Search Results - "BOULE, MICHELE"

Respiratory muscle decline in duchenne muscular dystrophy by Khirani, Sonia, Ramirez, Adriana, Aubertin, Guillaume, Boulé, Michèle, Chemouny, Chrystelle, Forin, Véronique, Fauroux, Brigitte

“…Summary Objectives Duchenne muscular dystrophy (DMD) causes progressive respiratory muscle weakness. The aim of the study was to analyze the trend of a large…”
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Sleep disordered breathing in patients with Prader-Willi syndrome: A multicenter study by Pavone, Martino, Caldarelli, Valeria, Khirani, Sonia, Colella, Marina, Ramirez, Adriana, Aubertin, Guillaume, Crinò, Antonino, Brioude, Frédéric, Gastaud, Frédérique, Beydon, Nicole, Boulé, Michèle, Giovannini-Chami, Lisa, Cutrera, Renato, Fauroux, Brigitte

“…Summary Objectives Sleep disordered breathing (SDB) is common in patients with Prader–Willi syndrome (PWS) and systematic screening is recommended, especially…”
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Sleep disordered breathing in Silver−Russell syndrome patients: a new outcome by Giabicani, Éloïse, Boulé, Michèle, Aubertin, Guillaume, Galliani, Eva, Brioude, Frédéric, Dubern, Béatrice, Netchine, Irène

“…Imprinting disorders (ID), such as Prader–Willi syndrome (PWS), are associated with sleep-disordered breathing (SDB). No data are available for Silver−Russell…”
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Diagnosis, follow-up and management of sleep-disordered breathing in children with osteogenesis imperfecta by Léotard, Antoine, Taytard, Jessica, Aouate, Marion, Boule, Michèle, Forin, Veronique, Lallemant-Dudek, Pauline

“…•First report about sleep-disordered breathing and clinical features in children with osteogenesis imperfecta.•The prevalence of sleep-disordered breathing…”
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Carbon dioxide levels during polygraphy in children with sleep-disordered breathing by Pautrat, Jade, Khirani, Sonia, Boulé, Michèle, Ramirez, Adriana, Beydon, Nicole, Fauroux, Brigitte

“…Purpose The recent scoring rules of the American Academy of Sleep Medicine (AASM) define hypoventilation in children as a carbon dioxide (CO 2 ) level of…”
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Forced expiratory flows' contribution to lung function interpretation in schoolchildren by Boutin, Bernard, Koskas, Marc, Guillo, Houda, Maingot, Lucia, La Rocca, Marie-Claude, Boulé, Michèle, Just, Jocelyne, Momas, Isabelle, Corinne, Alberti, Beydon, Nicole

“…Forced expiratory flow (FEF) at low lung volumes are supposed to be better at detecting lung-function impairment in asthmatic children than a forced volume…”
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Primary ciliary dyskinesia presentation in 60 children according to ciliary ultrastructure by Vallet, Christelle, Escudier, Estelle, Roudot-Thoraval, Françoise, Blanchon, Sylvain, Fauroux, Brigitte, Beydon, Nicole, Boulé, Michèle, Vojtek, Anne Marie, Amselem, Serge, Clément, Annick, Tamalet, Aline

“…Primary ciliary dyskinesia (PCD) is an inherited disease related to ciliary dysfunction, with heterogeneity in clinical presentation and in ciliary…”
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Nocturnal hypoxaemia and hypercapnia in children with neuromuscular disorders by BERSANINI, Chiara, KHIRANI, Sonia, RAMIREZ, Adriana, LOFASO, Frédéric, AUBERTIN, Guillaume, BEYDON, Nicole, MAYER, Michèle, MAINCENT, Kim, BOULE, Michèle, FAUROUX, Brigitte

“…The aim of the study was to identify daytime predictors of nocturnal gas exchange anomalies in children with neuromuscular disease (NMD) and normal daytime gas…”
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Pre/Postbronchodilator Interrupter Resistance Values in Healthy Young Children by Beydon, Nicole, Amsallem, Francis, Bellet, Michele, Boule, Michele, Chaussain, Michele, Denjean, Andre, Matran, Regis, Wuyam, Bernard, Alberti, Corinne, Gaultier, Claude

“…The interrupter technique estimates flow resistance. It entails occlusion of the airways during tidal breathing while flow and mouth pressure are recorded…”
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Lung function, diagnosis, and treatment of sleep‐disordered breathing in children with achondroplasia by Julliand, Sébastien, Boulé, Michèle, Baujat, Geneviève, Ramirez, Adriana, Couloigner, Vincent, Beydon, Nicole, Zerah, Michel, di Rocco, Federico, Lemerrer, Martine, Cormier‐Daire, Valérie, Fauroux, Brigitte

