Search Results - "BAKER, ALASTAIR J"

The frequency and outcome of biliary atresia in the UK and Ireland by McKiernan, Patrick J, Baker, Alastair J, Kelly, Deirdre A

“…Biliary atresia is an obliterative cholangiopathy of infancy that is fatal if untreated. Surgical treatment, the Kasai portoenterostomy, may restore bile flow…”
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British Paediatric Surveillance Unit Study of Biliary Atresia: Outcome at 13 Years by McKiernan, PJ, Baker, Alastair J, Lloyd, Carla, Mieli‐Vergani, Giorgina, Kelly, Deirdre A

“…ABSTRACT Background: Little information is available on contemporary, prospectively collected data on the long‐term outcome of national cohorts of children…”
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Neonatal Herpes Simplex Virus Infection Presenting as Acute Liver Failure: Prevalent Role of Herpes Simplex Virus Type I by Verma, Anita, Dhawan, Anil, Zuckerman, Mark, Hadzic, Nedim, Baker, Alastair J, Mieli-Vergani, Giorgina

“…BACKGROUND:Acute liver failure (ALF) in neonates is rare but carries a high mortality without liver transplantation. Herpes simplex virus (HSV) is one of the…”
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Serum hyaluronic acid as an early prognostic marker in biliary atresia by Dhawan, Anil, Trivedi, Premila, Cheeseman, Paul, Baker, Alastair J., Howard, Edward R., Mieli-Vergani, Giorgina

“…Purpose: The aim of this study was to assess whether serum concentrations of hyaluronic acid (HA), measured at diagnosis is an early biochemical marker of…”
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Can energy expenditure be predicted in critically ill children? by Taylor, Rachel M, Cheeseman, Paul, Preedy, Victor, Baker, Alastair J, Grimble, George

“…To determine whether critically ill children are hypermetabolic and to calculate whether predictive equations are appropriate for critically ill children…”
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VPS33B mutation with ichthyosis, cholestasis, and renal dysfunction but without arthrogryposis: Incomplete ARC syndrome phenotype by Bull, Laura N., Mahmoodi, Venus, Baker, Alastair J., Jones, Rosamond, Strautnieks, Sandra S., Thompson, Richard J., Knisely, A.S.

“…Arthrogryposis-renal dysfunction-cholestasis (ARC) syndrome is a rare multisystem disorder first described in 1979 1 and recently ascribed to mutation in…”
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Coincidental GM1 Gangliosidosis in an Infant With α‐1‐Antitrypsin Deficiency by Srinivasan, Ramesh, Sudeendra, Shalini, Cosgrove, Michael, Wagner, Bart, Baker, Alastair J, Portmann, Bernard

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Ocular abnormalities in Alagille syndrome by Hingorani, M, Nischal, K K, Davies, A, Bentley, C, Vivian, A, Baker, A J, Mieli-Vergani, G, Bird, A C, Aclimandos, W A

“…To assess the type and frequency of ocular abnormalities occurring in Alagille syndrome (AS) in a large group of affected patients and their parents and the…”
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Bone mineral density and height gain in children with chronic cholestatic liver disease undergoing transplantation by D'ANTIGA, Lorenzo, MONIZ, Caje, DHAWAN, Anil, BUXTON-THOMAS, Muriel, CHEESEMAN, Paul, GRAY, Beverly, ABRAHA, Hagosa, BAKER, Alastair J, HEATON, Nigel D, RELA, Mohammed, MIELI-VERGANI, Giorgina

“…Osteodystrophy is a well-described complication of chronic liver disease. Previous reports in adults and children undergoing liver transplantation (LT) were…”
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Calcineurin-inhibitor related nephrotoxicity-reversibility in paediatric liver transplant recipients by AW, Marion M, SAMAROO, Beatrice, BAKER, Alastair J, VERMA, Anita, RELA, Mohammed, HEATON, Nigel D, MIELI-VERGANI, Giorgina, DHAWAN, Anil

“…To study the efficacy of mycophenolate mofetil (MMF) as renal rescue in paediatric liver transplant recipients with calcineurin-inhibitor- (CI) related…”
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Neonatal Herpes Simplex Virus Infection Presenting as Acute Liver Failure by Verma, Anita, Dhawan, Anil, Zuckerman, Mark, Hadzic, Nedim, Baker, Alastair J., Mieli‐Vergani, Giorgina

