Search Results - "Biervliet, Stephanie Van"
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Pre-emptive transjugular intrahepatic portosystemic shunt in pediatric cystic fibrosis-related liver disease and portal hypertension: prospective long-term results
Published in Diagnostic and interventional radiology (Ankara, Turkey) (01-01-2024)“…Portal hypertension (PHT) and its sequelae are the most clinically important manifestations in cystic fibrosis-related liver disease (CFLD). This paper aimed…”
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Two cases of DCDC2‐related neonatal sclerosing cholangitis with developmental delay and literature review
Published in Clinical genetics (01-10-2021)“…Ciliopathies are a group of clinical and molecular heterogeneous conditions with pleiotropic manifestations affecting the central nervous system, renal, liver,…”
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Physicochemical stable standard all-in-one parenteral nutrition admixtures for infants and children in accordance with the ESPGHAN/ESPEN guidelines
Published in Nutrition (Burbank, Los Angeles County, Calif.) (01-05-2018)“…•Standard all-in-one (AIO) parenteral nutrition admixtures for pediatric patients from birth to adolescence were developed that meet the ESPGHAN/ESPEN…”
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4
Infliximab in young paediatric IBD patients: it is all about the dosing
Published in European journal of pediatrics (01-12-2020)“…Infliximab (IFX) is administered intravenously using weight-based dosing (5 mg/kg) in inflammatory bowel disease (IBD) patients. Our hypothesis is that…”
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Medical devices that look like medicines: safety and regulatory concerns for children in Europe
Published in Archives of disease in childhood (01-02-2020)“…IntroductionMedical devices (MedDevs) and medicines are assessed (and monitored) differently before and after launch. There are products for repeated oral…”
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Physical activity and its correlates in people with cystic fibrosis: a systematic review
Published in European respiratory review (30-09-2022)“…Cystic fibrosis (CF) is a life-shortening genetic disease, affecting multiple life domains including physical activity (PA). Although higher PA levels are…”
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The effect of an intensive residential rehabilitation program on body composition in patients with cystic fibrosis
Published in European journal of pediatrics (01-06-2021)“…The pulmonary function of patients with cystic fibrosis (CF) is associated with nutritional status not only expressed as body mass index (BMI) but also as…”
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Non-invasive assessment of liver abnormalities in pediatric Fontan patients
Published in European journal of pediatrics (2022)“…Liver abnormalities are well known among long-term survivors of Fontan palliation, which remains the definite surgery for complex congenital heart disease and…”
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Longitudinal Transient Elastography Measurements Used in Follow-up for Patients with Cystic Fibrosis
Published in Ultrasound in medicine & biology (01-04-2016)“…Abstract Cystic fibrosis–related liver disease (CFLD) is diagnosed using a combination of criteria. Transient elastography (TE), an ultrasonographic method to…”
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10
Primum non nocere: lingual frenotomy for breastfeeding problems, not as innocent as generally accepted
Published in European journal of pediatrics (01-08-2020)“…The frenotomy or surgical release of the lingual frenulum is performed with increasing frequency. Restricted tongue mobility, ankyloglossia, is the main…”
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Intra‐patient variability in tacrolimus exposure in pediatric liver transplant recipients: Evolution, risk factors, and impact on patient outcomes
Published in Pediatric transplantation (01-05-2019)“…Background This study aims to investigate the evolution and factors associated with TAC IPV and its impact on patient outcomes in pediatric LT recipients…”
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Predicting inflammatory bowel disease in children with abdominal pain and diarrhoea: calgranulin-C versus calprotectin stool tests
Published in Archives of disease in childhood (01-06-2018)“…ObjectiveCalgranulin-C (S100A12) is a new faecal marker of inflammation that is potentially more specific for inflammatory bowel disease (IBD) than…”
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13
Risk factors and impact of allergic bronchopulmonary aspergillosis in Pseudomonas aeruginosa‐negative CF patients
Published in Pediatric allergy and immunology (01-11-2018)“…Background Allergic bronchopulmonary aspergillosis (ABPA) is a major complication in cystic fibrosis (CF) patients. Risk factors for ABPA and clinical…”
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14
Bifidogenic Effect of Human Milk Oligosaccharides on Pediatric IBD Fecal Microbiota
Published in Microorganisms (Basel) (30-09-2024)“…The prevalence of pediatric inflammatory bowel disease (pIBD) has been increasing over the last two decades. Yet, treatment strategies are still limited, in…”
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Novel CFTR modulator combinations maximise rescue of G85E and N1303K in rectal organoids
Published in ERJ open research (01-04-2022)“…Cystic fibrosis (CF) is a severe monogenic disorder caused by mutations in the cystic fibrosis transmembrane conductance regulator ( ) gene. Several types of…”
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Efficacy of anti-TNF dosing interval lengthening in adolescents and young adults with inflammatory bowel disease in sustained remission (FREE-study): protocol for a partially randomised patient preference trial
Published in BMJ open (03-11-2021)“…IntroductionAnti-tumour necrosis factor (TNF) therapy has greatly improved treatment outcomes in patients with inflammatory bowel disease (IBD), but long-term…”
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Successful liver transplantation in hyperornithinemia‐hyperammonemia‐homocitrullinuria syndrome: Case report
Published in Pediatric transplantation (01-09-2021)“…Background HHH syndrome is a rare autosomal recessive disorder of the urea cycle, caused by a deficient mitochondrial ornithine transporter. We report the…”
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Altered intravenous drug disposition in people living with cystic fibrosis: A meta‐analysis integrating top‐down and bottom‐up data
Published in CPT: pharmacometrics and systems pharmacology (01-08-2022)“…Cystic fibrosis (CF) has been linked to altered drug disposition in various studies. However, the magnitude of these changes, influencing factors, and…”
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Vitamin K, an update for the paediatrician
Published in European journal of pediatrics (01-02-2009)“…Introduction This review summarizes current knowledge on vitamin K for the paediatrician. Vitamin K is a fat-soluble vitamin, present in plants as…”
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Comparison of SARS-CoV-2 seroconversion in children with chronic diseases with healthy children and adults during the first waves of the COVID-19 pandemic
Published in Frontiers in pediatrics (07-08-2023)“…Background Infection with severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) is clinically diverse, and children have a low risk of developing severe…”
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