“…Children with achondroplasia are at risk of sleep‐disordered breathing. The aim of the study was to evaluate lung function and sleep‐disordered breathing in…”
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Respiratory Muscle Testing: A Valuable Tool for Children with Neuromuscular Disorders by Nicot, Frederic, Hart, Nicholas, Forin, Veronique, Boule, Michele, Clement, Annick, Polkey, Michael I, Lofaso, Frederic, Fauroux, Brigitte

“…Data on respiratory muscle performance in children with neuromuscular disorders are limited. The aim of this study was to assess respiratory muscle strength by…”
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Genotype analysis and phenotypic manifestations of children with intermediate sweat chloride test results by Desmarquest, P, Feldmann, D, Tamalat, A, Boule, M, Fauroux, B, Tournier, G, Clement, A

“…Cystic fibrosis (CF) is one of the most common inherited diseases among whites. Since the cloning of the CF transmembrane conductance regulator (CFTR) gene, a…”
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Changes in Pulmonary Mechanics with Increasing Disease Severity in Children and Young Adults with Cystic Fibrosis by Hart, Nicholas, Polkey, Michael I, Clement, Annick, Boule, Michele, Moxham, John, Lofaso, Frederic, Fauroux, Brigitte

“…As forced expiratory volume in 1 second (FEV(1)) is a major predictor of outcome in patients with cystic fibrosis (CF), we investigated the effect of FEV(1) on…”
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Nutritional status is an important predictor of diaphragm strength in young patients with cystic fibrosis by Hart, Nicholas, Tounian, Patrick, Clément, Annick, Boulé, Michèle, Polkey, Michael I, Lofaso, Frédéric, Fauroux, Brigitte

“…The effect of nutritional status and lung disease progression on diaphragm strength in young patients with cystic fibrosis remains unclear. The aim of this…”
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Arterial alterations in severely obese children with obstructive sleep apnoea by Dubern, Beatrice, Aggoun, Yacine, Boulé, Michèle, Fauroux, Brigitte, Bonnet, Damien, Tounian, Patrick

“…Abstract Background. Obstructive sleep apnoea (OSA) in obese adults is associated with cardiovascular disease independently of obesity. Vascular alterations…”
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Mechanical limitation during CO2 rebreathing in young patients with cystic fibrosis by FAUROUX, Brigitte, NICOT, Frédéric, BOELLE, Pierre-Yves, BOULE, Michèle, CLEMENT, Annick, LOFASO, Frédéric, BONORA, Monique

“…The aim of the study was to determine whether a decrease in the ventilatory response to carbon dioxide (CO2) in children with cystic fibrosis (CF) is related…”
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Longitudinal course of lung function and respiratory muscle strength in spinal muscular atrophy type 2 and 3 by Khirani, Sonia, Colella, Marina, Caldarelli, Valeria, Aubertin, Guillaume, Boulé, Michèle, Forin, Véronique, Ramirez, Adriana, Fauroux, Brigitte

“…Abstract Background Spinal muscular atrophy (SMA) is a common genetic disorder that causes severe hypotonia and weakness, and often fatal restrictive lung…”
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Abnormal Central Complex Is a Marker of Severity in the Presence of Partial Ciliary Defect by Tamalet, Aline, Clement, Annick, Roudot-Thoraval, Francoise, Desmarquest, Pascale, Roger, Gilles, Boule, Michele, Millepied, Marie Claude, Baculard, TA{section}; Armelle, Escudier, Estelle

“…Ciliary ultrastructural defects with total lack of dynein arms (DA) cause abnormal mucociliary function leading to the chronic infections observed in primary…”
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Influence of Interleukin-10 on Aspergillus fumigatus Infection in Patients with Cystic Fibrosis by Brouard, Jacques, Knauer, Nicola, Boelle, Pierre-Yves, Corvol, Harriet, Henrion-Caude, Alexandra, Flamant, Cyril, Bremont, François, Delaisi, Bertrand, Duhamel, Jean-Francois, Marguet, Christophe, Roussey, Michel, Miesch, Marie-Claude, Chadelat, Katarina, Boule, Michele, Fauroux, Brigitte, Ratjen, Felix, Grasemann, Hartmut, Clement, Annick

“…Recent evidence suggests that genetic polymorphisms that affect the production of interleukin (IL)–10 may play a role in the response to pathogens in cystic…”
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Whole pulmonary assessment 1 year after paediatric acute respiratory distress syndrome: prospective multicentre study by Nève, Véronique, Sadik, Ahmed, Petyt, Laurent, Dauger, Stéphane, Kheniche, Ahmed, Denjean, André, Léger, Pierre-Louis, Chalard, François, Boulé, Michèle, Javouhey, Etienne, Reix, Philippe, Canterino, Isabelle, Deken, Valérie, Matran, Régis, Leteurtre, Stéphane, Leclerc, Francis

“…Background Long-term pulmonary sequelae, including 1-year thoracic computed tomography (CT) sequelae of paediatric acute respiratory distress syndrome (ARDS)…”
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