“…ABSTRACT Background: Acute liver failure (ALF) in neonates is rare but carries a high mortality without liver transplantation. Herpes simplex virus (HSV) is…”
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Recurrence of langerhans cell histiocytosis in the graft after pediatric liver transplantation by HADZIC, Nedim, PRITCHARD, Jon, WEBB, David, PORTMANN, Bernard, HEATON, Nigel D, RELA, Mohamed, DHAWAN, Anil, BAKER, Alastair J, MIELI-VERGANI, Giorgina

“…Two girls were diagnosed with Langerhans cell histiocytosis (LCH) at the age of 16 and 7 months and developed end stage chronic liver disease related to…”
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Liver dysfunction induced by bile duct ligation and galactosamine injection alters cardiac protein synthesis by Hunter, Ross J., Patel, Vinood B., Baker, Alastair J., Preedy, Victor R.

“…Liver disease has been shown to affect the cardiovascular system and may influence cardiac protein metabolism. This hypothesis was tested by measuring rates of…”
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Isoenzyme characterization in isolated elevation of alkaline phosphatase after liver transplantation in children by O'RIORDAN, Sean, BAKER, Alastair J, SHERWOOD, Roy A

“…Isolated transient elevation of alkaline phosphatase (ALP) in the absence of bone or liver disease has been reported in children including liver transplant…”
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Diaphragmatic dysfunction after pediatric orthotopic liver transplantation by MANCZUR, Terezia I, GREENOUGH, Anne, RAFFERTY, Gerrard F, DIMITRIOU, Gabriel, BAKER, Alastair J, MIELI-VERGANI, Giorgina, MOHAMMED RELA, S, HEATON, Nigel

“…Pediatric orthotopic liver transplantation (OLT) has a low mortality. Some children, however, have an adverse outcome defined as a prolonged ventilatory…”
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Liver transplant for giant cell hepatitis with autoimmune haemolytic anaemia by Melendez, Hector Vilca, Rela, Mohamed, Baker, Alastair J, Ball, Colin, Portmann, Bernard, Mieli-Vergani, Giorgina, Heaton, Nigel D

“…Giant cell hepatitis (CGH) with autoimmune haemolytic anaemia (AHA) is a distinct entity with an aggressive course. Immunosuppression may help early disease. A…”
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Mycobacterium tuberculosis infection in pediatric liver transplant recipients by VERMA, ANITA, DHAWAN, ANIL, WADE, JIM J, LIM, WAH H, RUIZ, GARY, PRICE, JOHN F, HADZIC, NEDIM, BAKER, ALASTAIR J, RELA, MOHEMMED, HEATON, NIGEL D, MIELI-VERGANI, GIORGINA

“…OBJECTIVES. METHODS. RESULTS.Mycobacterium tuberculosis infection occurred in 6 of 254 (2.4%) children undergoing liver transplantation between 1991 and 1998…”
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The Effect of Short Stature, Portal Hypertension, and Cholestasis on Growth Hormone Resistance in Children with Liver Disease by Holt, Richard I. G, Jones, Jennifer S, Baker, Alastair J, Buchanan, Charles R

“…ABSTRACTChronic liver disease is associated with GH resistance, which is characterized by high circulating GH and low insulin-like growth factor I (IGF-I)…”
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APLASTIC ANEMIA ASSOCIATED WITH FULMINANT LIVER FAILURE IN CHILDREN by Tung, John, Hadzic, Nedim, Layton, Mark, Baker, Alastair J, Dhawan, Anil, Heaton, Nigel D, Mieli-Vergani, Giorgina

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Bone Marrow Failure in Children With Acute Liver Failure by Tung, John, Hadzic, Nedim, Layton, Mark, Baker, Alastair J., Dhawan, Anil, Rela, Mohamed, Heaton, Nigel D., Mieli‐Vergani, Giorgina

“…ABSTRACT Background Aplastic anemia is a rare but well‐recognized complication of acute hepatitis and acute liver failure. The cause is unknown, and the…”
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