Unilateral agenesis of the pulmonary artery. Experience with 4 cases

We present our experience with four cases of unilateral pulmonary agenesis, 3 of the right artery and the other one of the left. Two of the patients had pulmonary hypertension and one of them died at two years of age. All cases were diagnosed by using pulmonary angiography. Aortography demonstrated...

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Bibliographic Details
Published in:	Anales españoles de pediatría Vol. 38; no. 2; p. 139
Main Authors:	Herraiz Sarachaga, I, Pérez González, W, Vergara Rodríguez, F, Alonso Lastra, M J, Acerete Guillén, F, Bermúdez-Cañete Fernández, R, Díaz García, P, Quero Jiménez, M
Format:	Journal Article
Language:	Spanish
Published:	Spain 01-02-1993
Subjects:	Angiography Child Child, Preschool Female Humans Hypertension, Pulmonary - etiology Infant Male Pulmonary Artery - abnormalities Pulmonary Artery - diagnostic imaging Pulmonary Artery - surgery Pulmonary Heart Disease - diagnostic imaging Pulmonary Heart Disease - etiology Radiography, Thoracic
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Summary:	We present our experience with four cases of unilateral pulmonary agenesis, 3 of the right artery and the other one of the left. Two of the patients had pulmonary hypertension and one of them died at two years of age. All cases were diagnosed by using pulmonary angiography. Aortography demonstrated the absence of circulatory supply to the lung and a contralateral aortic arch to the absent pulmonary artery. We have performed a review of the literature with an emphasis on the diagnostic aspects of this condition, and discuss the considerations for possible surgery in symptomatic patients.
ISSN:	0302-4342