (NF1). Management of these tumors remains a challenge for the clinician. The goal of the present study is to point out treatment guidelines for these lesions. Eighteen patients diagnosed with NF1 and presenting lesions of the craniomaxillofacial district were included in the study. On the basis of clinical evidence and patient's expectations, only six patients of this group underwent surgery. All patients that had no surgery were included in a follow-up protocol to evaluate progression of disease. Four patients who underwent surgery had good functional/aesthetic results, whereas two patients had incomplete rehabilitation.
Bibliography:ObjectType-Article-1
SourceType-Scholarly Journals-1
ObjectType-Feature-2
content type line 23
ISSN:1049-2275
DOI:10.1097/01.scs.0000249349.59096.06