Dural sinus malformation in the early childhood: case report

Abstract Background: Arteriovenous malformations (AVM) are rare disease in pediatric age group and dural sinus malformation (DSM) has even a lower incidence rate. DSMs are associated with a mild male dominance and onset symptoms appear around 5 months of age. The most common clinical presentation is...

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Bibliographic Details
Published in:Arquivos brasileiros de neurocirurgia Vol. 29; no. 4; pp. 143 - 146
Main Authors: Mattos, João Paulo, de Almeida, João Paulo C., Albuquerque, Lucas Alverne F., Otoch, Marcelo, de Aquino, Ricardo Leite, Bastos, Jubya L. R.
Format: Journal Article
Language:English
Published: Rio de Janeiro, Brazil Thieme Revinter Publicações Ltda 01-12-2010
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Summary:Abstract Background: Arteriovenous malformations (AVM) are rare disease in pediatric age group and dural sinus malformation (DSM) has even a lower incidence rate. DSMs are associated with a mild male dominance and onset symptoms appear around 5 months of age. The most common clinical presentation is macrocrania, seizures, psychomotor delay, intracranial hemorrhage, congestive heart failure and brain ischemia. Early recognition of these lesions is essential to prevent brain injury for ischemia and intracranial hypertension. Case description: We discuss the case of a 4 month-old boy presenting with macrocrania and signs of intracranial hypertension secondary to a transverse sinus dural arteriovenous malformation. This case was successfully treated by endovascular procedure reaching the goal of the treatment that is to obliterate the arterial portion of the fistula while preserving cerebral venous drainage to reduce the pial reflux in order to prevent venous hypertension and ischemic complications.
ISSN:0103-5355
2359-5922
DOI:10.1055/s-0038-1625617