Search Results - "Acosta, P B"

Intake of major nutrients by women in the Maternal Phenylketonuria (MPKU) Study and effects on plasma phenylalanine concentrations by ACOSTA, Phyllis B, MATALON, Kimberly, CASTIGLIONI, Lois, ROHR, Fran J, WENZ, Elizabeth, AUSTIN, Valerie, AZEN, Colleen

“…Women with untreated phenylketonuria (PKU) often have poor reproductive outcomes. We assessed the effects of intakes of major nutrients on plasma phenylalanine…”
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Fruits and vegetables are a source of galactose: Implications in planning the diets of patients with Galactosaemia by Gross, K. C., Acosta, P. B.

“…Summary It has become apparent that removing dairy products from the diets of patients with galactosaemia does not sufficiently diminish the deleterious signs…”
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Nutrition studies in treated infants and children with phenylketonuria: vitamins, minerals, trace elements by Acosta, P B

“…Chemically defined or elemental medical foods provide the majority of protein equivalent in the diets of children treated for phenylketonuria (PKU). Because of…”
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Plasma micronutrient concentrations in infants undergoing therapy for phenylketonuria by Acosta, P.B, Yannicelli, S

“…Twenty-seven infants with classical phenylketonuria were evaluated longitudinally for 6 mo while ingesting Phenex-1 Amino Acid Modified Medical Food With Iron…”
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Recommendations for protein and energy intakes by patients with phenylketonuria by Acosta, P B

“…Recent reports describe poor growth in treated children with phenylketonuria (PKU). That poor growth is not a concomitant of the disorder and need not result…”
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The effect of dietary fruits and vegetables on urinary galactitol excretion in galactose‐1‐phosphate uridyltransferase deficiency by Berry, G. T., Palmieri, M., Gross, K. C., Acosta, P. B., Henstenburg, J. A., Mazur, A., Reynolds, R., Segal, S.

“…Summary Even on a lactose‐restricted diet, urinary galactitol excretion and erythrocyte galactose‐1‐phosphate levels are persistently elevated in patients with…”
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Effect of Simultaneous Ingestion of L-Amino Acids and Whole Protein on Plasma Amino Acid and Urea Nitrogen Concentrations in Humans by Gropper, Sareen S., Acosta, Phyllis B.

“…The effect of whole protein and L-amino acid ingestion on plasma amino acid (PAA) and urea nitrogen (UN) concentrations was investigated. Ten males ingested…”
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Nutrition and reproductive outcome in maternal phenylketonuria by Michals, K, Acosta, P B, Austin, V, Castiglioni, L, Rohr, F, Wenz, E, Azen, C

“…Maternal weight gain and intake of selected nutrients were correlated with plasma phenylalanine (Phe) concentrations and reproductive outcomes (in 150 and 142…”
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Improved growth and nutrition status in children with methylmalonic or propionic acidemia fed an elemental medical food by Yannicelli, Steven, Acosta, Phyllis B, Velazquez, Antonio, Bock, Hans-Georg, Marriage, Barbara, Kurczynski, Thaddeus W, Miller, Marvin, Korson, Mark, Steiner, Robert D, Rutledge, Lane, Bernstein, Laurie, Chinsky, Jeffrey, Galvin-Parton, Patricia, Arnold, Georgianne L

“…Background: Failure-to-thrive (FTT) has been described in patients with organic acidemias treated with low protein diets. Objective: To determine if patients…”
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Hidden sources of galactose in the environment by Acosta, P B, Gross, K C

“…A galactose-restricted diet free of lactose is lifesaving in patients with galactose-1-phosphate uridyl transferase (GALT) deficiency, but does not prevent…”
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Protein Status of Infants with Phenylketonuria Undergoing Nutrition Management by Acosta, P.B., Yannicelli, S., Marriage, B., Steiner, R., Gaffield, B., Arnold, G., Lewis, V., Cho, S., Berstein, L., Parton, P., Leslie, N., Korson, M.

“…Objectives: The objectives of this study were to determine if Phenex-1, amino-acid modified medical food with iron maintained normal indices of protein status…”
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Nutritional therapy for pregnant women with a metabolic disorder by Koch, R, Acosta, P B, Williams, J C

“…Nutritional therapy is essential for a normal reproductive outcome in phenylketonuric women. In homocystinuria, fetal outcome is good in women whose disorder…”
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Osmolality of enteral formulas for maternal phenylketonuria by Anderson, K., Acosta, P. B., Kennedy, B.

“…Osmolalities of individual products and composite diets used in the treatment of maternal phenylketonuria were measured. Mathematical equations were developed…”
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RSH/SLO (Smith-Lemli-Opitz) syndrome: designing a high cholesterol diet for the SLO syndrome by Acosta, P B

“…A high cholesterol diet has been suggested to help prevent the poor reproductive outcomes found in heterozygote carriers of fetuses affected with the…”
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Phenylalanine intakes of 1- to 6-year-old children with phenylketonuria undergoing therapy by Acosta, PB, Trahms, C, Wellman, NS, Williamson, M

“…Mean of median phenylalanine intakes of 1 — to 6-yr-old treated phenylketonuria patients who were growing normally were evaluated by age, sex, and treatment…”
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Plasma vitamin E concentrations of older infants fed cow's milk or infant formula by Shank, J.S. (Florida State University, Tallahassee, FL), Dorsey, J.L, Anderson, K, Cooper, W.T, Acosta, P.B

“…Nutrition of older infants, though important for optimal brain development, is inadequately studied. The beverage choice markedly influences nutrient intake,…”
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The effect of a phenylalanine and tyrosine restricted diet on elemental balance studies and plasma aminograms of patients with disseminated malignant melanoma by Lawson, DH, Stockton, LH, Bleier, JC, Acosta, PB, Heymsfield, SB, Nixon, DW

“…Previous studies indicate dietary phenylalanine and tyrosine restriction may be of value in managing advanced cancer patients. To further evaluate this…”
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Trace Element Status of PKU Children Ingesting an Elemental Diet by Acosta, Phyllis B., Stepnick-Gropper, Sareen, Clarke-Sheehan, Noreen, Wenz, Elizabeth, Cheng, Mary, Anderson, Kathryn, Koch, Richard

“…We assessed the trace metal status of 10 children (3.5 to 13.3 yr) with phenylketonuria (PKU) who were successively treated for at least 6 months with a…”
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Protein intake affects phenylalanine requirements and growth of infants with phenylketonuria by Acosta, P B, Yannicelli, S

“…Growth and metabolic status of 25 infants with PKU were evaluated based on protein intake. Food A-fed infants received a medical food containing 3.12 g protein…”
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Nutrition support of inborn errors of amino acid metabolism by Kennedy, B, Anderson, K, Acosta, P B

“…Programs for nutrition support of patients with phenylketonuria, maternal phenylketonuria, branched chain ketoaciduria and vitamin B-6 non-responsive…”
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